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GeneE
10 sources retrieved Β· Most recent: April 2026 Β· Index updated 15 days ago
β“˜GeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
SLC5A7
solute carrier family 5 member 7
Chromosome 2 Β· 2q12.3
NCBI Gene: 60482Ensembl: ENSG00000115665.10HGNC: HGNC:14025UniProt: B2RCU2
50PubMed Papers
22Diseases
0Drugs
19Pathogenic Variants
FUNCTIONAL ROLE
Transporter
CLINICAL
OMIM Disease Gene
DATA QUALITY
βœ“ Experimental GO Evidenceβœ“ Swiss-Prot Reviewed
membraneplasma membranecholine:sodium symporter activityearly endosome membraneCongenital myasthenic syndromesPresynaptic congenital myasthenic syndromesdistal hereditary motor neuropathy type 7presynaptic congenital myasthenic syndrome
✦AI Summary

SLC5A7 encodes a high-affinity sodium-coupled choline transporter that plays a critical role in cholinergic neurotransmission 1. The protein functions as an electrogenic, voltage-dependent transporter that uptakes choline from the synaptic cleft into presynaptic nerve terminals, representing the rate-limiting step for acetylcholine synthesis 1. This choline transport is essential for maintaining cholinergic signaling pathways, as demonstrated by studies showing SLC5A7 downregulation disrupts cholinergic synaptic signaling and reduces acetylcholine concentration 2. The transporter is predominantly localized in presynaptic terminal intracellular organelles and translocates to the plasma membrane upon neuronal activity. Pathogenic variants in SLC5A7 cause congenital myasthenic syndrome type 20 (presynaptic) and distal hereditary motor neuropathy type 7, both affecting neuromuscular transmission 13. The gene also appears to have tumor suppressor functions in colorectal cancer, where promoter hypermethylation leads to SLC5A7 downregulation and cancer progression 4. Additionally, SLC5A7 polymorphisms influence autonomic nervous system reactivity and infant self-regulation, particularly in respiratory sinus arrhythmia responses to stress 5. These findings establish SLC5A7 as essential for both cholinergic neurotransmission and broader physiological regulation.

Sources cited
1
SLC5A7 encodes a high-affinity choline transporter essential for acetylcholine synthesis and is associated with congenital myasthenic syndromes
PMID: 36835142
2
SLC5A7 disruption affects cholinergic synaptic signaling pathways and reduces acetylcholine concentration
PMID: 38484610
3
SLC5A7 mutations cause distal hereditary motor neuropathy type 7
PMID: 38702287
4
SLC5A7 functions as a tumor suppressor in colorectal cancer and is silenced by promoter hypermethylation
PMID: 35858918
5
SLC5A7 polymorphisms influence autonomic nervous system reactivity and infant self-regulation
PMID: 30005279
Disease Associationsβ“˜22
Congenital myasthenic syndromesOpen Targets
0.78Strong
Presynaptic congenital myasthenic syndromesOpen Targets
0.72Strong
distal hereditary motor neuropathy type 7Open Targets
0.62Moderate
hereditary motor and sensory neuropathyOpen Targets
0.37Weak
presynaptic congenital myasthenic syndromeOpen Targets
0.37Weak
muscular atrophyOpen Targets
0.27Weak
Charcot-Marie-Tooth disease type 2Open Targets
0.27Weak
genetic disorderOpen Targets
0.19Weak
distal hereditary motor neuropathyOpen Targets
0.11Weak
prostate cancerOpen Targets
0.11Weak
Charcot-Marie-Tooth diseaseOpen Targets
0.11Weak
Familial prostate cancerOpen Targets
0.11Weak
colorectal carcinomaOpen Targets
0.09Suggestive
gestational diabetesOpen Targets
0.07Suggestive
hepatocellular carcinomaOpen Targets
0.05Suggestive
Trichodysplasia - xerodermaOpen Targets
0.04Suggestive
trichodysplasia-xeroderma syndromeOpen Targets
0.04Suggestive
hypotrichosis simplexOpen Targets
0.04Suggestive
wooly hair, autosomal recessive 3Open Targets
0.04Suggestive
hypotrichosis 4Open Targets
0.04Suggestive
Myasthenic syndrome, congenital, 20, presynapticUniProt
Neuronopathy, distal hereditary motor, autosomal dominant 7UniProt
Pathogenic Variants19
NM_021815.5(SLC5A7):c.895+1G>CLikely pathogenic
Neuronopathy, distal hereditary motor, type 7A;Congenital myasthenic syndrome 20|Congenital myasthenic syndrome 20
