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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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GJD3
gap junction protein delta 3
Chromosome 17 · 17q21.2
NCBI Gene: 125111Ensembl: ENSG00000183153.7HGNC: HGNC:19147UniProt: Q8N144
11PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
negative regulation of cell communication by electrical coupling involved in cardiac conductionAV node cell to bundle of His cell communication by electrical couplingcell communication involved in cardiac conductionprotein bindingVaricose veinsvein disorderlymphatic system diseaseneurodegenerative disease
✦AI Summary

GJD3 encodes gap junction protein delta 3, also known as connexin 31.9 (Cx31.9) in humans or connexin 30.2 (Cx30.2) in mice, which forms transmembrane channels that allow low molecular weight materials to diffuse between adjacent cells 1. The protein plays a crucial role in cardiac conduction, specifically in atrioventricular node (AVN) function, where it facilitates electrical coupling between AV node cells and bundle of His cells 2. GJD3 is expressed in cardiac tissue beginning at embryonic day 12.5 and labels AVN cardiomyocytes and cardiac endothelial cells 2. In the inner ear, GJD3 is expressed in the organ of Corti and vestibular organs, particularly in the tectorial membrane and hair cell regions 1. Disease relevance includes associations with familial Meniere's disease, where rare missense variants may interfere with connexin assembly and gap junction formation 1. A protective missense variant (p.Pro59Thr) enriched in the Finnish population is associated with reduced varicose vein risk, suggesting GJD3 as a potential therapeutic target for venous disease 3. The gene has also been implicated in familial atrioventricular nodal reentrant tachycardia through calcium signaling pathways 4.

Sources cited
1
GJD3 encodes connexin 31.9 and is expressed in inner ear structures; rare variants associated with familial Meniere's disease
PMID: 39815343
2
GJD3 functions in atrioventricular node, expressed from E12.5, labels AVN cardiomyocytes and endothelial cells
PMID: 30765799
3
Protective missense variant p.Pro59Thr in Finnish population reduces varicose vein risk
PMID: 36653477
4
GJD3 implicated in familial AVNRT through calcium signaling pathways
PMID: 35924220
⚠Limited data available — This gene has 4 indexed publications. Summary and analysis may be incomplete.
Disease Associationsⓘ20
Varicose veinsOpen Targets
0.39Weak
vein disorderOpen Targets
0.31Weak
lymphatic system diseaseOpen Targets
0.25Weak
neurodegenerative diseaseOpen Targets
0.24Weak
Romano-Ward syndromeOpen Targets
0.10Weak
familial atrial fibrillationOpen Targets
0.10Suggestive
Familial progressive cardiac conduction defectOpen Targets
0.09Suggestive
Brugada syndromeOpen Targets
0.09Suggestive
Familial short QT syndromeOpen Targets
0.08Suggestive
atrial fibrillationOpen Targets
0.08Suggestive
long QT syndrome 11Open Targets
0.08Suggestive
Arrhythmogenic right ventricular dysplasiaOpen Targets
0.08Suggestive
Brugada syndrome 9Open Targets
0.08Suggestive
hypertrophic cardiomyopathyOpen Targets
0.08Suggestive
Rare familial disorder with hypertrophic cardiomyopathyOpen Targets
0.08Suggestive
Wolff-Parkinson-White SyndromeOpen Targets
0.07Suggestive
long QT syndrome 10Open Targets
0.07Suggestive
dilated cardiomyopathyOpen Targets
0.07Suggestive
sinoatrial node dysfunction and deafnessOpen Targets
0.07Suggestive
familial sick sinus syndromeOpen Targets
0.07Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
TJP1Protein interaction100%GJA3Protein interaction91%GJA8Protein interaction91%GJB2Protein interaction91%GJB4Protein interaction74%GJB1Protein interaction73%
Tissue Expression6 tissues
Lung
100%
Liver
67%
Brain
50%
Heart
0%
Bone Marrow
0%
Ovary
0%
Gene Interaction Network
Click a node to explore
GJD3TJP1GJA3GJA8GJB2GJB4GJB1
PROTEIN STRUCTURE
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AlphaFoldAI-predicted · UniProt Q8N144
View on AlphaFold ↗
RankingsWhere GJD3 stands among ~20K protein-coding genes
  • #16,766of 20,598
    Most Researched11
Genes detectedGJD3
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
School-based interventions for elementary school students with ADHD.
PMID: 25220080
Child Adolesc Psychiatr Clin N Am · 2014
1.00
2
A rare haplotype of the GJD3 gene segregating in familial Meniere's disease interferes with connexin assembly.
PMID: 39815343
Genome Med · 2025
0.90
3
Using Gjd3-CreEGFP mice to examine atrioventricular node morphology and composition.
PMID: 30765799
Sci Rep · 2019
0.80
4
Spatial Transcriptomics Shows a Distinctive Tumour Microenvironment in the Invasive Versus Premalignant Portion of Early Cutaneous Squamous Cell Carcinoma.
PMID: 40462294
Exp Dermatol · 2025
0.70
5
Presenilin-1-Derived Circular RNAs: Neglected Epigenetic Regulators with Various Functions in Alzheimer's Disease.
PMID: 37759801
Biomolecules · 2023
0.60