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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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MAP3K15
mitogen-activated protein kinase kinase kinase 15
Chromosome X · Xp22.12
NCBI Gene: 389840Ensembl: ENSG00000180815.16HGNC: HGNC:31689UniProt: Q6ZN16
25PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Kinase
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
MAP kinase kinase kinase activityJNK cascadep38MAPK cascadeMAPK cascadediabetes mellitusneurodegenerative diseasegestational diabeteshypertension
✦AI Summary

MAP3K15 (mitogen-activated protein kinase kinase kinase 15) is a serine/threonine kinase that functions as an upstream component of the MAP kinase signaling pathway, particularly activating the p38 MAPK cascade through phosphorylation of downstream MAP kinase kinases 1. The protein plays a protective role against metabolic dysfunction, as rare damaging variants in MAP3K15 are associated with 30% reduced risk of diabetes development and lower glycosylated hemoglobin levels, independent of body mass index 2. This protective effect extends to both type 1 and type 2 diabetes, with protein-truncating variants showing similar benefits in Finnish populations 2. MAP3K15 variants have been implicated in male-predominant congenital heart disease, where X-linked rare damaging variants contribute to sex differences in disease prevalence 3. The gene has also been identified as a potential biomarker in various conditions including nonobstructive azoospermia 4, giant congenital melanocytic nevus 5, and idiopathic pulmonary fibrosis 6. Additionally, MAP3K15 serves as a specific marker for hippocampal CA2 neurons, enabling targeted research of this brain region's role in social memory 7. The gene's diverse roles suggest it functions as an important regulatory node in multiple physiological pathways.

Sources cited
1
MAP3K15 is a serine/threonine kinase that activates p38 MAPK cascade
PMID: 31196660
2
Rare damaging variants in MAP3K15 reduce diabetes risk by 30% and lower glycosylated hemoglobin
PMID: 36383675
3
X-linked MAP3K15 variants contribute to sex differences in congenital heart disease
PMID: 40347836
4
MAP3K15 identified as potential candidate gene for nonobstructive azoospermia
PMID: 36017582
5
MAP3K15 mutations associated with giant congenital melanocytic nevus
PMID: 36085074
6
MAP3K15 identified as key gene associated with idiopathic pulmonary fibrosis
PMID: 40187620
7
MAP3K15 serves as specific marker for hippocampal CA2 neurons
PMID: 37303064
Disease Associationsⓘ20
diabetes mellitusOpen Targets
0.46Moderate
neurodegenerative diseaseOpen Targets
0.41Moderate
gestational diabetesOpen Targets
0.30Weak
hypertensionOpen Targets
0.25Weak
type 2 diabetes mellitusOpen Targets
0.19Weak
pyruvate dehydrogenase E1-alpha deficiencyOpen Targets
0.19Weak
Neurodevelopmental disorderOpen Targets
0.12Weak
focal segmental glomerulosclerosisOpen Targets
0.07Suggestive
IGA glomerulonephritisOpen Targets
0.07Suggestive
familial idiopathic steroid-resistant nephrotic syndromeOpen Targets
0.07Suggestive
polycystic kidney disease 7Open Targets
0.06Suggestive
glomerulopathy with fibronectin deposits 2Open Targets
0.06Suggestive
glomerulopathy with fibronectin deposits 1Open Targets
0.05Suggestive
essential hypertensionOpen Targets
0.05Suggestive
essential hypertension, geneticOpen Targets
0.05Suggestive
nail-patella-like renal diseaseOpen Targets
0.05Suggestive
focal segmental glomerulosclerosis 5Open Targets
0.05Suggestive
Autosomal dominant polycystic kidney diseaseOpen Targets
0.05Suggestive
Denys-Drash syndromeOpen Targets
0.05Suggestive
autosomal dominant progressive nephropathy with hypertensionOpen Targets
0.05Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
MAP3K6Shared pathway75%SBK2Shared pathway33%RCE1Shared pathway33%DUSP9Shared pathway33%MAPK10Shared pathway25%MAP3K4Shared pathway25%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
52%
Lung
28%
Liver
24%
Brain
17%
Heart
13%
Gene Interaction Network
Click a node to explore
MAP3K15MAP3K6SBK2RCE1DUSP9MAPK10MAP3K4
PROTEIN STRUCTURE
Preparing viewer…
PDB6V0M · 1.80 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.45LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF1.25 [1.08–1.45]
RankingsWhere MAP3K15 stands among ~20K protein-coding genes
  • #13,015of 20,598
    Most Researched25
  • #14,841of 17,882
    Most Constrained (LOEUF)1.45
Genes detectedMAP3K15
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Exome sequencing and analysis of 454,787 UK Biobank participants.
PMID: 34662886
Nature · 2021
1.00
2
Whole-genome sequencing identifies new candidate genes for nonobstructive azoospermia.
PMID: 36017582
Andrology · 2022
0.90
3
MAP3K kinases and kidney injury.
PMID: 31196660
Nefrologia (Engl Ed) · 2019
0.80
4
Rare damaging variants in the sex differences of congenital heart disease: an exome sequencing study.
PMID: 40347836
EBioMedicine · 2025
0.70
5
Human genetics uncovers
PMID: 36383675
Sci Adv · 2022
0.60