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GeneE
27 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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IDO1
indoleamine 2,3-dioxygenase 1
Chromosome 8 · 8p11.21
NCBI Gene: 3620Ensembl: ENSG00000131203.13HGNC: HGNC:6059UniProt: A0A348GSI3
514PubMed Papers
20Diseases
2Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Hub Gene
RESEARCH IMPACT
Highly StudiedTrending
CLINICAL
FDA Approved Target
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
positive regulation of T cell apoptotic processindoleamine 2,3-dioxygenase activityregulation of activated T cell proliferation'de novo' NAD+ biosynthetic process from L-tryptophanneoplasmmelanomahead and neck malignant neoplasiaurogenital neoplasm
✦AI Summary

IDO1 (indoleamine 2,3-dioxygenase 1) catalyzes the first rate-limiting step of tryptophan catabolism along the kynurenine pathway 12. This metabolic activity generates kynurenine, which serves as substrate for NAD+ biosynthesis and 1-carbon metabolism 34. IDO1 functions as a critical immune regulator through dual mechanisms: tryptophan depletion inhibits T cell proliferation, while kynurenine accumulation induces T cell apoptosis and promotes regulatory T cell (Treg) differentiation via aryl hydrocarbon receptor (AhR) activation 56. Additionally, IDO1 expression in dendritic cells enables metabolic communication with other immune cells to maintain immune tolerance 6. In cancer, IDO1 acts as a suppressor of anti-tumor immunity by creating an immunosuppressive tumor microenvironment enriched with exhausted T cells and Tregs 78. IDO1-derived kynurenine also promotes anti-ferroptotic signaling, protecting cancer cells from ferroptotic death 3. Conversely, IDO1 limits intracellular pathogen growth through tryptophan depletion and protects fetuses from maternal immune rejection 9. In EBV-infected B cells, EBNA2-driven IDO1 expression sustains NAD biosynthesis supporting oncogenic transformation 4. IDO1 inhibition shows therapeutic potential in cancer and EBV-associated lymphoma 47.

Sources cited
1
IDO1 catalyzes the first rate-limiting step of tryptophan catabolism along the kynurenine pathway
PMID: 17671174
2
IDO1 catalyzes the first rate-limiting step of tryptophan catabolism along the kynurenine pathway
PMID: 18026683
3
IDO1 maintains immune tolerance, limits intracellular pathogen growth, and protects fetuses from maternal immune rejection
PMID: 25691885
4
IDO1-derived kynurenine generates metabolites that suppress ferroptotic cell death through ROS scavenging and AhR-independent pathways
PMID: 35245456
5
IDO1 expression in mature dendritic cells enables metabolic communication extending immunoregulatory capacity through kynurenine production
PMID: 35704993
6
Tryptophan depletion sensitizes AhR pathway and potentiates Treg differentiation; kynurenine activates AhR to suppress immunity
PMID: 37344101
7
EBV protein EBNA2 drives IDO1 expression to sustain NAD biosynthesis supporting B cell transformation and lymphomagenesis
PMID: 38781354
8
IDO1-expressing macrophages create immunosuppressive tumor microenvironment in oral carcinogenesis; IDO1 inhibition reduces carcinogenesis
PMID: 39239507
9
Tolerogenic IDO1+ dendritic cells in pancreatic cancer spleens contribute to systemic immunosuppression through AhR and IDO1 signaling
PMID: 39547331
Disease Associationsⓘ20
neoplasmOpen Targets
0.42Moderate
melanomaOpen Targets
0.39Weak
head and neck malignant neoplasiaOpen Targets
0.34Weak
urogenital neoplasmOpen Targets
0.33Weak
renal cell carcinomaOpen Targets
0.29Weak
stomach diseaseOpen Targets
0.27Weak
skin cancerOpen Targets
0.27Weak
facial morphologyOpen Targets
0.24Weak
cancerOpen Targets
0.14Weak
head and neck squamous cell carcinomaOpen Targets
0.13Weak
non-small cell lung carcinomaOpen Targets
0.12Weak
ulcerative colitisOpen Targets
0.12Weak
colorectal carcinomaOpen Targets
0.12Weak
breast cancerOpen Targets
0.11Weak
acute myeloid leukemiaOpen Targets
0.11Weak
hepatocellular carcinomaOpen Targets
0.11Weak
infectionOpen Targets
0.11Weak
glioblastoma multiformeOpen Targets
0.11Weak
chronic kidney diseaseOpen Targets
0.11Weak
oral squamous cell carcinomaOpen Targets
0.11Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets2
EPACADOSTATApproved
Indoleamine 2,3-dioxygenase inhibitor
neoplasm
LINRODOSTATPhase III
Indoleamine 2,3-dioxygenase inhibitor
melanoma
Related Genes
CD8AProtein interaction100%TNFSF18Protein interaction100%IFNGProtein interaction99%QPRTProtein interaction98%FOXP3Protein interaction98%IL10Protein interaction98%
Tissue Expression6 tissues
Lung
100%
Heart
10%
Liver
2%
Ovary
1%
Brain
0%
Bone Marrow
0%
Gene Interaction Network
Click a node to explore
IDO1CD8ATNFSF18IFNGQPRTFOXP3IL10
PROTEIN STRUCTURE
Preparing viewer…
PDB8ABX · 1.65 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.24LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.80 [0.54–1.24]
RankingsWhere IDO1 stands among ~20K protein-coding genes
  • #513of 20,598
    Most Researched514 · top 5%
  • #741of 1,025
    FDA-Approved Drug Targets1
  • #13,036of 17,882
    Most Constrained (LOEUF)1.24
Genes detectedIDO1
Sources retrieved27 papers
Response time—
📄 Sources
27▼
1
IL-1β-induced epithelial cell and fibroblast transdifferentiation promotes neutrophil recruitment in chronic rhinosinusitis with nasal polyps.
PMID: 39438439
Nat Commun · 2024
1.00
2
Kynurenine importation by SLC7A11 propagates anti-ferroptotic signaling.
PMID: 35245456
Mol Cell · 2022
1.00
3
Indoleamine 2,3-dioxygenase 1 activation in mature cDC1 promotes tolerogenic education of inflammatory cDC2 via metabolic communication.
PMID: 35704993
Immunity · 2022
0.90
4
The IFN-γ-IDO1-kynureine pathway-induced autophagy in cervical cancer cell promotes phagocytosis of macrophage.
PMID: 33390854
Int J Biol Sci · 2021
0.80
5
Role of indoleamine 2,3-dioxygenase 1 (IDO1) and kynurenine pathway in the regulation of the aging process.
PMID: 35085834
Ageing Res Rev · 2022
0.70