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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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PACRG
parkin coregulated
Chromosome 6 · 6q26
NCBI Gene: 135138Ensembl: ENSG00000112530.13HGNC: HGNC:19152UniProt: Q96M98
51PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
G protein-coupled receptor bindingactin bindingprotein bindingHsp70 protein bindingYoung adult-onset ParkinsonismobesityHereditary late-onset Parkinson diseasesmoking behavior
✦AI Summary

PACRG (parkin coregulated) is a multifunctional protein with distinct roles in ciliary motility and cellular signaling. As a microtubule inner protein (MIP), PACRG is essential for motile cilia beating, forming part of dynein-decorated doublet microtubules in cilia axonemes 1. PACRG binds directly to microtubules and alpha/beta-tubulin heterodimers with high affinity, bundling microtubules and forming branched aggregates 2. Structurally, PACRG adopts a helical repeat fold and forms complexes with MEIG1, facilitating axoneme formation through dual tubulin interactions 3. Beyond its ciliary functions, PACRG plays a protective role in cellular stress responses by suppressing cell death induced by unfolded proteins and facilitating inclusion body formation when proteasome function is inhibited 4. The protein also promotes TNF-induced NF-κB activation by interacting with the linear ubiquitin chain assembly complex (LUBAC), functionally replacing SHARPIN in this pathway 5. PACRG shares a bidirectional promoter with parkin and is co-regulated with it 6. Like parkin, PACRG is regulated by the ubiquitin-proteasomal system and is found in pathological features of Parkinsonian diseases, including Lewy bodies, suggesting potential involvement in neurodegeneration 7.

Sources cited
1
PACRG is a microtubule inner protein required for motile cilia beating
PMID: 36191189
2
PACRG directly binds microtubules and tubulin with high affinity, bundling microtubules
PMID: 18387367
3
PACRG has helical repeat fold, complexes with MEIG1, and facilitates axoneme formation
PMID: 33529594
4
PACRG suppresses cell death from unfolded proteins and facilitates inclusion formation
PMID: 14532270
5
PACRG promotes TNF-induced NF-κB activation via LUBAC interaction
PMID: 32019898
6
PACRG shares bidirectional promoter with parkin and is co-regulated
PMID: 12547187
7
PACRG is regulated by ubiquitin-proteasomal system and found in Parkinsonian pathology
PMID: 17590346
Disease Associationsⓘ20
Young adult-onset ParkinsonismOpen Targets
0.48Moderate
obesityOpen Targets
0.36Weak
Hereditary late-onset Parkinson diseaseOpen Targets
0.34Weak
smoking behaviorOpen Targets
0.33Weak
hypertensionOpen Targets
0.33Weak
alcohol drinkingOpen Targets
0.33Weak
type 2 diabetes mellitusOpen Targets
0.33Weak
diabetes mellitusOpen Targets
0.32Weak
Abnormality of the skeletal systemOpen Targets
0.32Weak
male reproductive system diseaseOpen Targets
0.31Weak
post-traumatic stress disorderOpen Targets
0.30Weak
ocular hypotensionOpen Targets
0.28Weak
Tietze syndromeOpen Targets
0.28Weak
benign digestive system neoplasmOpen Targets
0.27Weak
young-onset Parkinson diseaseOpen Targets
0.27Weak
diabetic neuropathyOpen Targets
0.27Weak
smoking initiationOpen Targets
0.27Weak
osteoarthritisOpen Targets
0.26Weak
central nervous system cancerOpen Targets
0.26Weak
trauma complicationOpen Targets
0.26Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
PRKNProtein interaction91%WDR90Protein interaction90%TEKT4Protein interaction90%CFAP53Protein interaction89%TUBA1AProtein interaction88%TUBB4BProtein interaction88%
Tissue Expression6 tissues
Heart
100%
Ovary
21%
Brain
21%
Liver
20%
Lung
5%
Bone Marrow
1%
Gene Interaction Network
Click a node to explore
PACRGPRKNWDR90TEKT4CFAP53TUBA1ATUBB4B
PROTEIN STRUCTURE
Preparing viewer…
PDB6NDU · 2.10 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.30LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.95 [0.71–1.30]
RankingsWhere PACRG stands among ~20K protein-coding genes
  • #8,706of 20,598
    Most Researched51
  • #13,695of 17,882
    Most Constrained (LOEUF)1.30
Genes detectedPACRG
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Identification of a novel gene linked to parkin via a bi-directional promoter.
PMID: 12547187
J Mol Biol · 2003
1.00
2
Crystal structure of human PACRG in complex with MEIG1 reveals roles in axoneme formation and tubulin binding.
PMID: 33529594
Structure · 2021
0.90
3
Parkin-co-regulated gene (PACRG) product interacts with tubulin and microtubules.
PMID: 18387367
FEBS Lett · 2008
0.80
4
Parkin Co-Regulated Gene (PACRG) is regulated by the ubiquitin-proteasomal system and is present in the pathological features of Parkinsonian diseases.
PMID: 17590346
Neurobiol Dis · 2007
0.70
5
Associations of PRKN-PACRG SNPs and G × G and G × E interactions with the risk of hyperlipidaemia.
PMID: 32747620
Sci Rep · 2020
0.60