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50 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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FCGR2A
Fc gamma receptor IIa
Chromosome 1 · 1q23.3
NCBI Gene: 2212Ensembl: ENSG00000143226.16HGNC: HGNC:3616UniProt: A0A8V8TPS4
534PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
RESEARCH IMPACT
Highly StudiedTrending
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
plasma membraneprotein bindingIgG bindingantibody-dependent cellular cytotoxicityulcerative colitissystemic lupus erythematosusinflammatory bowel diseaserheumatoid arthritis
✦AI Summary

FCGR2A encodes Fc gamma receptor IIa, a low-affinity IgG receptor expressed on the plasma membrane that binds the Fc region of immunoglobulin G and initiates cellular immune responses 1. The receptor promotes phagocytosis of opsonized antigens and activates cellular FcγRIIA on platelets and monocytes to propagate immune responses 1. FCGR2A is expressed across diverse immune contexts, including intestinal immune cells where it functions in IgG sensing 2, and myeloid cells in pancreatic cancer where expression increases during disease progression 3. Disease relevance is substantial. The FCGR2A H131R polymorphism significantly associates with Kawasaki disease susceptibility in Asian populations 4, and FCGR2A variants affect binding affinity for IgG, modulating inflammation in ulcerative colitis through commensal-IgG immune complexes that engage gut macrophages to induce IL-1β production and type 17 immunity 5. FCGR2A is also implicated in Takayasu arteritis 6 and identified as a hub biomarker for post-transplant renal fibrosis with positive correlation to immune cell infiltration 7. Conversely, FCGR2A rs1801274 shows no significant association with pneumonia susceptibility 8. These findings establish FCGR2A as a critical mediator of antibody-dependent immune activation with important roles in inflammatory and autoimmune diseases, particularly those involving dysregulated IgG responses.

Sources cited
1
FcγRIIA binds IgG and activates immune responses on platelets and monocytes; relevant to pathogenic antibody-mediated disease
PMID: 28416511
2
FCGR2A expression in intestinal cells; IgG sensing function in intestinal immune response
PMID: 34497389
3
FCGR2A expression increases in myeloid cells during pancreatic adenosquamous carcinoma progression
PMID: 34326696
4
FCGR2A H131R polymorphism associates with Kawasaki disease susceptibility in Asian populations
PMID: 26125827
5
FCGR2A variants affect IgG binding affinity; modulate gut inflammation in ulcerative colitis through macrophage activation and IL-1β production
PMID: 30876876
6
FCGR2A implicated as genetic risk factor in Takayasu arteritis
PMID: 25405827
7
FCGR2A identified as hub biomarker for post-transplant renal fibrosis with correlation to immune cell activity
PMID: 38378674
8
FCGR2A rs1801274 shows no significant association with pneumonia susceptibility
PMID: 32252656
Disease Associationsⓘ20
ulcerative colitisOpen Targets
0.55Moderate
systemic lupus erythematosusOpen Targets
0.53Moderate
inflammatory bowel diseaseOpen Targets
0.53Moderate
rheumatoid arthritisOpen Targets
0.44Moderate
mucocutaneous lymph node syndromeOpen Targets
0.41Moderate
ulcerative proctosigmoiditisOpen Targets
0.41Moderate
Crohn's diseaseOpen Targets
0.38Weak
cutaneous LeishmaniasisOpen Targets
0.37Weak
ankylosing spondylitisOpen Targets
0.37Weak
colitisOpen Targets
0.34Weak
enteritisOpen Targets
0.34Weak
Parkinson diseaseOpen Targets
0.33Weak
intestinal diseaseOpen Targets
0.33Weak
schizophreniaOpen Targets
0.32Weak
peripheral neuropathyOpen Targets
0.32Weak
cystic fibrosisOpen Targets
0.24Weak
psoriasisOpen Targets
0.15Weak
sclerosing cholangitisOpen Targets
0.14Weak
Takayasu arteritisOpen Targets
0.11Weak
neoplasmOpen Targets
0.11Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
CD8AProtein interaction100%GP6Protein interaction100%APCSProtein interaction99%CRPProtein interaction99%FCARProtein interaction99%IFNGProtein interaction99%
Tissue Expression6 tissues
Lung
100%
Bone Marrow
28%
Brain
20%
Liver
8%
Heart
8%
Ovary
8%
Gene Interaction Network
Click a node to explore
FCGR2ACD8AGP6APCSCRPFCARIFNG
PROTEIN STRUCTURE
Preparing viewer…
PDB3RY4 · 1.50 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.92LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.62 [0.43–0.92]
RankingsWhere FCGR2A stands among ~20K protein-coding genes
  • #472of 20,598
    Most Researched534 · top 5%
  • #8,469of 17,882
    Most Constrained (LOEUF)0.92
Genes detectedFCGR2A
Sources retrieved50 papers
Response time—
📄 Sources
50▼
1
Cells of the human intestinal tract mapped across space and time.
PMID: 34497389
Nature · 2021
1.00
2
Heparin-induced thrombocytopenia.
PMID: 28416511
Blood · 2017
0.90
3
FCGR2A and FCGR3A Genotypes in Human Immunodeficiency Virus Mother-to-Child Transmission.
PMID: 26613093
Open Forum Infect Dis · 2015
0.88
4
Identifying prioritization of therapeutic targets for ankylosing spondylitis: a multi-omics Mendelian randomization study.
PMID: 39707330
J Transl Med · 2024
0.82
5
Single-cell transcriptomics reveals heterogeneous progression and EGFR activation in pancreatic adenosquamous carcinoma.
PMID: 34326696
Int J Biol Sci · 2021
0.80