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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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ARPP19
cAMP regulated phosphoprotein 19
Chromosome 15 · 15q21.2
NCBI Gene: 10776Ensembl: ENSG00000128989.11HGNC: HGNC:16967UniProt: H3BMD8
43PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein phosphatase inhibitor activitysignaling receptor bindingprotein bindingpotassium channel regulator activityacute myeloid leukemiagastric cancerhepatocellular carcinomaHypercholesterolemia
✦AI Summary

ARPP19 (cAMP-regulated phosphoprotein 19) is a protein phosphatase inhibitor that specifically suppresses protein phosphatase 2A (PP2A), particularly the PP2A:B55 holoenzyme complex, during mitosis 1. When phosphorylated at Ser-62 by Greatwall kinase, ARPP19 becomes a potent PP2A inhibitor 2, binding to the B55 regulatory subunit (specifically PPP2R2D/PR55-delta) through intrinsically disordered regions 1. This inhibition maintains elevated cyclin-B1-CDK1 kinase activity during M phase, essential for proper mitotic progression 3. ARPP19 is uniquely essential for mouse embryonic development and mitotic cell division, unlike its paralog ENSA, which suggests specialized roles despite shared PP2A inhibition mechanisms 3. The Greatwall-ARPP19-PP2A axis operates in diverse cell types, including platelets where cAMP/PKA signaling regulates ARPP19 phosphorylation 4. Beyond cell cycle control, ARPP19 dysregulation associates with cancer progression; elevated ARPP19 expression drives proliferation, migration, and invasion in colorectal and prostate cancers, partly through miR-26b-5p regulation 5 6. These findings establish ARPP19 as a critical mitotic regulator with therapeutic implications in cancer.

Sources cited
1
ARPP19 is a phosphorylated intrinsically disordered protein that inhibits PP2A:B55 through specific binding interactions revealed by cryo-EM structures
PMID: 38123684
2
Greatwall kinase phosphorylates ARPP19 to create a potent PP2A-B55 inhibitor essential for mitotic progression
PMID: 30355803
3
ARPP19 is essential for mouse embryonic development and mitotic cell division by maintaining PP2A-B55 inhibition during mitosis, unlike ENSA
PMID: 30626720
4
ARPP19 phosphorylation at Ser-62 by MASTL acts as a PP2A inhibitor in human platelets and is regulated by cAMP/PKA signaling
PMID: 32085646
5
ARPP19 upregulation promotes colorectal cancer cell proliferation, migration, and invasion, regulated by the miR-26b-5p/HCG11 axis
PMID: 36874625
6
ARPP19 acts as a proteomic hub protein driving metastatic heterogeneity in advanced prostate cancer
PMID: 40345286
Disease Associationsⓘ20
acute myeloid leukemiaOpen Targets
0.08Suggestive
gastric cancerOpen Targets
0.08Suggestive
hepatocellular carcinomaOpen Targets
0.06Suggestive
HypercholesterolemiaOpen Targets
0.06Suggestive
colorectal carcinomaOpen Targets
0.05Suggestive
laryngeal neoplasmOpen Targets
0.05Suggestive
placenta praeviaOpen Targets
0.04Suggestive
gliomaOpen Targets
0.03Suggestive
pleural empyemaOpen Targets
0.03Suggestive
pneumothoraxOpen Targets
0.03Suggestive
polyarteritis nodosaOpen Targets
0.03Suggestive
nephrotic syndromeOpen Targets
0.03Suggestive
head injuryOpen Targets
0.03Suggestive
laryngeal carcinomaOpen Targets
0.03Suggestive
neoplasmOpen Targets
0.02Suggestive
glioblastoma multiformeOpen Targets
0.02Suggestive
oral squamous cell carcinomaOpen Targets
0.02Suggestive
KeloidOpen Targets
0.02Suggestive
chondrocalcinosisOpen Targets
0.02Suggestive
Alzheimer diseaseOpen Targets
0.02Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
PPP2R2DProtein interaction100%PPP2CAProtein interaction100%PPP2R2AProtein interaction100%CDK1Protein interaction90%ARPP21Protein interaction84%MASTLProtein interaction84%
Tissue Expression6 tissues
Brain
100%
Bone Marrow
55%
Heart
45%
Lung
28%
Ovary
22%
Liver
18%
Gene Interaction Network
Click a node to explore
ARPP19PPP2R2DPPP2CAPPP2R2ACDK1ARPP21MASTL
PROTEIN STRUCTURE
Preparing viewer…
PDB8TTB · 2.77 Å · EM
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.75LoF Tolerant
pLIⓘ
0.01Tolerant
Observed/Expected LoF0.92 [0.47–1.75]
RankingsWhere ARPP19 stands among ~20K protein-coding genes
  • #9,691of 20,598
    Most Researched43
  • #16,320of 17,882
    Most Constrained (LOEUF)1.75
Genes detectedARPP19
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Cryo-EM structures of PP2A:B55-FAM122A and PP2A:B55-ARPP19.
PMID: 38123684
Nature · 2024
1.00
2
Greatwall kinase at a glance.
PMID: 30355803
J Cell Sci · 2018
0.90
3
ENSA and ARPP19 differentially control cell cycle progression and development.
PMID: 30626720
J Cell Biol · 2019
0.80
4
The Cell Cycle Checkpoint System MAST(L)-ENSA/ARPP19-PP2A is Targeted by cAMP/PKA and cGMP/PKG in Anucleate Human Platelets.
PMID: 32085646
Cells · 2020
0.70
5
Proteomic hub proteins CDKN2B, TRAPPC2L, WFS1, and ARPP19 drive biochemical recurrence and metastatic progression in prostate cancer: Protein macromolecule action.
PMID: 40345286
Int J Biol Macromol · 2025
0.60