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GeneE
26 sources retrieved Β· Most recent: April 2026 Β· Index updated 14 days ago
β“˜GeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
GNB3
G protein subunit beta 3
Chromosome 12 Β· 12p13.31
NCBI Gene: 2784Ensembl: ENSG00000111664.11HGNC: HGNC:4400UniProt: E9PCP0
429PubMed Papers
21Diseases
0Drugs
2Pathogenic Variants
FUNCTIONAL ROLE
Hub Gene
RESEARCH IMPACT
Highly Studied
CLINICAL
OMIM Disease Gene
DATA QUALITY
βœ“ Experimental GO Evidenceβœ“ Swiss-Prot Reviewed
regulation of feeding behaviorregulation of locomotion involved in locomotory behaviorprotein bindingGTPase bindingcongenital stationary night blindness 1Hmyopiaopen-angle glaucomarefractive error
✦AI Summary

GNB3 encodes the G protein subunit beta 3, a critical component of heterotrimeric G proteins essential for transmembrane signaling. As part of the G protein complex, GNB3 facilitates GTPase activity, GDP-GTP exchange, and G protein-effector interactions 1. The protein regulates diverse cellular processes including glucose metabolism, hormone signaling, blood pressure control, and fat cell differentiation 1. GNB3's primary disease association is congenital stationary night blindness type 1H, resulting from pathogenic variants disrupting phototransduction in retinal cells 1. Additionally, GNB3 expression marks medullary thymic epithelial cells in thymic epithelial tumors, potentially predicting tumor immunological behavior 2. The common C825T polymorphism (rs5443) shows associations with metabolic and cardiovascular phenotypes. The TT genotype correlates with increased obesity risk and elevated leptin levels 3. Gene-environment interaction studies reveal that in physically inactive African Americans, the 825T allele associates with 23% greater obesity prevalence, while active carriers show 20% lower obesity risk 4. The maternal 825T variant also increases pre-eclampsia risk 5. However, GNB3 polymorphisms show no significant association with antipsychotic-induced weight gain 6 or endurance athlete status 7. The variant may influence triptan treatment response in cluster headache patients 8.

Sources cited
1
GNB3 pathogenic variants cause congenital stationary night blindness type 1H and are involved in phototransduction
PMID: 40013354
2
GNB3 expression marks medullary thymic epithelial cells in thymic epithelial tumors and may predict immunological behavior
PMID: 36115836
3
GNB3 C825T TT genotype associates with increased obesity risk and leptin levels in Saudi population
PMID: 29937877
4
GNB3 825T allele shows gene-environment interaction with physical activity: associated with lower obesity in active individuals and higher obesity in inactive African Americans
PMID: 17299380
5
Maternal GNB3 C825T polymorphism is associated with increased pre-eclampsia risk
PMID: 33368205
6
GNB3 C825T polymorphism shows no significant association with antipsychotic-induced weight gain in meta-analysis
PMID: 18793692
7
GNB3 rs5443 polymorphism shows no significant association with endurance athlete status
PMID: 38753016
8
GNB3 rs5443 T allele may influence triptan treatment response in cluster headache patients
PMID: 31768945
Disease Associationsβ“˜21
congenital stationary night blindness 1HOpen Targets
0.64Moderate
myopiaOpen Targets
0.31Weak
open-angle glaucomaOpen Targets
0.29Weak
refractive errorOpen Targets
0.29Weak
HypermetropiaOpen Targets
0.26Weak
Abnormality of refractionOpen Targets
0.22Weak
AstigmatismOpen Targets
0.20Weak
eye diseaseOpen Targets
0.20Weak
genetic disorderOpen Targets
0.19Weak
essential hypertension, geneticOpen Targets
0.12Weak
Retinal dystrophyOpen Targets
0.12Weak
irritable bowel syndromeOpen Targets
0.10Suggestive
depressive disorderOpen Targets
0.08Suggestive
obesityOpen Targets
0.07Suggestive
pancreatic adenocarcinomaOpen Targets
0.07Suggestive
hypertensionOpen Targets
0.07Suggestive
strokeOpen Targets
0.05Suggestive
Fabry diseaseOpen Targets
0.05Suggestive
cancerOpen Targets
0.04Suggestive
type 2 diabetes mellitusOpen Targets
0.04Suggestive
Night blindness, congenital stationary, 1HUniProt
Pathogenic Variants2
NM_002075.4(GNB3):c.1017G>A (p.Trp339Ter)Pathogenic
Congenital stationary night blindness 1H
β˜†β˜†β˜†β˜†2016β†’ Residue 339
NM_002075.4(GNB3):c.170_172del (p.Lys57del)Pathogenic
Congenital stationary night blindness 1H
β˜†β˜†β˜†β˜†2016β†’ Residue 57
View on ClinVar β†—
Related Genes
GNG13Protein interaction100%GNG5Protein interaction100%GNG12Protein interaction100%PDCLProtein interaction100%GNASProtein interaction98%PLCB2Protein interaction98%
Tissue Expression6 tissues
Ovary
100%
Heart
77%
Bone Marrow
27%
Lung
15%
Brain
11%
Liver
6%
Gene Interaction Network
Click a node to explore
GNB3GNG13GNG5GNG12PDCLGNASPLCB2
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted Β· UniProt P16520
View on AlphaFold β†—
Constraintβ“˜
LOEUFβ“˜
1.07LoF Tolerant
pLIβ“˜
0.00Tolerant
Observed/Expected LoF0.79 [0.60–1.07]
RankingsWhere GNB3 stands among ~20K protein-coding genes
  • #650of 20,598
    Most Researched429 Β· top 5%
  • #4,200of 5,498
    Most Pathogenic Variants2
  • #10,833of 17,882
    Most Constrained (LOEUF)1.07
Genes detectedGNB3
Sources retrieved26 papers
Response timeβ€”
πŸ“„ Sources
26β–Ό
1
Monogenic Retinal Diseases Associated With Genes Encoding Phototransduction Proteins: A Review.
PMID: 40013354
Clin Exp Ophthalmol Β· 2025
1.00
2
Genetic association studies on gender- and age-related phenotypes: the case of GNB3 gene.
PMID: 12658009
J Hypertens Β· 2003
0.90
3
GNB3 gene C825T and ACE gene I/D polymorphisms in essential hypertension in a Kazakh genetic isolate.
PMID: 15042113
J Hum Hypertens Β· 2004
0.84
4
The immune landscape of human thymic epithelial tumors.
PMID: 36115836
Nat Commun Β· 2022
0.80
5
GNB3 gene c.825C>T polymorphism and performance parameters in professional basketball players.
PMID: 24901079
Acta Physiol Hung Β· 2014
0.76