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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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TNFRSF25
TNF receptor superfamily member 25
Chromosome 1 · 1p36.31
NCBI Gene: 8718Ensembl: ENSG00000215788.12HGNC: HGNC:11910UniProt: Q93038
77PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
plasma membranesignaling receptor activityapoptotic processsignal transductionneuronopathy, distal hereditary motor, autosomal recessive 4distal hereditary motor neuropathyneoplasmcancer
✦AI Summary

TNFRSF25 (DR3) is a death domain-containing receptor that functions as a TNF receptor superfamily member with dual roles in immune regulation and apoptosis. The receptor binds its monogamous ligand TL1A (TNFSF15) and can be antagonized by the decoy receptor TR6/DcR3 1. TNFRSF25 mediates signaling through recruitment of TNFR-associated factor 2 and TNFR-associated death domain, leading to activation of NF-κB and PI3K/Akt pathways 2. The receptor serves as a broad-acting T cell costimulator, promoting IL-2 responsiveness and proinflammatory cytokine secretion in activated T cells 1. TNFRSF25 signaling provides constitutive proliferation signals to regulatory T cells through tonic self-antigen exposure while requiring foreign antigen for conventional T cell activation 2. In inflammatory bowel disease, TL1A-DR3 signaling plays a central role in intestinal inflammation, serving as a universal costimulator of effector immune responses while also regulating Tregs and innate lymphoid cells 34. The system demonstrates dichotomous roles, providing protective functions during acute mucosal injury but contributing to chr1 inflammatory responses and intestinal fibrosis 4. These diverse functions make TNFRSF25 a promising therapeutic target for autoimmune diseases and cancer immunotherapy 5.

Sources cited
1
TL1A is a ligand for DR3 and TR6/DcR3, induces NF-κB activation and apoptosis, and acts as T cell costimulator
PMID: 11911831
2
TNFRSF25 signaling mechanisms involve TRAF2 and TRADD recruitment, NF-κB and PI3K/Akt activation, and differential effects on regulatory vs conventional T cells
PMID: 24242819
3
TL1A-DR3 signaling serves as universal costimulator in IBD and regulates Tregs and innate lymphoid cells
PMID: 39266053
4
DR3 has dichotomous roles in mucosal immunity, protective in acute injury but pro-inflammatory in chronic responses, and mediates intestinal fibrosis
PMID: 30972074
5
TNFRSF25 agonists show antitumor effects and potential for cancer immunotherapy
PMID: 39142717
Disease Associationsⓘ20
neuronopathy, distal hereditary motor, autosomal recessive 4Open Targets
0.19Weak
distal hereditary motor neuropathyOpen Targets
0.16Weak
neoplasmOpen Targets
0.11Weak
cancerOpen Targets
0.10Weak
colitisOpen Targets
0.10Suggestive
prostate cancerOpen Targets
0.09Suggestive
sarcoidosisOpen Targets
0.09Suggestive
Varicose veinsOpen Targets
0.09Suggestive
chronic lymphocytic leukemiaOpen Targets
0.08Suggestive
cardiac hypertrophyOpen Targets
0.07Suggestive
lung cancerOpen Targets
0.07Suggestive
type 2 diabetes mellitusOpen Targets
0.06Suggestive
rheumatoid arthritisOpen Targets
0.06Suggestive
Sensorineural hearing impairmentOpen Targets
0.06Suggestive
prostate neoplasmOpen Targets
0.06Suggestive
acute respiratory distress syndromeOpen Targets
0.05Suggestive
cervical cancerOpen Targets
0.05Suggestive
reticular dysgenesisOpen Targets
0.05Suggestive
inflammatory bowel diseaseOpen Targets
0.05Suggestive
type 1 diabetes mellitusOpen Targets
0.05Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
RIPK1Protein interaction100%FADDProtein interaction100%TOR1AProtein interaction100%HLA-DQA1Protein interaction100%HLA-DQB1Protein interaction100%HLA-DRB1Protein interaction100%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
32%
Heart
26%
Liver
23%
Lung
22%
Brain
7%
Gene Interaction Network
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TNFRSF25RIPK1FADDTOR1AHLA-DQA1HLA-DQB1HLA-DRB1
PROTEIN STRUCTURE
Preparing viewer…
PDB5YGP · 2.09 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.84LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.61 [0.46–0.84]
RankingsWhere TNFRSF25 stands among ~20K protein-coding genes
  • #6,221of 20,598
    Most Researched77
  • #7,170of 17,882
    Most Constrained (LOEUF)0.84
Genes detectedTNFRSF25
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Targeting TL1A and DR3: the new frontier of anti-cytokine therapy in IBD.
PMID: 39266053
Gut · 2025
1.00
2
The TL1A inhibitors in IBD: what's in the pot?
PMID: 39772947
Expert Rev Gastroenterol Hepatol · 2025
0.90
3
TL1A (TNFSF15) and DR3 (TNFRSF25): A Co-stimulatory System of Cytokines With Diverse Functions in Gut Mucosal Immunity.
PMID: 30972074
Front Immunol · 2019
0.80
4
Targeting TNFRSF25 by agonistic antibodies and multimeric TL1A proteins co-stimulated CD8
PMID: 39142717
J Immunother Cancer · 2024
0.70
5
Pancreatic islet transplantation in type 1 diabetes: 20-year experience from a single-centre cohort in Canada.
PMID: 35588757
Lancet Diabetes Endocrinol · 2022
0.60