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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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HERC5
HECT and RLD domain containing E3 ubiquitin protein ligase 5
Chromosome 4 · 4q22.1
NCBI Gene: 51191Ensembl: ENSG00000138646.10HGNC: HGNC:24368UniProt: B4DXV3
105PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
ISG15-protein conjugationRNA bindingcytoplasmprotein bindingtype 2 diabetes mellitusNephropathynephritishepatocellular carcinoma
✦AI Summary

HERC5 (HECT and RLD domain containing E3 ubiquitin protein ligase 5) functions as a crucial E3 ligase that catalyzes ISGylation, a post-translational modification involving the covalent attachment of ISG15 to target proteins 1. The primary function of HERC5 is to enhance antiviral innate immune responses by ISGylating key immune signaling proteins. Mechanistically, HERC5 ISGylates STING at K150, preventing its K48-linked ubiquitination and degradation, thereby facilitating STING activation and type I interferon responses 2. HERC5 also ISGylates the cytosolic DNA sensor cGAS at multiple lysine residues (K21, K187, K219, K458), promoting cGAS oligomerization and enhancing its enzymatic activity 3. Additionally, HERC5 ISGylates NLRP3 inflammasome components, stabilizing the protein by preventing proteasomal degradation 4. Disease relevance includes viral infections, where HERC5 demonstrates potent antiviral activity against hepatitis C, influenza A, HIV, and SARS-CoV-2 1. However, some viruses have evolved countermeasures, such as SARS-CoV-2's papain-like protease that cleaves HERC5-mediated ISGylation 2. Clinically, HERC5 shows cancer-type specific expression patterns, being highly expressed in esophageal cancer, suggesting potential as a therapeutic target 5. HERC5 also inhibits LINE-1 retrotransposition by destabilizing ORF1p 6.

Sources cited
1
HERC5 functions as E3 ligase for ISGylation and shows antiviral activity against multiple viruses
PMID: 34207696
2
HERC5 ISGylates STING at K150, preventing degradation and facilitating activation
PMID: 38652662
3
HERC5 ISGylates cGAS at specific lysine residues, promoting oligomerization and enzymatic activity
PMID: 38421872
4
HERC5 ISGylates NLRP3, stabilizing the protein by preventing proteasomal degradation
PMID: 37651190
5
HERC5 is highly expressed in esophageal cancer with potential therapeutic relevance
PMID: 40446800
6
HERC5 inhibits LINE-1 retrotransposition by destabilizing ORF1p
PMID: 36639706
Disease Associationsⓘ20
type 2 diabetes mellitusOpen Targets
0.16Weak
NephropathyOpen Targets
0.13Weak
nephritisOpen Targets
0.13Weak
hepatocellular carcinomaOpen Targets
0.08Suggestive
oral squamous cell carcinomaOpen Targets
0.08Suggestive
neoplasmOpen Targets
0.07Suggestive
non-small cell lung carcinomaOpen Targets
0.06Suggestive
SepsisOpen Targets
0.04Suggestive
chronic obstructive pulmonary diseaseOpen Targets
0.03Suggestive
lobular neoplasiaOpen Targets
0.03Suggestive
cancerOpen Targets
0.03Suggestive
response to bronchodilatorOpen Targets
0.03Suggestive
juvenile dermatomyositisOpen Targets
0.03Suggestive
osteoarthritis, kneeOpen Targets
0.03Suggestive
idiopathic pulmonary fibrosisOpen Targets
0.03Suggestive
breast cancerOpen Targets
0.03Suggestive
systemic lupus erythematosusOpen Targets
0.02Suggestive
gestational diabetesOpen Targets
0.02Suggestive
colorectal cancerOpen Targets
0.02Suggestive
handednessOpen Targets
0.02Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
STAT2Protein interaction96%IFI6Protein interaction96%IFI27Protein interaction96%IFIT2Protein interaction96%IFIT1Protein interaction96%IFIT3Protein interaction96%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
70%
Lung
27%
Liver
25%
Heart
25%
Brain
17%
Gene Interaction Network
Click a node to explore
HERC5STAT2IFI6IFI27IFIT2IFIT1IFIT3
PROTEIN STRUCTURE
Preparing viewer…
PDB8Y4Z · NMR
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.93LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.72 [0.57–0.93]
RankingsWhere HERC5 stands among ~20K protein-coding genes
  • #4,526of 20,598
    Most Researched105 · top quartile
  • #8,571of 17,882
    Most Constrained (LOEUF)0.93
Genes detectedHERC5
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
ISGylation by HERCs facilitates STING activation.
PMID: 38652662
Cell Rep · 2024
1.00
2
The pan-cancer proteome atlas, a mass spectrometry-based landscape for discovering tumor biology, biomarkers, and therapeutic targets.
PMID: 40446800
Cancer Cell · 2025
0.90
3
Posttranslational ISGylation of NLRP3 by HERC enzymes facilitates inflammasome activation in models of inflammation.
PMID: 37651190
J Clin Invest · 2023
0.80
4
Integrative RNA profiling of TBEV-infected neurons and astrocytes reveals potential pathogenic effectors.
PMID: 35685361
Comput Struct Biotechnol J · 2022
0.70
5
HERC5 and the ISGylation Pathway: Critical Modulators of the Antiviral Immune Response.
PMID: 34207696
Viruses · 2021
0.60