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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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CD300A
CD300a molecule
Chromosome 17 · 17q25.1
NCBI Gene: 11314Ensembl: ENSG00000167851.16HGNC: HGNC:19319UniProt: J3QKQ4
44PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
phosphatidylserine bindingnegative regulation of NK T cell activationnegative regulation of phagocytosis, engulfmentnegative regulation of neutrophil activationdengue diseaseinjuryacute myeloid leukemianeoplasm
✦AI Summary

CD300a is an inhibitory immunoreceptor expressed broadly on myeloid and lymphoid cells that negatively regulates immune activation through ITIM-mediated signaling 1. The receptor recognizes phosphatidylserine and phosphatidylethanolamine exposed on apoptotic cells, modulating phagocytosis by macrophages and suppressing engulfment of dead cells 2. CD300a inhibits natural killer cell cytolytic activity 1 and suppresses mast cell and basophil degranulation by downregulating IgE-mediated activation signals 3. Additionally, CD300a negatively regulates MyD88-dependent Toll-like receptor signaling 1 and modulates T cell receptor-mediated calcium mobilization in CD4+ T cells, particularly suppressing activation in Th1-polarized cells 4. Clinically, CD300a has emerged as a universal NK inhibitory target for protecting allogeneic cell therapies; engineered CD300a ligands successfully prevented NK cell-mediated rejection across diverse human donors 5. In ischemic tissue injury, CD300a deficiency enhances macrophage-mediated clearance of dead cells and promotes pro-angiogenic neutrophil responses, resulting in reduced inflammation and adverse cardiac and renal remodeling 6. CD300a expression on marginal zone B cells correlates with enhanced polysaccharide-specific IgM responses, and reduced expression in HIV-infected individuals correlates with impaired pneumococcal immunity 7.

Sources cited
1
CD300a is an inhibitory receptor expressed on myeloid and lymphoid cells, recognizes phosphatidylserine and phosphatidylethanolamine, inhibits NK cell activity, suppresses mast cell degranulation, and negatively regulates MyD88-dependent TLR signaling
PMID: 25980030
2
CD300a binds to phosphatidylserine and phosphatidylethanolamine on apoptotic cells and downregulates macrophage phagocytosis of dead cells
PMID: 22302738
3
CD300a is expressed on human basophils and suppresses IgE-mediated anaphylactic degranulation
PMID: 22173928
4
CD300a is differentially expressed on CD4+ T cells with higher expression on Th1 cells; co-ligation of TCR and CD300a inhibits calcium mobilization and modulates IFN-γ production
PMID: 22046970
5
CD300a-engineered trans-antigen signaling receptors universally protected allogeneic T cells against NK cell responses across 45 human donors with diverse demographics
PMID: 39368806
6
CD300a deficiency enhances macrophage efferocytosis, reduces inflammation, and mitigates adverse remodeling following myocardial infarction and kidney ischemia-reperfusion injury
PMID: 40705472
7
CD300a is expressed on marginal zone IgM memory B cells that show enhanced responses to pneumococcal polysaccharides and TLR9 agonists; CD300a+ B cell frequency is reduced in HIV-infected individuals
PMID: 37762055
Disease Associationsⓘ20
dengue diseaseOpen Targets
0.37Weak
injuryOpen Targets
0.30Weak
acute myeloid leukemiaOpen Targets
0.10Suggestive
neoplasmOpen Targets
0.10Suggestive
diffuse large B-cell lymphomaOpen Targets
0.08Suggestive
non-small cell lung carcinomaOpen Targets
0.08Suggestive
myocardial infarctionOpen Targets
0.07Suggestive
melanomaOpen Targets
0.07Suggestive
post-transplant lymphoproliferative diseaseOpen Targets
0.05Suggestive
infectionOpen Targets
0.05Suggestive
hemolytic anemiaOpen Targets
0.04Suggestive
ThrombocytopeniaOpen Targets
0.04Suggestive
Familial exudative vitreoretinopathyOpen Targets
0.04Suggestive
neutropenia, severe congenital, 1, autosomal dominantOpen Targets
0.04Suggestive
Familial drusenOpen Targets
0.04Suggestive
aortic atherosclerosisOpen Targets
0.04Suggestive
retinitis pigmentosa and erythrocytic microcytosisOpen Targets
0.04Suggestive
autosomal dominant macrothrombocytopeniaOpen Targets
0.04Suggestive
Abruptio PlacentaeOpen Targets
0.04Suggestive
X-linked retinoschisisOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
CD300LBProtein interaction98%PRG2Protein interaction77%RNASE2Protein interaction77%CD300CProtein interaction75%PTPN6Protein interaction72%CD300LFProtein interaction61%
Tissue Expression6 tissues
Lung
100%
Bone Marrow
87%
Liver
38%
Heart
14%
Brain
14%
Ovary
6%
Gene Interaction Network
Click a node to explore
CD300ACD300LBPRG2RNASE2CD300CPTPN6CD300LF
PROTEIN STRUCTURE
Preparing viewer…
PDB2Q87 · 1.70 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.93LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.65 [0.47–0.93]
RankingsWhere CD300A stands among ~20K protein-coding genes
  • #9,566of 20,598
    Most Researched44
  • #8,621of 17,882
    Most Constrained (LOEUF)0.93
Genes detectedCD300A
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Universal protection of allogeneic T-cell therapies from natural killer cells via CD300a agonism.
PMID: 39368806
Blood Adv · 2025
1.00
2
Immunoreceptor CD300a regulates ischemic tissue damage and adverse remodeling in the mouse heart and kidney.
PMID: 40705472
J Clin Invest · 2025
0.90
3
The Biology and Disease Relevance of CD300a, an Inhibitory Receptor for Phosphatidylserine and Phosphatidylethanolamine.
PMID: 25980030
J Immunol · 2015
0.80
4
CD300a and CD300f molecules regulate the function of leukocytes.
PMID: 33548578
Int Immunopharmacol · 2021
0.70
5
Human CD300a binds to phosphatidylethanolamine and phosphatidylserine, and modulates the phagocytosis of dead cells.
PMID: 22302738
Blood · 2012
0.60