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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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EPHB3
EPH receptor B3
Chromosome 3 · 3q27.1
NCBI Gene: 2049Ensembl: ENSG00000182580.4HGNC: HGNC:3394UniProt: P54753
64PubMed Papers
20Diseases
1Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
KinaseReceptor
CLINICAL
FDA Approved Target
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingplasma membraneephrin receptor signaling pathwaycell migrationmedullary thyroid gland carcinomaneoplasmthyroid neoplasmnon-small cell lung carcinoma
✦AI Summary

EPHB3 is a receptor tyrosine kinase mediating bidirectional signaling through transmembrane ephrin-B ligands, functioning as a key regulator of developmental processes and tissue homeostasis. Primary functions include axon guidance, dendritic spine development, angiogenesis, and intestinal epithelium differentiation 1. In the intestinal epithelium, EPHB3 regulates Paneth cell localization and crypt symmetry during regeneration, with WNT4 promoting symmetric fission through EphB3-mediated positioning 2. Mechanistically, EPHB3 controls cell-cell adhesion and intercellular communication. In CNS inflammation, microglia-expressed ephrin-B3 signals through EphB3 on astrocytes to promote proinflammatory responses in experimental autoimmune encephalomyelitis, with CNS-penetrant EphB3 inhibitors suppressing these pathological interactions 3. In fibrosis, soluble ephrin-B2 generated by ADAM10 shedding activates fibroblasts via EphB3 signaling, promoting myofibroblast activation and organ fibrosis 4. Clinical significance: EPHB3 functions as a tumor suppressor in colorectal cancer through transcriptional enhancer regulation involving Wnt/β-catenin and Notch signaling; enhancer decommissioning causes EPHB3 silencing at the adenoma-carcinoma transition 1. Elevated EphB3 expression serves as a biomarker in 37% of colorectal cancer samples, with diagnostic potential alongside miR-3168 in serum exosomes 5. Additionally, EPHB3 participates in ferroptosis-related preeclampsia pathogenesis through ARID3A regulation 6.

Sources cited
1
Microglia-expressed ephrin-B3 signals through EphB3 on astrocytes to promote proinflammatory CNS responses; EphB3 inhibition ameliorates experimental autoimmune encephalomyelitis
PMID: 33888612
2
EPHB3 acts as a tumor/invasion suppressor in colorectal cancer through regulating intercellular adhesion; transcriptional enhancer dysfunction and low Notch activity cause EPHB3 silencing during adenoma-carcinoma transition
PMID: 24707046
3
Soluble ephrin-B2 shed via ADAM10 promotes myofibroblast activation and fibrosis through EphB3 receptor signaling in lung and skin tissues
PMID: 29058717
4
WNT4 promotes symmetric crypt fission by regulating EphB3 expression to correctly localize Paneth cells at the crypt base during intestinal epithelial regeneration
PMID: 39725925
5
High EphB3 expression detected in 37% of colorectal cancer samples; EphB3 and miR-3168 identified as potential biomarkers for colorectal cancer diagnosis and disease monitoring
PMID: 40790791
6
EPHB3 participates in ferroptosis-related preeclampsia pathogenesis through ARID3A-mediated transcriptional regulation
PMID: 39707003
7
EphB3 is a direct target of miR-149 in colorectal cancer; EphB3 knockdown suppresses cell proliferation, migration, invasion, and in vivo tumor growth
PMID: 28370854
Disease Associationsⓘ20
medullary thyroid gland carcinomaOpen Targets
0.52Moderate
neoplasmOpen Targets
0.41Moderate
thyroid neoplasmOpen Targets
0.39Weak
non-small cell lung carcinomaOpen Targets
0.39Weak
alcohol drinkingOpen Targets
0.38Weak
thyroid carcinomaOpen Targets
0.37Weak
lung cancerOpen Targets
0.35Weak
thyroid cancerOpen Targets
0.34Weak
neuroinflammatory disorderOpen Targets
0.29Weak
corneal neovascularizationOpen Targets
0.27Weak
Abnormality of limbsOpen Targets
0.21Weak
liver diseaseOpen Targets
0.21Weak
nerve plexus diseaseOpen Targets
0.19Weak
hypertensionOpen Targets
0.16Weak
adolescent idiopathic scoliosisOpen Targets
0.16Weak
breast cancerOpen Targets
0.12Weak
HematemesisOpen Targets
0.11Weak
age-related macular degenerationOpen Targets
0.10Weak
prostate cancerOpen Targets
0.10Weak
cancerOpen Targets
0.10Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets1
VANDETANIBApproved
Ephrin receptor inhibitor
Related Genes
EFNA1Protein interaction100%EFNA3Protein interaction100%EFNA4Protein interaction100%EFNB1Protein interaction100%EFNB2Protein interaction100%EFNB3Protein interaction100%
Tissue Expression6 tissues
Ovary
100%
Brain
56%
Lung
26%
Heart
23%
Liver
13%
Bone Marrow
11%
Gene Interaction Network
Click a node to explore
EPHB3EFNA1EFNA3EFNA4EFNB1EFNB2EFNB3
PROTEIN STRUCTURE
Preparing viewer…
PDB5L6O · 1.88 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.43Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.32 [0.24–0.43]
RankingsWhere EPHB3 stands among ~20K protein-coding genes
  • #7,262of 20,598
    Most Researched64
  • #991of 1,025
    FDA-Approved Drug Targets1
  • #2,357of 17,882
    Most Constrained (LOEUF)0.43 · top quartile
Genes detectedEPHB3
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Barcoded viral tracing of single-cell interactions in central nervous system inflammation.
PMID: 33888612
Science · 2021
1.00
2
Retraction.
PMID: 29399985
Cancer Sci · 2018
0.90
3
Silencing of the EPHB3 tumor-suppressor gene in human colorectal cancer through decommissioning of a transcriptional enhancer.
PMID: 24707046
Proc Natl Acad Sci U S A · 2014
0.80
4
ADAM10-mediated ephrin-B2 shedding promotes myofibroblast activation and organ fibrosis.
PMID: 29058717
Nat Med · 2017
0.70
5
WNT4 promotes the symmetric fission of crypt in radiation-induced intestinal epithelial regeneration.
PMID: 39725925
Cell Mol Biol Lett · 2024
0.60