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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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FBXW2
F-box and WD repeat domain containing 2
Chromosome 9 · 9q33.2
NCBI Gene: 26190Ensembl: ENSG00000119402.18HGNC: HGNC:13608UniProt: B4DT60
60PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingproteolysisregulation of cell cycle processSCF-dependent proteasomal ubiquitin-dependent protein catabolic processHypercholesterolemiapoisoninglung cancerneoplasm
✦AI Summary

FBXW2 (F-box and WD repeat domain containing 2) functions as a substrate recognition component of SCF-type E3 ubiquitin ligase complexes, directing multiple oncogenic proteins for proteasomal degradation 1. The protein acts as a broad-spectrum tumor suppressor across multiple cancer types by targeting distinct substrates: NF-κB p65 in breast cancer 1, EGFR in prostate cancer 2, β-catenin in lung and gastric cancers 34, Moesin in breast cancer 5, WASL in gastric cancer 6, and MSX2 in breast cancer 7. Mechanistically, FBXW2 binds to substrates through specific degron motifs and catalyzes their ubiquitination in cooperation with E2 enzyme UBE2D2 8, leading to their degradation and suppression of oncogenic signaling pathways including Wnt/β-catenin, NF-κB, and EGF-EGFR pathways. Clinically, FBXW2 downregulation is significantly associated with poor prognosis in breast, lung, prostate, and gastric cancers 136. FBXW2 overexpression inhibits tumor growth, metastasis, cancer stemness, and chemotherapy resistance in multiple cancer models 126, making it a promising therapeutic target for cancer treatment.

Sources cited
1
FBXW2 ubiquitinates and degrades NF-κB p65, suppressing breast cancer stemness, tumorigenesis, and paclitaxel resistance
PMID: 34465889
2
FBXW2 functions as E3 ligase for EGFR ubiquitination and degradation in prostate cancer, inhibiting proliferation and metastasis
PMID: 35499593
3
FBXW2 promotes β-catenin ubiquitylation and degradation in lung cancer, suppressing migration and metastasis
PMID: 30918250
4
FBXW2 targets WASL for ubiquitin-mediated degradation in gastric cancer; FBXW2 downregulation is associated with poor survival
PMID: 40721413
5
FBXW2 expression is downregulated in gastric cancer tissues with inverse correlation to β-catenin expression
PMID: 40225854
6
FBXW2 suppresses breast cancer by targeting Moesin for proteasomal degradation, restricting AKT-Moesin-SKP2 axis
PMID: 37736741
7
UBE2D2 is the E2 ubiquitin-conjugating enzyme required for FBXW2-mediated substrate ubiquitination
PMID: 18703417
8
FBXW2 promotes MSX2 ubiquitylation and degradation, regulating SOX2 expression and cancer stem cell properties
PMID: 31548378
Disease Associationsⓘ20
HypercholesterolemiaOpen Targets
0.27Weak
poisoningOpen Targets
0.10Suggestive
lung cancerOpen Targets
0.09Suggestive
neoplasmOpen Targets
0.09Suggestive
posterior cortical atrophyOpen Targets
0.08Suggestive
response to xenobiotic stimulusOpen Targets
0.08Suggestive
breast cancerOpen Targets
0.08Suggestive
gastric cancerOpen Targets
0.06Suggestive
eosinophil peroxidase deficiencyOpen Targets
0.05Suggestive
obesityOpen Targets
0.05Suggestive
immunodeficiency 88Open Targets
0.04Suggestive
neutropenia, severe congenital, 2, autosomal dominantOpen Targets
0.04Suggestive
nonimmune chronic idiopathic neutropenia of adultsOpen Targets
0.04Suggestive
linear and whorled nevoid hypermelanosisOpen Targets
0.04Suggestive
cancerOpen Targets
0.04Suggestive
atherosclerosisOpen Targets
0.04Suggestive
chronic myeloproliferative disorderOpen Targets
0.04Suggestive
chronic myelogenous leukemiaOpen Targets
0.04Suggestive
neutropenia, severe congenital, 1, autosomal dominantOpen Targets
0.04Suggestive
metabolic diseaseOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
SKP1Protein interaction100%CAND1Protein interaction100%BTRCProtein interaction100%CUL2Protein interaction100%FBXW7Protein interaction100%FBXW4Protein interaction99%
Tissue Expression6 tissues
Lung
100%
Liver
88%
Heart
84%
Brain
83%
Bone Marrow
78%
Ovary
60%
Gene Interaction Network
Click a node to explore
FBXW2SKP1CAND1BTRCCUL2FBXW7FBXW4
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q9UKT8
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
0.42Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.26 [0.16–0.42]
RankingsWhere FBXW2 stands among ~20K protein-coding genes
  • #7,659of 20,598
    Most Researched60
  • #2,248of 17,882
    Most Constrained (LOEUF)0.42 · top quartile
Genes detectedFBXW2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Ubiquitination of NF-κB p65 by FBXW2 suppresses breast cancer stemness, tumorigenesis, and paclitaxel resistance.
PMID: 34465889
Cell Death Differ · 2022
1.00
2
FBXW2 inhibits prostate cancer proliferation and metastasis via promoting EGFR ubiquitylation and degradation.
PMID: 35499593
Cell Mol Life Sci · 2022
0.90
3
FBXW2 suppresses migration and invasion of lung cancer cells via promoting β-catenin ubiquitylation and degradation.
PMID: 30918250
Nat Commun · 2019
0.80
4
FOXP2 suppresses gastric cancer progression by transcriptionally repressing FBXW2 via WASL degradation.
PMID: 40721413
Cell Death Discov · 2025
0.70
5
FBXW2 inhibits the progression of gastric cancer via promoting β-catenin ubiquitylation.
PMID: 40225854
Int J Med Sci · 2025
0.60