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10 sources retrieved Β· Most recent: April 2026 Β· Index updated 14 days ago
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CRYBA4
crystallin beta A4
Chromosome 22 Β· 22q12.1
NCBI Gene: 1413Ensembl: ENSG00000196431.4HGNC: HGNC:2396UniProt: A0A097PIJ6
30PubMed Papers
21Diseases
0Drugs
6Pathogenic Variants
CLINICAL
OMIM Disease Gene
DATA QUALITY
βœ“ Experimental GO Evidenceβœ“ Swiss-Prot Reviewed
visual perceptioncamera-type eye developmentidentical protein bindingprotein bindingcataractearly-onset non-syndromic cataractearly-onset zonular cataractCataract-microcornea syndrome
✦AI Summary

CRYBA4 encodes crystallin beta A4, a dominant structural protein of the vertebrate eye lens essential for lens transparency 1. As a member of the beta-crystallin family, CRYBA4 maintains lens clarity through precise protein-protein interactions, particularly with CRYBB2, and is expressed from bidirectional promoters with CRYBB1 during lens fiber differentiation 2. CRYBA4 is located on chromosome 22.2-q13.1 3. Mutations in CRYBA4 cause autosomal dominant congenital cataracts through protein misfolding and reduced monomer stability. The pathogenic c.317T>C mutation (Phe94Ser) destabilizes the crystallin monomer, impairing critical lens protein associations 1. A c.225G>T mutation (Gly64Trp) associates with congenital cataract and microcornea 4. Beyond cataracts, CRYBA4 variants link to microphthalmia, with the Leu69Pro mutation disrupting beta-sheet structure 1. Genetically, CRYBA4 polymorphisms contribute to high myopia susceptibility. The rs2009066 SNP showed significant association with high myopia in Chinese populations (meta-analysis P=1.54e-5, OR=1.41) 56. Additionally, CRYBA4 expression responds to mechanical stress and estrogen signaling in tendon cells, suggesting broader roles beyond the eye 7. CRYBA4 expression increases in male diabetic retinas, indicating potential involvement in diabetic retinopathy pathogenesis 8.

Sources cited
1
CRYBA4 is a cataract gene; mutations cause protein misfolding and reduced stability; associated with microphthalmia
PMID: 16960806
2
CRYBA4 chromosomal localization to 22q11.2-q13.1
PMID: 1424806
3
CRYBA4 rs2009066 SNP associated with high myopia susceptibility
PMID: 22792142
4
Meta-analysis confirming rs2009066 and rs2071861 in CRYBA4 as genetic biomarkers for high myopia
PMID: 41151778
5
Novel c.225G>T (Gly64Trp) CRYBA4 mutation associated with congenital cataract and microcornea
PMID: 20577656
6
CRYBA4 and CRYBB1 simultaneously transcribed from bidirectional promoters during lens fiber differentiation
PMID: 30646012
7
CRYBA4 expression responds to mechanical stress and estrogen in tendon cells
PMID: 29683234
8
CRYBA4 expression increased in male diabetic retinas, relevant to diabetic retinopathy
PMID: 39354039
Disease Associationsβ“˜21
cataractOpen Targets
0.67Moderate
early-onset non-syndromic cataractOpen Targets
0.62Moderate
early-onset zonular cataractOpen Targets
0.48Moderate
cataract - microcornea syndromeOpen Targets
0.37Weak
Cataract-microcornea syndromeOpen Targets
0.37Weak
genetic disorderOpen Targets
0.19Weak
alcohol drinkingOpen Targets
0.16Weak
adverse effectOpen Targets
0.11Weak
infectious arthritisOpen Targets
0.11Weak
Abnormal nasolacrimal system morphologyOpen Targets
0.10Suggestive
Abnormality of the integumentOpen Targets
0.10Suggestive
frozen shoulderOpen Targets
0.10Suggestive
mixed connective tissue diseaseOpen Targets
0.10Suggestive
mathematical abilityOpen Targets
0.09Suggestive
autoimmune disorder of musculoskeletal systemOpen Targets
0.08Suggestive
color vision disorderOpen Targets
0.08Suggestive
Abnormality of refractionOpen Targets
0.08Suggestive
invasive mechanical ventilationOpen Targets
0.08Suggestive
neuroendocrine neoplasmOpen Targets
0.08Suggestive
male reproductive organ cancerOpen Targets
0.08Suggestive
Cataract 23, multiple typesUniProt
Pathogenic Variants6
NM_001886.3(CRYBA4):c.220T>C (p.Tyr74His)Pathogenic
Early-onset non-syndromic cataract
β˜…β˜†β˜†β˜†2025β†’ Residue 74
NM_001886.3(CRYBA4):c.277T>C (p.Ser93Pro)Likely pathogenic
Cataract 23
β˜…β˜†β˜†β˜†2021β†’ Residue 93
NM_001886.3(CRYBA4):c.198_200del (p.Gln66_Tyr67delinsHis)Likely pathogenic
Cataract 23
β˜…β˜†β˜†β˜†2020β†’ Residue 66
NM_001886.3(CRYBA4):c.190G>T (p.Gly64Trp)Pathogenic
Cataract 23
β˜†β˜†β˜†β˜†2017β†’ Residue 64
NM_001886.3(CRYBA4):c.281T>C (p.Phe94Ser)Pathogenic
Cataract 23
β˜†β˜†β˜†β˜†2006β†’ Residue 94
NM_001886.3(CRYBA4):c.206T>C (p.Leu69Pro)Pathogenic
Cataract 23
β˜†β˜†β˜†β˜†2006β†’ Residue 69
View on ClinVar β†—
Related Genes
CRYBB2Shared pathway100%CRYABProtein interaction91%GJA8Protein interaction86%GJA3Protein interaction79%BFSP1Protein interaction75%CRYAAProtein interaction75%
Tissue Expression6 tissues
Liver
100%
Brain
75%
Lung
50%
Ovary
0%
Heart
0%
Bone Marrow
0%
Gene Interaction Network
Click a node to explore
CRYBA4CRYBB2CRYABGJA8GJA3BFSP1CRYAA
PROTEIN STRUCTURE
Preparing viewer…
PDB3LWK Β· 1.70 Γ… Β· X-ray
View on RCSB β†—
Constraintβ“˜
LOEUFβ“˜
1.24LoF Tolerant
pLIβ“˜
0.00Tolerant
Observed/Expected LoF0.91 [0.68–1.24]
RankingsWhere CRYBA4 stands among ~20K protein-coding genes
  • #11,894of 20,598
    Most Researched30
  • #3,428of 5,498
    Most Pathogenic Variants6
  • #13,053of 17,882
    Most Constrained (LOEUF)1.24
Genes detectedCRYBA4
Sources retrieved10 papers
Response timeβ€”
πŸ“„ Sources
10β–Ό
1
CRYBA4, a novel human cataract gene, is also involved in microphthalmia.
PMID: 16960806
Am J Hum Genet Β· 2006
1.00
2
Localization of the beta A4-crystallin gene (CRYBA4) on human chromosome 22 in the region q11.2-->q13.1.
PMID: 1424806
Cytogenet Cell Genet Β· 1992
0.90
3
Association of high myopia with crystallin beta A4 (CRYBA4) gene polymorphisms in the linkage-identified MYP6 locus.
PMID: 22792142
PLoS One Β· 2012
0.80
4
Genetic associations of high myopia.
PMID: 41151778
Br J Ophthalmol Β· 2026
0.70
5
Sex differences in the development of experimental diabetic retinopathy.
PMID: 39354039
Sci Rep Β· 2024
0.60