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4 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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CARD19
caspase recruitment domain family member 19
Chromosome 9 · 9q22.31
NCBI Gene: 84270Ensembl: ENSG00000165233.19HGNC: HGNC:28148UniProt: Q96LW7
24PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
mitochondrioncytosolnegative regulation of canonical NF-kappaB signal transductionnucleusadolescent idiopathic scoliosisAbnormal urine outputidiopathic membranous glomerulonephritisMorvan syndrome
✦AI Summary

CARD19 (caspase recruitment domain family member 19), also known as BinCARD-2, is a mitochondrial CARD-containing protein with emerging roles in innate immunity. Originally characterized as a negative regulator of BCL10-mediated NF-κB signaling 1, CARD19 interacts with BCL10 through its CARD domain and suppresses BCL10 phosphorylation in overexpression systems 1. However, recent evidence demonstrates that endogenous CARD19 plays a negligible role in TCR-dependent BCL10-mediated NF-κB activation in primary T cells 2. Instead, CARD19 functions as a positive regulator of antiviral innate immunity by associating with MAVS to facilitate MAVS oligomerization and enhance RIG-I-like receptor signaling, ultimately promoting interferon-β production in response to viral infection 3. Structurally, CARD19's CARD domain is susceptible to redox modification, with all three cysteines capable of oxidation 4, suggesting potential redox-regulatory mechanisms at mitochondria. These findings reveal CARD19 as a multi-functional adapter protein whose primary physiological role centers on potentiating antiviral immune responses rather than inhibiting canonical NF-κB signaling during T cell activation.

Sources cited
1
CARD19 is a mitochondrial protein that does not regulate BCL10-dependent NF-κB activation after TCR engagement in primary T cells
PMID: 32763502
2
CARD19 (BinCARD2) functions as a positive regulator of interferon response by promoting MAVS oligomerization in the RIG-I pathway
PMID: 30795865
3
CARD19's CARD domain undergoes redox modification with all three cysteines capable of oxidation, suggesting redox-regulatory roles
PMID: 23633586
4
CARD19 interacts with BCL10 through its CARD domain and suppresses BCL10 phosphorylation and NF-κB activation in overexpression systems
PMID: 15637807
⚠Limited data available — This gene has 4 indexed publications. Summary and analysis may be incomplete.
Disease Associationsⓘ20
adolescent idiopathic scoliosisOpen Targets
0.15Weak
Abnormal urine outputOpen Targets
0.14Weak
idiopathic membranous glomerulonephritisOpen Targets
0.07Suggestive
Morvan syndromeOpen Targets
0.07Suggestive
C1 inhibitor deficiencyOpen Targets
0.07Suggestive
autoimmune diseaseOpen Targets
0.07Suggestive
immune system diseaseOpen Targets
0.07Suggestive
type II hypersensitivity reaction diseaseOpen Targets
0.07Suggestive
Hashimoto's thyroiditisOpen Targets
0.06Suggestive
pemphigus vulgarisOpen Targets
0.05Suggestive
Autosomal recessive systemic lupus erythematosusOpen Targets
0.05Suggestive
autosomal systemic lupus erythematosus type 16Open Targets
0.05Suggestive
knee fractureOpen Targets
0.04Suggestive
Immunodeficiency due to a late component of complements deficiencyOpen Targets
0.04Suggestive
immunodeficiency due to a classical component pathway complement deficiencyOpen Targets
0.04Suggestive
Immunodeficiency due to a complement cascade protein anomalyOpen Targets
0.04Suggestive
complement component C1s deficiencyOpen Targets
0.04Suggestive
C1Q deficiency 1Open Targets
0.04Suggestive
preeclampsiaOpen Targets
0.04Suggestive
oral squamous cell carcinomaOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
NKIRAS2Shared pathway100%NKIRAS1Shared pathway100%MTX2Protein interaction80%C15orf39Shared pathway50%NLRX1Shared pathway50%TSPAN6Shared pathway33%
Tissue Expression6 tissues
Bone Marrow
100%
Lung
67%
Ovary
47%
Liver
25%
Heart
22%
Brain
20%
Gene Interaction Network
Click a node to explore
CARD19NKIRAS2NKIRAS1MTX2C15orf39NLRX1TSPAN6
PROTEIN STRUCTURE
Preparing viewer…
PDB4FH0 · 1.40 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.56LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF1.12 [0.82–1.56]
RankingsWhere CARD19 stands among ~20K protein-coding genes
  • #13,150of 20,598
    Most Researched24
  • #15,500of 17,882
    Most Constrained (LOEUF)1.56
Genes detectedCARD19
Sources retrieved4 papers
Response time—
📄 Sources
4
1
CARD19, the protein formerly known as BinCARD, is a mitochondrial protein that does not regulate Bcl10-dependent NF-κB activation after TCR engagement.
PMID: 32763502
Cell Immunol · 2020
1.00
2
BinCARD2 as a positive regulator of interferon response in innate immunity.
PMID: 30795865
Biochem Biophys Res Commun · 2019
0.75
3
The structure of the caspase recruitment domain of BinCARD reveals that all three cysteines can be oxidized.
PMID: 23633586
Acta Crystallogr D Biol Crystallogr · 2013
0.50
4
Inhibition of Bcl10-mediated activation of NF-kappa B by BinCARD, a Bcl10-interacting CARD protein.
PMID: 15637807
FEBS Lett · 2004
0.25