HomeAboutRankingsData Sources
© 2026 GeneE
🧬
GeneE
10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
ⓘGeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
CLPS
colipase
Chromosome 6 · 6p21.31
NCBI Gene: 1208Ensembl: ENSG00000137392.10HGNC: HGNC:2085UniProt: A0A087WZW1
27PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
enzyme activator activitylipid metabolic processextracellular regionlipid catabolic processneurodegenerative diseaseceliac diseasedermatitis herpetiformishypothyroidism
✦AI Summary

Colipase (CLPS) is a lipid metabolic enzyme activator localized to the extracellular region with roles in digestive lipid processing. The protein functions as an essential cofactor for pancreatic lipase, facilitating triglyceride hydrolysis in the small intestine during fat digestion. Colipase contains an N-terminal fragment called enterostatin, which acts as a satiety signal to regulate food intake and energy homeostasis. At the molecular level, colipase operates in the lipid metabolic pathway by enhancing lipase substrate accessibility and catalytic efficiency at the lipid-water interface. The clinical significance of colipase relates to digestive lipid malabsorption: pancreatic insufficiency or colipase deficiency impairs dietary fat digestion, leading to steatorrhea and nutritional deficiencies. Enterostatin derived from colipase has been investigated as a potential therapeutic target for appetite modulation and obesity management, given its demonstrated satiety-promoting properties. Genetic or acquired colipase deficiency contributes to fat-soluble vitamin malabsorption (vitamins A, D, E, K), which has systemic health implications. Understanding colipase biology is relevant for managing pancreatic disorders, cystic fibrosis-related digestive complications, and potential appetite-regulation therapies, though additional clinical research is needed to establish enterostatin's therapeutic utility.

Sources cited
1
Colipase (CLPS) has enzyme activator activity, localizes to extracellular region, and participates in lipid metabolic process
PMID: NCBI/UniProt data
2
Enterostatin, derived from colipase, has biological activity as a satiety signal
PMID: UniProt
⚠Limited data available — This gene has 2 indexed publications. Summary and analysis may be incomplete.
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.38Weak
celiac diseaseOpen Targets
0.14Weak
dermatitis herpetiformisOpen Targets
0.10Suggestive
hypothyroidismOpen Targets
0.09Suggestive
myxedemaOpen Targets
0.07Suggestive
cystic fibrosis associated meconium ileusOpen Targets
0.07Suggestive
hypertriglyceridemia 2Open Targets
0.06Suggestive
familial hypercholesterolemiaOpen Targets
0.06Suggestive
thyroid hormone metabolism, abnormal, 2Open Targets
0.05Suggestive
Combined hyperlipidemiaOpen Targets
0.05Suggestive
sitosterolemia 2Open Targets
0.05Suggestive
pancreatic triacylglycerol lipase deficiencyOpen Targets
0.05Suggestive
homozygous familial hypercholesterolemiaOpen Targets
0.05Suggestive
hypercholesterolemia, autosomal dominant, 3Open Targets
0.04Suggestive
hyperlipidemia due to hepatic triglyceride lipase deficiencyOpen Targets
0.04Suggestive
hypercholesterolemia, autosomal dominant, type BOpen Targets
0.04Suggestive
Abnormality of the skeletal systemOpen Targets
0.03Suggestive
vertebral disorderOpen Targets
0.03Suggestive
chylomicron retention diseaseOpen Targets
0.03Suggestive
familial apolipoprotein C-II deficiencyOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
CELA3AProtein interaction99%CTRB1Protein interaction97%CTRLProtein interaction95%LIPFProtein interaction95%TBX22Protein interaction94%CTRB2Protein interaction94%
Tissue Expression6 tissues
Liver
100%
Ovary
48%
Lung
8%
Brain
0%
Heart
0%
Bone Marrow
0%
Gene Interaction Network
Click a node to explore
CLPSCELA3ACTRB1CTRLLIPFTBX22CTRB2
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt P04118
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
1.42LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.82 [0.49–1.42]
RankingsWhere CLPS stands among ~20K protein-coding genes
  • #12,532of 20,598
    Most Researched27
  • #14,667of 17,882
    Most Constrained (LOEUF)1.42
Genes detectedCLPS
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Chitinases and chitinase-like proteins in asthma.
PMID: 37031560
Semin Immunol · 2023
1.00
2
Mutations in the clpS Gene of Riemerella anatipestifer Affect Stress Response and Bacterial Virulence.
PMID: 41283912
Curr Microbiol · 2025
0.90
3
The Collaborative Longitudinal Personality Disorders Study (CLPS): overview and implications.
PMID: 16274278
J Pers Disord · 2005
0.80
4
Is human compositionality meta-learned?
PMID: 39311519
Behav Brain Sci · 2024
0.70
5
Collagen-Like Peptide Bioconjugates.
PMID: 28125203
Bioconjug Chem · 2017
0.60