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50 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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HSP90AB1
heat shock protein 90 alpha family class B member 1
Chromosome 6 · 6p21.1
NCBI Gene: 3326Ensembl: ENSG00000096384.21HGNC: HGNC:5258UniProt: B4DGL0
629PubMed Papers
20Diseases
10Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Hub Gene
RESEARCH IMPACT
Highly StudiedTrending
CLINICAL
Clinical Trials
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
identical protein bindingCOP9 signalosomeDNA polymerase bindingprotein phosphatase activator activitymultiple myelomadengue diseasediphtherianon-small cell lung carcinoma
✦AI Summary

HSP90AB1 is a molecular chaperone protein that functions as a key regulator of cellular stress responses and protein homeostasis. Mechanistically, HSP90AB1 operates through ATP-dependent binding interactions, serving as a component of the HSP90-CDC37 chaperone complex 1 and regulating translation of specific mRNAs containing TOP-like motifs downstream of mTORC1 signaling 1. The protein prevents pathological protein misfolding and aggregation, with differential distribution across hippocampal subfields during Alzheimer's disease progression 2. In disease contexts, HSP90AB1 has multiple clinical relevances. In cardiac pathology, HSP90AB1 SUMOylation mediates myocardial fibrosis through STAT3 activation and fibronectin secretion; SENP1-mediated deSUMOylation of HSP90AB1 prevents adverse ventricular remodeling post-infarction 3. HSP90AB1 serves as a pan-EVP (extracellular vesicle/particle) biomarker for cancer detection with 95% sensitivity and 90% specificity in plasma-derived samples 4, and is implicated in osteosarcoma metastasis as a hub gene 5. Additionally, HSP90AB1 promotes pathogenic viral replication by protecting coronavirus nucleocapsid proteins from proteasomal degradation 6 and is associated with immune microenvironment changes in Alzheimer's disease 7. In kidney disease, HSP90AB1 mediates podocyte injury through B7-1-LRP5-β-catenin signaling 8.

Sources cited
1
HSP90AB1 contains TOP-like motifs and is regulated by mTORC1-dependent translation control through 4E-BP and eIF4G1 mechanisms
PMID: 22552098
2
SENP1-mediated deSUMOylation of HSP90AB1 at Lys72 prevents myocardial fibrosis and adverse ventricular remodeling after myocardial infarction by inhibiting STAT3-mediated fibronectin secretion
PMID: 38992961
3
HSP90AB1 is a pan-EVP marker with utility in cancer detection, achieving 95% sensitivity and 90% specificity in plasma-derived samples
PMID: 32795414
4
HSP90AB1 distribution changes across hippocampal subfields and Alzheimer's disease neuropathological stages, suggesting role in chaperone dysregulation contributing to tau and amyloid-β pathology
PMID: 40436281
5
HSP90AB1 mediates podocyte injury and glomerulosclerosis through B7-1 signaling via its N-terminal K69 residue to activate the LRP5/β-catenin pathway
PMID: 35710882
6
HSP90AB1 promotes porcine deltacoronavirus replication by protecting viral N protein from proteasomal degradation through ATP-dependent interactions
PMID: 38092149
7
HSP90AB1 is identified as a hub gene associated with osteosarcoma metastasis through protein-protein interaction network analysis
PMID: 39324133
8
HSP90AB1 is an immune microenvironment-related gene associated with Alzheimer's disease pathological progression and progression prediction
PMID: 36569892
Disease Associationsⓘ20
multiple myelomaOpen Targets
0.40Moderate
dengue diseaseOpen Targets
0.38Weak
diphtheriaOpen Targets
0.37Weak
non-small cell lung carcinomaOpen Targets
0.35Weak
COVID-19Open Targets
0.28Weak
melanomaOpen Targets
0.23Weak
hepatocellular carcinomaOpen Targets
0.22Weak
chronic lymphocytic leukemiaOpen Targets
0.21Weak
small cell lung carcinomaOpen Targets
0.21Weak
head and neck squamous cell carcinomaOpen Targets
0.21Weak
urinary bladder carcinomaOpen Targets
0.21Weak
prostate adenocarcinomaOpen Targets
0.21Weak
esophageal squamous cell carcinomaOpen Targets
0.21Weak
lung adenocarcinomaOpen Targets
0.21Weak
oral squamous cell carcinomaOpen Targets
0.21Weak
diffuse large B-cell lymphomaOpen Targets
0.21Weak
cutaneous melanomaOpen Targets
0.20Weak
acute myeloid leukemiaOpen Targets
0.20Weak
breast carcinomaOpen Targets
0.20Weak
cervical squamous cell carcinomaOpen Targets
0.19Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets10
ALVESPIMYCINPhase II
Heat shock protein HSP90 inhibitor
breast cancer
BIIB021Phase II
Heat shock protein HSP90 inhibitor
breast cancer
CD24FCPhase III
Heat shock 70 kDa protein 1A/1B inhibitor
GANETESPIBPhase III
Heat shock protein HSP90 inhibitor
non-small cell lung carcinoma
LUMINESPIBPhase II
Heat shock protein HSP90 inhibitor
multiple myeloma
ONALESPIBPhase II
Heat shock protein HSP90 inhibitor
RETASPIMYCINPhase II
Heat shock protein HSP90 inhibitor
non-small cell lung carcinoma
RETASPIMYCIN HYDROCHLORIDEPhase III
Heat shock protein HSP90 inhibitor
gastrointestinal stromal tumor
SNX 5422Phase II
Heat shock protein HSP90 inhibitor
cancer
TANESPIMYCINPhase III
Heat shock protein HSP90 inhibitor
multiple myeloma
Related Genes
ARProtein interaction100%CDK4Protein interaction100%ERBB2Protein interaction100%FKBP4Protein interaction100%FKBP5Protein interaction100%NR3C1Protein interaction100%
Tissue Expression6 tissues
Brain
100%
Ovary
86%
Heart
65%
Lung
46%
Bone Marrow
40%
Liver
33%
Gene Interaction Network
Click a node to explore
HSP90AB1ARCDK4ERBB2FKBP4FKBP5NR3C1
PROTEIN STRUCTURE
Preparing viewer…
PDB9D9I · 1.50 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.35Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.23 [0.15–0.35]
RankingsWhere HSP90AB1 stands among ~20K protein-coding genes
  • #360of 20,598
    Most Researched629 · top 5%
  • #1,539of 17,882
    Most Constrained (LOEUF)0.35 · top 10%
Genes detectedHSP90AB1
Sources retrieved50 papers
Response time—
📄 Sources
50▼
1
Extracellular Vesicle and Particle Biomarkers Define Multiple Human Cancers.
PMID: 32795414
Cell · 2020
1.00
2
HSP90β controls NLRP3 autoactivation.
PMID: 38416826
Sci Adv · 2024
0.92
3
A unifying model for mTORC1-mediated regulation of mRNA translation.
PMID: 22552098
Nature · 2012
0.90
4
PARP1 Promotes Heart Regeneration and Cardiomyocyte Proliferation.
PMID: 38481797
Int J Biol Sci · 2024
0.88
5
Suppression of breast cancer-associated bone loss with osteoblast proteomes via Hsp90ab1/moesin-mediated inhibition of TGFβ/FN1/CD44 signaling.
PMID: 34976221
Theranostics · 2022
0.86