β˜…β˜…β˜†β˜†2025
NM_021815.5(SLC5A7):c.101dup (p.Ser34fs)Pathogenic
Congenital myasthenic syndrome 20;Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2026β†’ Residue 34
NM_021815.5(SLC5A7):c.1082G>A (p.Arg361Gln)Likely pathogenic
Congenital myasthenic syndrome 20|Congenital myasthenic syndrome 20;Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2025β†’ Residue 361
NM_021815.5(SLC5A7):c.179-2A>GLikely pathogenic
Neuronopathy, distal hereditary motor, type 7A;Congenital myasthenic syndrome 20
β˜…β˜†β˜†β˜†2025
NM_021815.5(SLC5A7):c.134del (p.Gly45fs)Pathogenic
Congenital myasthenic syndrome 20;Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2025β†’ Residue 45
NM_021815.5(SLC5A7):c.292+1G>ALikely pathogenic
Neuronopathy, distal hereditary motor, type 7A;Congenital myasthenic syndrome 20
β˜…β˜†β˜†β˜†2025
NM_021815.5(SLC5A7):c.364dup (p.Tyr122fs)Pathogenic
Neuronopathy, distal hereditary motor, type 7A;Congenital myasthenic syndrome 20
β˜…β˜†β˜†β˜†2025β†’ Residue 122
NM_021815.5(SLC5A7):c.836del (p.Phe279fs)Pathogenic
Congenital myasthenic syndrome 20;Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2025β†’ Residue 279
NM_021815.5(SLC5A7):c.881T>C (p.Ile294Thr)Likely pathogenic
Congenital myasthenic syndrome 20
β˜…β˜†β˜†β˜†2024β†’ Residue 294
NM_021815.5(SLC5A7):c.719G>A (p.Trp240Ter)Pathogenic
Congenital myasthenic syndrome 20;Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2024β†’ Residue 240
NM_021815.5(SLC5A7):c.1503_1506del (p.Phe502fs)Likely pathogenic
Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2023β†’ Residue 502
NM_021815.5(SLC5A7):c.742-2A>GLikely pathogenic
Neuronopathy, distal hereditary motor, type 7A
β˜…β˜†β˜†β˜†2023
NM_021815.5(SLC5A7):c.1113+2T>ALikely pathogenic
Charcot-Marie-Tooth disease type 2
β˜…β˜†β˜†β˜†2021
NM_021815.5(SLC5A7):c.1231G>A (p.Asp411Asn)Likely pathogenic
not provided
β˜…β˜†β˜†β˜†2019β†’ Residue 411
NM_021815.5(SLC5A7):c.123_126del (p.Ala41_Ile42insTer)Likely pathogenic
Congenital myasthenic syndrome 20
β˜…β˜†β˜†β˜†2016β†’ Residue 41
NM_021815.5(SLC5A7):c.178+2T>CLikely pathogenic
Congenital myasthenic syndrome 20
β˜†β˜†β˜†β˜†2024
NM_021815.5(SLC5A7):c.1207T>C (p.Tyr403His)Likely pathogenic
Congenital myasthenic syndrome 20
β˜†β˜†β˜†β˜†2024β†’ Residue 403
NM_021815.5(SLC5A7):c.1349G>A (p.Gly450Glu)Likely pathogenic
Congenital myasthenic syndrome 20
β˜†β˜†β˜†β˜†2024β†’ Residue 450
NM_021815.5(SLC5A7):c.143A>G (p.Asp48Gly)Pathogenic
Congenital myasthenic syndrome 20
β˜†β˜†β˜†β˜†2016β†’ Residue 48
View on ClinVar β†—
Related Genes
RANBP2Protein interaction75%SLC18A3Protein interaction71%CHATProtein interaction61%SLC44A5Shared pathway33%SLC44A3Shared pathway33%SLC44A4Shared pathway29%
Tissue Expression6 tissues
Heart
100%
Ovary
21%
Lung
16%
Liver
6%
Bone Marrow
4%
Brain
2%
Gene Interaction Network
Click a node to explore
SLC5A7RANBP2SLC18A3CHATSLC44A5SLC44A3SLC44A4
PROTEIN STRUCTURE
Preparing viewer…
PDB9BFJ Β· 2.35 Γ… Β· EM
View on RCSB β†—
Constraintβ“˜
LOEUFβ“˜
0.46Moderately Constrained
pLIβ“˜
1.00Intolerant
Observed/Expected LoF0.30 [0.20–0.46]
RankingsWhere SLC5A7 stands among ~20K protein-coding genes
  • #8,878of 20,598
    Most Researched50
  • #2,245of 5,498
    Most Pathogenic Variants19
  • #2,621of 17,882
    Most Constrained (LOEUF)0.46 Β· top quartile
Genes detectedSLC5A7
Sources retrieved10 papers
Response timeβ€”
πŸ“„ Sources
10β–Ό
1
Distal hereditary motor neuropathies.
PMID: 38702287
Rev Neurol (Paris) Β· 2024
1.00
2
Clinical and Pathologic Features of Congenital Myasthenic Syndromes Caused by 35 Genes-A Comprehensive Review.
PMID: 36835142
Int J Mol Sci Β· 2023
0.90
3
A 20-year Clinical and Genetic Neuromuscular Cohort Analysis in Lebanon: An International Effort.
PMID: 34602496
J Neuromuscul Dis Β· 2022
0.80
4
Oxidized/unmodified-polyethylene microplastics neurotoxicity in mice: Perspective from microbiota-gut-brain axis.
PMID: 38484610
Environ Int Β· 2024
0.70
5
Targeted demethylation of the SLC5A7 promotor inhibits colorectal cancer progression.
PMID: 35858918
Clin Epigenetics Β· 2022
0.60