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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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CLK2
CDC like kinase 2
Chromosome 1 · 1q22
NCBI Gene: 1196Ensembl: ENSG00000176444.20HGNC: HGNC:2069UniProt: A8K7I0
72PubMed Papers
20Diseases
1Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Highly ConstrainedKinase
CLINICAL
Clinical Trials
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
response to ionizing radiationregulation of RNA splicingnucleoplasmnuclear bodyAlzheimer diseaseneurodegenerative diseaseParkinson diseaselysosomal storage disease
✦AI Summary

CLK2 (CDC-like kinase 2) is a dual-specificity kinase that phosphorylates both serine/threonine and tyrosine residues, playing critical roles in RNA splicing regulation and cellular stress responses. CLK2 phosphorylates serine/arginine-rich (SR) splicing factors, modulating alternative splicing patterns and intron retention 1. The kinase undergoes liquid-liquid phase separation within nuclear speckles during stress conditions, forming condensates that reorganize nuclear architecture and promote intron retention by sequestering splicing factors 2. CLK2 also regulates the NF-κB inflammatory pathway through IκBα-independent mechanisms, phosphorylating RelA/p65 at Ser180 to promote its degradation and nuclear export, thereby providing rapid termination of NF-κB activation 3. In cancer contexts, CLK2 functions as a ferroptosis suppressor by stabilizing KEAP1 to inhibit NRF2 activity and downregulating p53, which disrupts the balance between pro-ferroptotic HMOX1 and anti-ferroptotic SLC7A11 4. CLK2 promotes tumor progression in pancreatic cancer through enhanced translation efficiency via PABPC1 deubiquitination 5. Therapeutically, CLK2 represents a promising target for osteoarthritis treatment through Wnt pathway inhibition 67, while genetic variants in CLK2 are associated with early-onset cerebellar atrophy 8.

Sources cited
1
CLK2 regulates alternative polyadenylation through phase separation and phosphorylation of CPSF6
PMID: 37777964
2
CLK2 undergoes liquid-liquid phase separation in nuclear speckles and promotes intron retention during heat shock stress
PMID: 39119950
3
CLK2 provides IκBα-independent termination of NF-κB activation by phosphorylating RelA/p65 at Ser180
PMID: 38724505
4
CLK2 suppresses ferroptosis in colorectal cancer by regulating KEAP1/NRF2 and p53 pathways
PMID: 40882016
5
CLK2 promotes pancreatic cancer progression through USP10-mediated deubiquitination of PABPC1
PMID: 37757903
6
CLK2 inhibition modulates Wnt pathway for osteoarthritis treatment
PMID: 31132406
7
CLK2 inhibitors show therapeutic potential for knee osteoarthritis treatment
PMID: 38500250
8
CLK2 genetic variants are associated with early-onset cerebellar atrophy
PMID: 38003592
Disease Associationsⓘ20
Alzheimer diseaseOpen Targets
0.48Moderate
neurodegenerative diseaseOpen Targets
0.44Moderate
lysosomal storage diseaseOpen Targets
0.44Moderate
multiple sclerosisOpen Targets
0.44Moderate
Parkinson diseaseOpen Targets
0.44Moderate
neuroinflammatory disorderOpen Targets
0.39Weak
osteoarthritis, kneeOpen Targets
0.39Weak
osteoarthritisOpen Targets
0.10Suggestive
Miyoshi myopathyOpen Targets
0.07Suggestive
Decreased total leukocyte countOpen Targets
0.07Suggestive
attention deficit hyperactivity disorderOpen Targets
0.05Suggestive
colorectal carcinomaOpen Targets
0.05Suggestive
glioblastomaOpen Targets
0.05Suggestive
neoplasmOpen Targets
0.05Suggestive
hereditary attention deficit-hyperactivity disorderOpen Targets
0.04Suggestive
cancerOpen Targets
0.04Suggestive
viral diseaseOpen Targets
0.04Suggestive
Intervertebral disk degenerationOpen Targets
0.04Suggestive
schizophrenia 15Open Targets
0.04Suggestive
intellectual developmental disorder, autosomal dominant 69Open Targets
0.04Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets1
LORECIVIVINTPhase III
Dual specificity protein kinase CLK2 inhibitor
osteoarthritis, knee
Related Genes
LUC7L2Protein interaction94%BCLAF1Protein interaction87%RSRP1Protein interaction85%SRSF8Protein interaction82%RBBP6Protein interaction79%PAFAH1B3Protein interaction77%
Tissue Expression6 tissues
Ovary
100%
Liver
92%
Lung
71%
Bone Marrow
50%
Heart
41%
Brain
19%
Gene Interaction Network
Click a node to explore
CLK2LUC7L2BCLAF1RSRP1SRSF8RBBP6PAFAH1B3
PROTEIN STRUCTURE
Preparing viewer…
PDB6FYL · 1.95 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.27Highly Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.17 [0.11–0.27]
RankingsWhere CLK2 stands among ~20K protein-coding genes
  • #6,536of 20,598
    Most Researched72
  • #935of 17,882
    Most Constrained (LOEUF)0.27 · top 10%
Genes detectedCLK2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Modulation of the Wnt pathway through inhibition of CLK2 and DYRK1A by lorecivivint as a novel, potentially disease-modifying approach for knee osteoarthritis treatment.
PMID: 31132406
Osteoarthritis Cartilage · 2019
1.00
2
CLK2 Regulates the KEAP1/NRF2 and p53 Pathways to Suppress Ferroptosis in Colorectal Cancer.
PMID: 40882016
Cancer Res · 2025
0.90
3
CPSF6 regulates alternative polyadenylation and proliferation of cancer cells through phase separation.
PMID: 37777964
Cell Rep · 2023
0.80
4
CLK2 mediates IκBα-independent early termination of NF-κB activation by inducing cytoplasmic redistribution and degradation.
PMID: 38724505
Nat Commun · 2024
0.70
5
CLK2 Condensates Reorganize Nuclear Speckles and Induce Intron Retention.
PMID: 39119950
Adv Sci (Weinh) · 2024
0.60