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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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DCPS
decapping enzyme, scavenger
Chromosome 11 · 11q24.2
NCBI Gene: 28960Ensembl: ENSG00000110063.11HGNC: HGNC:29812UniProt: A0A384MTI8
60PubMed Papers
21Diseases
0Drugs
7Pathogenic Variants
CLINICAL
OMIM Disease Gene
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
RNA 7-methylguanosine cap bindingmRNA methylguanosine-cap decappingnucleusnucleoplasmautosomal recessive non-syndromic intellectual disabilityneurodegenerative diseaseneuroinflammatory disorderresponse to statin
✦AI Summary

DCPS (decapping enzyme, scavenger) is a cap-hydrolyzing enzyme that catalyzes the cleavage of residual mRNA cap structures following 3'→5' exosome-mediated mRNA decay 1. The enzyme specifically hydrolyzes 7-methylguanosine-capped short oligoribonucleotides (up to ~10 nucleotides), releasing 5'-phosphorylated RNA fragments and m7GMP, but shows no activity on intact capped mRNAs longer than 25 nucleotides 1. This scavenging function prevents accumulation of inhibitory cap structures that would otherwise sequester cap-binding proteins, thereby regulating the availability of these proteins for downstream functions 2. Beyond canonical mRNA decay, DCPS plays regulatory roles in pre-mRNA splicing and may participate in 5'→3' decay pathways 2. Recently, DCPS has emerged as a dependency in cancer and neurodegeneration; DCPS is overexpressed in glioblastoma and associated with poor prognosis, with the DCPS inhibitor RG3039 demonstrating anti-tumor activity through STAT5B downregulation 3. In neurodegenerative disease, DCPS modulates TDP-43-mediated neurodegeneration through processing body (P-body) regulation, identifying it as a potential therapeutic target 4. Mutations in DCPS cause Al-Raqad syndrome, a rare disorder characterized by growth retardation, craniofacial anomalies, and neuromuscular defects 5.

Sources cited
1
DCPS structure, catalytic mechanism of m7GpppN hydrolysis, and role in mRNA metabolism
PMID: 24742626
2
DCPS regulation of cap-binding protein availability and roles in mRNA splicing and decay
PMID: 18948758
3
DCPS overexpression in glioblastoma, association with poor prognosis, and anti-tumor activity of RG3039 via STAT5B downregulation
PMID: 39350123
4
DCPS modulation of TDP-43-mediated neurodegeneration through P-body regulation
PMID: 40661462
5
DCPS mutations cause Al-Raqad syndrome with growth retardation, craniofacial anomalies, and neuromuscular defects
PMID: 30289615
Disease Associationsⓘ21
autosomal recessive non-syndromic intellectual disabilityOpen Targets
0.69Moderate
neurodegenerative diseaseOpen Targets
0.57Moderate
neuroinflammatory disorderOpen Targets
0.43Moderate
response to statinOpen Targets
0.27Weak
urinary system diseaseOpen Targets
0.26Weak
genetic disorderOpen Targets
0.19Weak
coronary atherosclerosisOpen Targets
0.10Weak
interstitial lung diseaseOpen Targets
0.09Suggestive
Romano-Ward syndromeOpen Targets
0.08Suggestive
familial atrial fibrillationOpen Targets
0.08Suggestive
glioblastoma multiformeOpen Targets
0.08Suggestive
metabolic diseaseOpen Targets
0.08Suggestive
dermatomyositisOpen Targets
0.07Suggestive
Familial short QT syndromeOpen Targets
0.07Suggestive
Brugada syndromeOpen Targets
0.07Suggestive
atrial fibrillationOpen Targets
0.07Suggestive
neoplasmOpen Targets
0.07Suggestive
Familial progressive cardiac conduction defectOpen Targets
0.07Suggestive
catecholaminergic polymorphic ventricular tachycardiaOpen Targets
0.07Suggestive
Arrhythmogenic right ventricular dysplasiaOpen Targets
0.07Suggestive
Al-Raqad syndromeUniProt
Pathogenic Variants7
NM_014026.6(DCPS):c.454C>T (p.Arg152Ter)Likely pathogenic
Al-Raqad syndrome
★★☆☆2025→ Residue 152
NM_014026.6(DCPS):c.201+1G>TLikely pathogenic
Al-Raqad syndrome
★☆☆☆2023
NM_014026.6(DCPS):c.856G>T (p.Glu286Ter)Likely pathogenic
Al-Raqad syndrome
★☆☆☆2023→ Residue 286
NM_014026.6(DCPS):c.562C>T (p.Arg188Trp)Likely pathogenic
not provided
★☆☆☆2015→ Residue 188
NM_014026.6(DCPS):c.201+2T>CPathogenic
Al-Raqad syndrome
☆☆☆☆2019
NM_014026.6(DCPS):c.636+1G>APathogenic
Al-Raqad syndrome
☆☆☆☆2019
NM_014026.6(DCPS):c.260C>T (p.Thr87Met)Pathogenic
Al-Raqad syndrome
☆☆☆☆2019→ Residue 87
View on ClinVar ↗
Related Genes
NDOR1Protein interaction95%XRN1Protein interaction87%EIF4EProtein interaction72%DCP2Protein interaction64%DCP1BShared pathway50%EDC4Shared pathway50%
Tissue Expression6 tissues
Liver
100%
Lung
22%
Bone Marrow
20%
Ovary
18%
Heart
18%
Brain
16%
Gene Interaction Network
Click a node to explore
DCPSNDOR1XRN1EIF4EDCP2DCP1BEDC4
PROTEIN STRUCTURE
Preparing viewer…
PDB3BL9 · 1.80 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.00LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.73 [0.53–1.00]
RankingsWhere DCPS stands among ~20K protein-coding genes
  • #7,648of 20,598
    Most Researched60
  • #3,212of 5,498
    Most Pathogenic Variants7
  • #9,656of 17,882
    Most Constrained (LOEUF)1.00
Genes detectedDCPS
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Cytokine-armed dendritic cell progenitors for antigen-agnostic cancer immunotherapy.
PMID: 37996514
Nat Cancer · 2024
1.00
2
Cleaners and airway diseases.
PMID: 33284160
Curr Opin Allergy Clin Immunol · 2021
0.90
3
Effect of the mRNA decapping enzyme scavenger (DCPS) inhibitor RG3039 on glioblastoma.
PMID: 39350123
J Transl Med · 2024
0.80
4
Decapping Scavenger (DcpS) enzyme: advances in its structure, activity and roles in the cap-dependent mRNA metabolism.
PMID: 24742626
Biochim Biophys Acta · 2014
0.70
5
An additional patient with a homozygous mutation in DCPS contributes to the delination of Al-Raqad syndrome.
PMID: 30289615
Am J Med Genet A · 2018
0.60