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25 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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RIPK3
receptor interacting serine/threonine kinase 3
Chromosome 14 · 14q12
NCBI Gene: 11035Ensembl: ENSG00000129465.17HGNC: HGNC:10021UniProt: Q9Y572
215PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Kinase
RESEARCH IMPACT
Trending
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein-containing complex bindingcytosolnucleusprotein serine/threonine kinase bindingsevere acute respiratory syndromeviral diseaseneoplasmhypertension
✦AI Summary

RIPK3 (receptor interacting serine/threonine kinase 3) is a critical mediator of necroptosis, a form of programmed cell death characterized by cell rupture 1. The protein functions primarily through interaction with RIPK1 via RIP homotypic interaction motifs and phosphorylates mixed lineage kinase domain-like protein (MLKL) at threonine 357 and serine 358 residues, which is essential for necroptosis execution 2. RIPK3 activation occurs through various triggers including TNF, Toll-like receptors, or viral infections when caspase-8 is inhibited 1. Beyond cell death, RIPK3 serves scaffolding functions in inflammatory signaling pathways, promoting cytokine production through K63- and M1-linked ubiquitination independently of necroptosis 3. The protein also acts as a damage-associated molecular pattern when released extracellularly, binding to RAGE receptors and activating CaMKII signaling to exacerbate tissue injury 4. RIPK3 modulates metabolic functions by dampening mitochondrial bioenergetics and affecting lipid droplet dynamics in liver disease 5. Clinically, elevated plasma RIPK3 levels correlate with poor outcomes in acute myocardial infarction patients 4, and RIPK3 deficiency ameliorates various pathological conditions including sepsis and metabolic liver disease, making it a potential therapeutic target 6.

Sources cited
1
RIPK3 mediates necroptosis through interaction with RIPK1 and is triggered by TNF, TLRs, or TCR when caspase-8 is inhibited
PMID: 25662614
2
RIPK3 phosphorylates MLKL at threonine 357 and serine 358 residues, which is critical for necroptosis
PMID: 22265413
3
RIPK3 serves scaffolding functions in inflammatory signaling through ubiquitination pathways independent of cell death
PMID: 36268590
4
Extracellular RIPK3 acts as a DAMP, binding RAGE receptors and activating CaMKII signaling; elevated plasma levels correlate with poor cardiac outcomes
PMID: 39411860
5
RIPK3 dampens mitochondrial bioenergetics and affects lipid droplet dynamics in metabolic liver disease
PMID: 36029129
6
RIPK3 deficiency ameliorates STING-driven inflammatory diseases and sepsis
PMID: 37475188
Disease Associationsⓘ20
severe acute respiratory syndromeOpen Targets
0.53Moderate
viral diseaseOpen Targets
0.38Weak
neoplasmOpen Targets
0.12Weak
hypertensionOpen Targets
0.11Weak
essential hypertensionOpen Targets
0.11Weak
acute kidney injuryOpen Targets
0.10Weak
cancerOpen Targets
0.10Weak
acute myeloid leukemiaOpen Targets
0.10Weak
colitisOpen Targets
0.10Weak
non-alcoholic steatohepatitisOpen Targets
0.10Weak
SepsisOpen Targets
0.10Weak
acute respiratory distress syndromeOpen Targets
0.10Weak
hepatocellular carcinomaOpen Targets
0.10Suggestive
cholangiocarcinomaOpen Targets
0.10Suggestive
infectionOpen Targets
0.10Suggestive
melanomaOpen Targets
0.10Suggestive
cardiac hypertrophyOpen Targets
0.10Suggestive
myocardial infarctionOpen Targets
0.09Suggestive
non-alcoholic fatty liver diseaseOpen Targets
0.09Suggestive
colorectal carcinomaOpen Targets
0.09Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
IKBKGProtein interaction100%FASLGProtein interaction100%TICAM1Protein interaction98%GLULProtein interaction97%GLUD1Protein interaction97%HSP90AA1Protein interaction97%
Tissue Expression6 tissues
Lung
100%
Bone Marrow
66%
Heart
23%
Liver
15%
Ovary
6%
Brain
2%
Gene Interaction Network
Click a node to explore
RIPK3IKBKGFASLGTICAM1GLULGLUD1HSP90AA1
PROTEIN STRUCTURE
Preparing viewer…
PDB5ZCK · 1.27 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.22LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.96 [0.77–1.22]
RankingsWhere RIPK3 stands among ~20K protein-coding genes
  • #1,931of 20,598
    Most Researched215 · top 10%
  • #12,807of 17,882
    Most Constrained (LOEUF)1.22
Genes detectedRIPK3
Sources retrieved25 papers
Response time—
📄 Sources
25▼
1
Influenza Virus Z-RNAs Induce ZBP1-Mediated Necroptosis.
PMID: 32200799
Cell · 2020
1.00
2
Human ZBP1 induces cell death-independent inflammatory signaling via RIPK3 and RIPK1.
PMID: 36268590
EMBO Rep · 2022
0.90
3
Z-DNA binding protein 1 promotes heatstroke-induced cell death.
PMID: 35511979
Science · 2022
0.80
4
RIPK1 and RIPK3: critical regulators of inflammation and cell death.
PMID: 25662614
Trends Cell Biol · 2015
0.70
5
Extracellular RIPK3 Acts as a Damage-Associated Molecular Pattern to Exaggerate Cardiac Ischemia/Reperfusion Injury.
PMID: 39411860
Circulation · 2024
0.60