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25 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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SIRT3
sirtuin 3
Chromosome 11 · 11p15.5
NCBI Gene: 23410Ensembl: ENSG00000142082.15HGNC: HGNC:14931UniProt: E9PK80
382PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
RESEARCH IMPACT
Highly StudiedTrending
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
zinc ion bindingpositive regulation of oxidative phosphorylationpositive regulation of superoxide dismutase activitypositive regulation of catalase activityuterine fibroidneurodegenerative diseaseneoplasmhepatocellular carcinoma
✦AI Summary

SIRT3 is a mitochondrial NAD+-dependent deacetylase that regulates cellular energy metabolism through protein deacetylation of key metabolic enzymes including SOD2, PDHA1, and ATP synthase components 1. Beyond its classical deacetylase activity, SIRT3 functions as a protein-lysine deacylase, catalyzing debenzoylation and delactylation of substrates such as CCNE2 and histone H4 23. In response to metabolic stress, SIRT3 deacetylates the transcription factor FOXO3 to promote mitochondrial DNA transcription 4, while regulating hepatic ceramide metabolism and lipogenesis 5. Beyond mitochondrial functions, SIRT3 consolidates heterochromatin and stabilizes nuclear integrity through interaction with nuclear envelope proteins, counteracting senescence in mesenchymal stem cells 6. SIRT3 protects against oxidative stress-induced ferroptosis by activating the SIRT3/FoxO3a pathway and increasing SOD2 and catalase expression to reduce ROS generation 7. The deubiquitinase USP11 stabilizes SIRT3 through deubiquitination, protecting against ferroptosis in intervertebral disc degeneration 8. Clinically, SIRT3 downregulation associates with hepatocellular carcinoma progression, where SIRT3 activation suppresses HCC cell growth by delactylating CCNE2 2. In glioblastoma, SIRT3 inhibition sensitizes cells to ferroptosis through mitophagy promotion and SLC7A11 downregulation 9, suggesting SIRT3 as a therapeutic target across multiple malignancies.

Sources cited
1
SIRT3 is a mitochondrial NAD+-dependent deacetylase that regulates cellular energy metabolism through protein deacetylation of key metabolic enzymes including SOD2, PDHA1, and ATP synthase components .
PMID: 24252090
2
In response to metabolic stress, SIRT3 deacetylates the transcription factor FOXO3 to promote mitochondrial DNA transcription , while regulating hepatic ceramide metabolism and lipogenesis .
PMID: 23283301
3
In response to metabolic stress, SIRT3 deacetylates the transcription factor FOXO3 to promote mitochondrial DNA transcription , while regulating hepatic ceramide metabolism and lipogenesis .
PMID: 38561088
4
Beyond mitochondrial functions, SIRT3 consolidates heterochromatin and stabilizes nuclear integrity through interaction with nuclear envelope proteins, counteracting senescence in mesenchymal stem cells .
PMID: 33706382
5
SIRT3 protects against oxidative stress-induced ferroptosis by activating the SIRT3/FoxO3a pathway and increasing SOD2 and catalase expression to reduce ROS generation .
PMID: 37858064
6
The deubiquitinase USP11 stabilizes SIRT3 through deubiquitination, protecting against ferroptosis in intervertebral disc degeneration .
PMID: 37099926
7
Beyond its classical deacetylase activity, SIRT3 functions as a protein-lysine deacylase, catalyzing debenzoylation and delactylation of substrates such as CCNE2 and histone H4 , .
PMID: 36896611
8
In glioblastoma, SIRT3 inhibition sensitizes cells to ferroptosis through mitophagy promotion and SLC7A11 downregulation , suggesting SIRT3 as a therapeutic target across multiple malignancies.
PMID: 38395990
Disease Associationsⓘ20
uterine fibroidOpen Targets
0.32Weak
neurodegenerative diseaseOpen Targets
0.19Weak
neoplasmOpen Targets
0.11Weak
hepatocellular carcinomaOpen Targets
0.11Weak
brain aneurysmOpen Targets
0.11Weak
acute kidney injuryOpen Targets
0.11Weak
cancerOpen Targets
0.11Weak
Uterine leiomyomaOpen Targets
0.11Weak
Alzheimer diseaseOpen Targets
0.11Weak
infectionOpen Targets
0.11Weak
non-small cell lung carcinomaOpen Targets
0.10Weak
subarachnoid hemorrhageOpen Targets
0.10Weak
polycystic ovary syndromeOpen Targets
0.10Weak
female reproductive system diseaseOpen Targets
0.10Suggestive
acute myeloid leukemiaOpen Targets
0.10Suggestive
diffuse large B-cell lymphomaOpen Targets
0.10Suggestive
gastric cancerOpen Targets
0.10Suggestive
SepsisOpen Targets
0.10Suggestive
coronary artery diseaseOpen Targets
0.10Suggestive
oral squamous cell carcinomaOpen Targets
0.10Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
FOXO1Protein interaction100%NDUFA9Protein interaction98%FOXO3Protein interaction98%SOD2Protein interaction98%TFAMProtein interaction98%PPARGC1AProtein interaction98%
Tissue Expression6 tissues
Liver
100%
Heart
97%
Ovary
63%
Brain
40%
Lung
37%
Bone Marrow
37%
Gene Interaction Network
Click a node to explore
SIRT3FOXO1NDUFA9FOXO3SOD2TFAMPPARGC1A
PROTEIN STRUCTURE
Preparing viewer…
PDB8ANC · 1.11 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.17LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.83 [0.60–1.17]
RankingsWhere SIRT3 stands among ~20K protein-coding genes
  • #789of 20,598
    Most Researched382 · top 5%
  • #12,272of 17,882
    Most Constrained (LOEUF)1.17
Genes detectedSIRT3
Sources retrieved25 papers
Response time—
📄 Sources
25▼
1
SIRT3 consolidates heterochromatin and counteracts senescence.
PMID: 33706382
Nucleic Acids Res · 2021
1.00
2
Resveratrol reduces ROS-induced ferroptosis by activating SIRT3 and compensating the GSH/GPX4 pathway.
PMID: 37858064
Mol Med · 2023
0.90
3
Sirt3-mediated mitophagy regulates AGEs-induced BMSCs senescence and senile osteoporosis.
PMID: 33662874
Redox Biol · 2021
0.80
4
SIRT3-dependent delactylation of cyclin E2 prevents hepatocellular carcinoma growth.
PMID: 36896611
EMBO Rep · 2023
0.70
5
SIRT3-Mediated Deacetylation of DRP1
PMID: 39976201
Adv Sci (Weinh) · 2025
0.60