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50 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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IL10
interleukin 10
Chromosome 1 · 1q32.1
NCBI Gene: 3586Ensembl: ENSG00000136634.7HGNC: HGNC:5962UniProt: A0A286YEX3
3,486PubMed Papers
20Diseases
0Drugs
2Pathogenic Variants
FUNCTIONAL ROLE
Hub Gene
RESEARCH IMPACT
Highly StudiedLandmark GeneTrending
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein dimerization activitypositive regulation of B cell apoptotic processregulation of gene expressionnegative regulation of B cell proliferationCrohn's diseaseinflammatory bowel diseaseulcerative colitisIL10-related early-onset inflammatory bowel disease
✦AI Summary

IL10 is a major immune regulatory cytokine that functions as a potent anti-inflammatory mediator acting on multiple immune cell types 1. Mechanistically, IL10 binds to a heterotetrameric receptor (IL10RA/IL10RB) triggering JAK1-mediated phosphorylation and STAT3 activation, which translocates to the nucleus to drive expression of anti-inflammatory mediators 23. IL10 targets antigen-presenting cells including macrophages and monocytes, inhibiting their production of pro-inflammatory cytokines (TNF, IL-6, IL-8, GM-CSF, G-CSF, IL-1α/β) while reducing MHC-II and co-stimulatory molecule expression to suppress T cell activation 4567. IL10 also maintains tissue homeostasis during infection and inflammation through upregulation of innate immunity and promotion of tissue repair 1. Regulatory B cell subsets, particularly plasma cells, produce IL10 to mediate suppressive immune functions during autoimmune and infectious diseases 8. In disease contexts, IL10 plays complex roles: CD169+ macrophages produce IL10 to mitigate sepsis mortality 9, while IL10 can alternatively promote immunosuppression in glioblastoma microenvironments 10. Elevated IL10 serves as a biomarker for primary CNS lymphoma diagnosis 11, and IL10 polymorphisms associate with community-acquired pneumonia susceptibility 12.

Sources cited
1
IL-10 maintains tissue homeostasis during infection and inflammation through restriction of excessive inflammatory responses and promotion of tissue repair
PMID: 30995504
2
IL-10 binds to heterotetrameric receptor (IL10RA/IL10RB) leading to JAK1-mediated signaling
PMID: 16982608
3
STAT3 translocates to nucleus to drive expression of anti-inflammatory mediators
PMID: 18025162
4
IL-10 inhibits pro-inflammatory cytokine release from macrophages and monocytes
PMID: 11564774
5
IL-10 inhibits production of pro-inflammatory cytokines including TNF and IL-6
PMID: 1940799
6
IL-10 inhibits cytokine production by antigen-presenting cells
PMID: 7512027
7
IL-10 reduces MHC-II and co-stimulatory molecule expression to inhibit T cell activation
PMID: 8144879
8
Regulatory plasma cells produce IL-10 to mediate suppressive immune functions in autoimmune and infectious diseases
PMID: 25978519
9
CD169+ macrophage-intrinsic IL-10 production mitigates mortality from sepsis
PMID: 37027482
10
IL-10 plays immunosuppressive roles in glioblastoma tumor microenvironment
PMID: 34349251
11
IL-10 measured in blood, CSF, and vitreous humor serves as a reliable diagnostic biomarker for primary CNS lymphoma
PMID: 38937027
12
IL-10 polymorphisms are associated with increased susceptibility to community-acquired pneumonia
PMID: 30920458
Disease Associationsⓘ20
Crohn's diseaseOpen Targets
0.63Moderate
inflammatory bowel diseaseOpen Targets
0.63Moderate
ulcerative colitisOpen Targets
0.59Moderate
IL10-related early-onset inflammatory bowel diseaseOpen Targets
0.57Moderate
type 1 diabetes mellitusOpen Targets
0.54Moderate
systemic lupus erythematosusOpen Targets
0.54Moderate
rheumatoid arthritisOpen Targets
0.49Moderate
Behcet's syndromeOpen Targets
0.48Moderate
ulcer diseaseOpen Targets
0.45Moderate
ulcerative proctosigmoiditisOpen Targets
0.45Moderate
Oral ulcerOpen Targets
0.43Moderate
colitisOpen Targets
0.40Moderate
cancerOpen Targets
0.40Weak
Autosomal recessive early-onset inflammatory bowel diseaseOpen Targets
0.39Weak
type 2 diabetes mellitusOpen Targets
0.39Weak
enteritisOpen Targets
0.38Weak
psoriasisOpen Targets
0.37Weak
autoimmune diseaseOpen Targets
0.37Weak
proctitisOpen Targets
0.37Weak
sclerosing cholangitisOpen Targets
0.37Weak
Pathogenic Variants2
NC_000001.11:g.206773552T>CPathogenic
Leprosy, susceptibility to, 1|Hepatitis C virus, susceptibility to
★☆☆☆2025
NC_000001.11:g.206775286T>CPathogenic
Rheumatoid arthritis, progression of
☆☆☆☆2003
View on ClinVar ↗
Related Genes
IL23AProtein interaction100%IL1R2Protein interaction100%FOXP3Protein interaction98%FASLGProtein interaction98%ARG1Protein interaction98%CD1BProtein interaction98%
Tissue Expression6 tissues
Bone Marrow
100%
Lung
55%
Ovary
17%
Heart
16%
Liver
16%
Brain
11%
Gene Interaction Network
Click a node to explore
IL10IL23AIL1R2FOXP3FASLGARG1CD1B
PROTEIN STRUCTURE
Preparing viewer…
PDB2ILK · 1.60 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.71LoF Tolerant
pLIⓘ
0.48Tolerant
Observed/Expected LoF0.38 [0.21–0.71]
RankingsWhere IL10 stands among ~20K protein-coding genes
  • #13of 20,598
    Most Researched3,486 · top 1%
  • #4,178of 5,498
    Most Pathogenic Variants2
  • #5,454of 17,882
    Most Constrained (LOEUF)0.71
Genes detectedIL10
Sources retrieved50 papers
Response time—
📄 Sources
50▼
1
IL-10 Family Cytokines IL-10 and IL-22: from Basic Science to Clinical Translation.
PMID: 30995504
Immunity · 2019
1.00
2
Association between IL10 rs1800896 polymorphism and risk of pediatric asthma: A meta-analysis.
PMID: 37937689
Clin Respir J · 2023
0.92
3
Molecular diagnosis of primary CNS lymphoma in 2024 using MYD88
PMID: 38937027
Lancet Haematol · 2024
0.90
4
Pathobiont-driven antibody sialylation through IL-10 undermines vaccination.
PMID: 39680460
J Clin Invest · 2024
0.84
5
IL-10 in glioma.
PMID: 34349251
Br J Cancer · 2021
0.80