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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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SENP2
SUMO specific peptidase 2
Chromosome 3 · 3q27.2
NCBI Gene: 59343Ensembl: ENSG00000163904.14HGNC: HGNC:23116UniProt: Q9HC62
122PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Highly ConstrainedProteaseTransporter
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
positive regulation of protein ubiquitinationnegative regulation of protein ubiquitinationnuclear poreprotein bindingneurodegenerative diseaseatrioventricular blocklysosomal storage diseasediabetes mellitus
✦AI Summary

SENP2 (SUMO specific peptidase 2) is a critical desumoylating enzyme that regulates cellular homeostasis and disease processes through removal of Small Ubiquitin-like Modifier (SUMO) proteins from target substrates. SENP2 catalyzes desumoylation by cleaving SUMO proteins from lysine residues on target proteins, thereby modulating their stability, localization, and function 1. In metabolic regulation, SENP2 controls energy homeostasis in human adipocytes and skeletal muscle cells, where knockdown reduces glucose metabolism and lipid accumulation while increasing lipid oxidation 2. SENP2 is essential for insulin signaling in human skeletal muscle, as its depletion completely abolishes insulin-stimulated glycogen synthesis and Akt phosphorylation 3. In cardiovascular protection, SENP2 prevents ferroptosis during myocardial ischemia-reperfusion injury by desumoylating NCOA4, which stabilizes the protein and reduces ferritinophagy-dependent cell death 4. SENP2 also regulates epithelial cell fate by controlling the mitosis-differentiation checkpoint through its localization to mitotic spindles, where loss causes mitotic defects and premature differentiation 5. Additionally, SENP2 modulates DNA damage responses by stabilizing hSSB1 through desumoylation, enhancing recruitment of DNA repair complexes 1. Clinical significance includes potential therapeutic targeting in cancer, metabolic disorders, and cardiovascular disease.

Sources cited
1
SENP2 catalyzes desumoylation by cleaving SUMO proteins from lysine residues on target proteins, thereby modulating their stability, localization, and function .
PMID: 32576812
2
In metabolic regulation, SENP2 controls energy homeostasis in human adipocytes and skeletal muscle cells, where knockdown reduces glucose metabolism and lipid accumulation while increasing lipid oxidation .
PMID: 37013149
3
SENP2 is essential for insulin signaling in human skeletal muscle, as its depletion completely abolishes insulin-stimulated glycogen synthesis and Akt phosphorylation .
PMID: 34909683
4
In cardiovascular protection, SENP2 prevents ferroptosis during myocardial ischemia-reperfusion injury by desumoylating NCOA4, which stabilizes the protein and reduces ferritinophagy-dependent cell death .
PMID: 40366738
5
SENP2 also regulates epithelial cell fate by controlling the mitosis-differentiation checkpoint through its localization to mitotic spindles, where loss causes mitotic defects and premature differentiation .
PMID: 39152119
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.52Moderate
atrioventricular blockOpen Targets
0.40Weak
lysosomal storage diseaseOpen Targets
0.33Weak
diabetes mellitusOpen Targets
0.33Weak
alopecia areataOpen Targets
0.33Weak
First degree atrioventricular blockOpen Targets
0.31Weak
spinal cord injuryOpen Targets
0.30Weak
goutOpen Targets
0.22Weak
breast cancerOpen Targets
0.09Suggestive
esophageal squamous cell carcinomaOpen Targets
0.08Suggestive
hepatocellular carcinomaOpen Targets
0.08Suggestive
chronic lymphocytic leukemiaOpen Targets
0.07Suggestive
MODYOpen Targets
0.07Suggestive
bipolar disorderOpen Targets
0.06Suggestive
benign adult familial myoclonic epilepsyOpen Targets
0.06Suggestive
Romano-Ward syndromeOpen Targets
0.06Suggestive
maturity-onset diabetes of the young type 3Open Targets
0.05Suggestive
Rolandic epilepsyOpen Targets
0.05Suggestive
Familial progressive cardiac conduction defectOpen Targets
0.05Suggestive
type 2 diabetes mellitusOpen Targets
0.05Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
LMNB2Protein interaction100%SUMO1Protein interaction100%SUMO2Protein interaction100%DVL1Protein interaction99%SUMO3Protein interaction98%DVL2Protein interaction91%
Tissue Expression6 tissues
Bone Marrow
100%
Brain
91%
Heart
83%
Ovary
70%
Liver
59%
Lung
47%
Gene Interaction Network
Click a node to explore
SENP2LMNB2SUMO1SUMO2DVL1SUMO3DVL2
PROTEIN STRUCTURE
Preparing viewer…
PDB3ZO5 · 2.15 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.25Highly Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.12 [0.06–0.25]
RankingsWhere SENP2 stands among ~20K protein-coding genes
  • #3,864of 20,598
    Most Researched122 · top quartile
  • #791of 17,882
    Most Constrained (LOEUF)0.25 · top 5%
Genes detectedSENP2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
SENP2-mediated deSUMOylation of NCOA4 protects against ferritinophagy-dependent ferroptosis in myocardial ischemia-reperfusion injury.
PMID: 40366738
Autophagy · 2025
1.00
2
Astragaloside IV combined with ligustrazine ameliorates abnormal mitochondrial dynamics via Drp1 SUMO/deSUMOylation in cerebral ischemia-reperfusion injury.
PMID: 38615367
CNS Neurosci Ther · 2024
0.90
3
SENP2 knockdown in human adipocytes reduces glucose metabolism and lipid accumulation, while increases lipid oxidation.
PMID: 37013149
Metabol Open · 2023
0.80
4
SUMOylation stabilizes hSSB1 and enhances the recruitment of NBS1 to DNA damage sites.
PMID: 32576812
Signal Transduct Target Ther · 2020
0.70
5
MicroRNA-145-5p inhibits the tumorigenesis of breast cancer through SENP2-regulated ubiquitination of ERK2.
PMID: 39578257
Cell Mol Life Sci · 2024
0.60