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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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TIPRL
TOR signaling pathway regulator
Chromosome 1 · 1q24.2
NCBI Gene: 261726Ensembl: ENSG00000143155.14HGNC: HGNC:30231UniProt: O75663
82PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
DNA damage checkpoint signalingprotein phosphatase inhibitor activityprotein bindingTOR signalingneurodegenerative diseasehepatocellular carcinomaneoplasmliver cancer
✦AI Summary

TIPRL (TOR signaling pathway regulator-like) is a regulatory protein that functions primarily as an allosteric inhibitor of protein phosphatases PP2A and PP4. Structurally, TIPRL adopts a novel fold with a central antiparallel beta-sheet core and contains a conserved cleft that preferentially binds the unmodified C-terminal tail of PP2A 1. The protein inhibits PP2A catalytic activity by blocking the phosphatase's active site and coordinates with latency chaperone α4 to disassemble active holoenzymes in a methylation-dependent manner 2. TIPRL negatively regulates PP4 activity by inhibiting formation of the active PP4C:PP4R2 complex, thereby promoting H2AX phosphorylation and enhancing DNA damage response signaling 3. In cancer contexts, TIPRL is significantly upregulated in hepatocellular carcinoma and non-small cell lung cancer, where it contributes to tumor progression through multiple mechanisms 45. In lung cancer stem cells, TIPRL maintains stemness and survival by binding CaMKK2 and activating a CaMKK2-CaMK4-CREB feedback loop 5. In hepatocellular carcinoma, TIPRL promotes TRAIL resistance by facilitating MKK7-PP2Ac interactions and preventing prolonged JNK activation 6. Pan-cancer analysis reveals TIPRL overexpression correlates with poor prognosis and genomic instability across multiple tumor types 7.

Sources cited
1
TIPRL structure with novel fold and preferential binding to unmodified PP2A C-terminal tail
PMID: 27489114
2
TIPRL coordinates with α4 chaperone for methylation-dependent PP2A holoenzyme disassembly
PMID: 29273778
3
TIPRL inhibits PP4 activity and promotes H2AX phosphorylation in DNA damage response
PMID: 26717153
4
TIPRL upregulation in hepatocellular carcinoma and correlation with LC3 and CD133
PMID: 31727942
5
TIPRL maintains lung cancer stem cell properties through CaMKK2-CaMK4-CREB pathway
PMID: 39076120
6
TIPRL promotes TRAIL resistance in HCC by mediating MKK7-PP2Ac interactions
PMID: 22841785
7
Pan-cancer analysis showing TIPRL overexpression and poor prognosis correlation
PMID: 40088344
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.42Moderate
hepatocellular carcinomaOpen Targets
0.10Suggestive
neoplasmOpen Targets
0.09Suggestive
liver cancerOpen Targets
0.09Suggestive
lung cancerOpen Targets
0.09Suggestive
cancerOpen Targets
0.09Suggestive
response to xenobiotic stimulusOpen Targets
0.09Suggestive
non-small cell lung carcinomaOpen Targets
0.08Suggestive
poisoningOpen Targets
0.08Suggestive
gastric cancerOpen Targets
0.08Suggestive
infectionOpen Targets
0.05Suggestive
liver diseaseOpen Targets
0.04Suggestive
Pallister-Hall syndromeOpen Targets
0.03Suggestive
adrenal cortex carcinomaOpen Targets
0.02Suggestive
infantile convulsions and choreoathetosisOpen Targets
0.02Suggestive
Insulin resistanceOpen Targets
0.02Suggestive
viral diseaseOpen Targets
0.02Suggestive
head and neck squamous cell carcinomaOpen Targets
0.02Suggestive
breast cancerOpen Targets
0.02Suggestive
Alzheimer diseaseOpen Targets
0.02Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
IGBP1Protein interaction99%PPP2R1AProtein interaction99%PPP4CProtein interaction99%LCMT1Protein interaction99%PPP4R2Protein interaction99%PPP2CAProtein interaction97%
Tissue Expression6 tissues
Heart
100%
Brain
98%
Liver
55%
Bone Marrow
51%
Ovary
48%
Lung
44%
Gene Interaction Network
Click a node to explore
TIPRLIGBP1PPP2R1APPP4CLCMT1PPP4R2PPP2CA
PROTEIN STRUCTURE
Preparing viewer…
PDB5D9G · 2.15 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.62LoF Tolerant
pLIⓘ
0.84Intermediate
Observed/Expected LoF0.29 [0.15–0.62]
RankingsWhere TIPRL stands among ~20K protein-coding genes
  • #5,830of 20,598
    Most Researched82
  • #4,295of 17,882
    Most Constrained (LOEUF)0.62 · top quartile
Genes detectedTIPRL
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
TIPRL Regulates Stemness and Survival in Lung Cancer Stem Cells through CaMKK2-CaMK4-CREB Feedback Loop Activation.
PMID: 39076120
Adv Sci (Weinh) · 2024
1.00
2
Crystal structure of the human Tip41 orthologue, TIPRL, reveals a novel fold and a binding site for the PP2Ac C-terminus.
PMID: 27489114
Sci Rep · 2016
0.90
3
TIPRL, a Potential Double-edge Molecule to be Targeted and Re-targeted Toward Cancer.
PMID: 38888871
Cell Biochem Biophys · 2024
0.80
4
Pan-cancer bioinformatics analysis of TIPRL in human tumors.
PMID: 40088344
Discov Oncol · 2025
0.70
5
Methylation-regulated decommissioning of multimeric PP2A complexes.
PMID: 29273778
Nat Commun · 2017
0.60