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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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ZRANB2
zinc finger RANBP2-type containing 2
Chromosome 1 · 1p31.1
NCBI Gene: 9406Ensembl: ENSG00000132485.15HGNC: HGNC:13058UniProt: O95218
127PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
RNA bindingnucleoplasmprotein bindinglipopolysaccharide bindingneurodegenerative diseaselysosomal storage diseasejoint diseasefemoral neck fracture
✦AI Summary

ZRANB2 is a nuclear zinc finger protein that functions as a regulator of alternative splicing through RNA binding and interactions with splicing machinery 1. The protein contains two C4 zinc finger motifs that recognize the consensus RNA sequence 5'-AGGUAA-3' 2 and binds to splicing factors U170K, U2AF35, and SFRS17A 1. ZRANB2 localizes to supraspliceosomes and influences splicing of multiple genes including CENTB1, WDR78, CABP4, and SMARCC2 3. Beyond splicing, ZRANB2 suppresses bone morphogenetic protein signaling by interacting with Smad proteins in the nucleus 4. Pathologically, ZRANB2 is upregulated in grade III ovarian carcinoma and regulates splicing programs promoting doxorubicin resistance in breast cancer through ECT2-Ex5 isoform inclusion 5. In glioma, ZRANB2 binds and stabilizes the long non-coding RNA SNHG20, promoting vasculogenic mimicry formation 6. Environmental exposure to arsenite displaces zinc from ZRANB2 zinc fingers, impairing its splicing function and increasing protein expression as a compensatory response 7. These findings establish ZRANB2 as a multifunctional regulatory protein with significant roles in both normal splicing and cancer-associated pathways.

Sources cited
1
ZRANB2 binds to ssRNA containing the consensus sequence 5'-AGGUAA-3'
PMID: 21256132
2
ZRANB2 is a nuclear protein with two zinc fingers that binds to mRNA and splicing factors U170K, U2AF35, and SFRS17A; upregulated in grade III ovarian serous papillary carcinoma
PMID: 17905639
3
ZRANB2 is part of the supraspliceosome and influences alternative splicing of multiple genes including CENTB1, WDR78, CABP4, and SMARCC2
PMID: 23666063
4
ZRANB2 interacts with Smad1/5/8 proteins and suppresses BMP signaling without affecting Smad phosphorylation or DNA binding
PMID: 22021003
5
ZRANB2 controls alternative splicing programs involved in breast cancer doxorubicin resistance through regulation of ECT2-Ex5 isoform inclusion
PMID: 31943118
6
ZRANB2 binds and stabilizes SNHG20 lncRNA, regulating vasculogenic mimicry formation in glioma through the FOXK1 pathway
PMID: 30744670
7
Arsenite displaces zinc from ZRANB2 zinc finger motifs, impairing its splicing function and increasing ZRANB2 protein expression at environmental and therapeutic doses
PMID: 32274925
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.56Moderate
lysosomal storage diseaseOpen Targets
0.37Weak
joint diseaseOpen Targets
0.31Weak
femoral neck fractureOpen Targets
0.26Weak
ovarian neoplasmOpen Targets
0.20Weak
HirsutismOpen Targets
0.19Weak
alcohol drinkingOpen Targets
0.19Weak
ProptosisOpen Targets
0.17Weak
response to stimulusOpen Targets
0.14Weak
spinal cord injuryOpen Targets
0.14Weak
facial painOpen Targets
0.13Weak
ankylosing spondylitisOpen Targets
0.11Weak
laryngeal diseaseOpen Targets
0.11Weak
adverse effectOpen Targets
0.10Suggestive
metabolic syndromeOpen Targets
0.10Suggestive
gliomaOpen Targets
0.08Suggestive
hepatocellular carcinomaOpen Targets
0.07Suggestive
acquired thrombocytopeniaOpen Targets
0.02Suggestive
breast cancerOpen Targets
0.02Suggestive
Febrile seizure (within the age range of 3 months to 6 years)Open Targets
0.02Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
RBMS2Shared pathway100%RTCAShared pathway100%RMP24Shared pathway100%TRMT2BShared pathway100%SUGP1Shared pathway100%TRMT2AShared pathway100%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
86%
Heart
55%
Lung
50%
Liver
39%
Brain
29%
Gene Interaction Network
Click a node to explore
ZRANB2RBMS2RTCARMP24TRMT2BSUGP1TRMT2A
PROTEIN STRUCTURE
Preparing viewer…
PDB3G9Y · 1.40 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.52Moderately Constrained
pLIⓘ
0.96Intolerant
Observed/Expected LoF0.33 [0.21–0.52]
RankingsWhere ZRANB2 stands among ~20K protein-coding genes
  • #3,710of 20,598
    Most Researched127 · top quartile
  • #3,222of 17,882
    Most Constrained (LOEUF)0.52 · top quartile
Genes detectedZRANB2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
ZRANB2: structural and functional insights into a novel splicing protein.
PMID: 17905639
Int J Biochem Cell Biol · 2008
1.00
2
Arsenite Exposure Displaces Zinc from ZRANB2 Leading to Altered Splicing.
PMID: 32274925
Chem Res Toxicol · 2020
0.90
3
ZRANB2 and SYF2-mediated splicing programs converging on ECT2 are involved in breast cancer cell resistance to doxorubicin.
PMID: 31943118
Nucleic Acids Res · 2020
0.80
4
ZRANB2/SNHG20/FOXK1 Axis regulates Vasculogenic mimicry formation in glioma.
PMID: 30744670
J Exp Clin Cancer Res · 2019
0.70
5
Intron Retention and TE Exonization Events in ZRANB2.
PMID: 22778693
Comp Funct Genomics · 2012
0.60