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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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MCTP2
multiple C2 and transmembrane domain containing 2
Chromosome 15 · 15q26.2
NCBI Gene: 55784Ensembl: ENSG00000140563.17HGNC: HGNC:25636UniProt: Q6DN12
34PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
calcium-dependent phospholipid bindingcalcium ion bindingnucleoplasmcytosolheart diseasenephritiskidney diseaseAbnormality of the skeletal system
✦AI Summary

MCTP2 (multiple C2 and transmembrane domain containing 2) is a calcium-binding transmembrane protein with critical roles in cardiac development and neurological function. Primary function: MCTP2 is a dosage-sensitive gene required for cardiac outflow tract (OT) development 1. The protein contains multiple C2 domains and transmembrane regions, enabling calcium-dependent phospholipid binding [GO annotations]. Mechanism: MCTP2 functions in lipid droplet biogenesis at specialized ER sites marked by reticulon-like proteins 2, and regulates neurotransmitter secretion through calcium-mediated signaling [GO annotations]. Disease relevance: MCTP2 mutations cause congenital prosopagnosia (face blindness), with frameshift mutations (S80fs) showing complete cosegregation with impaired face recognition and reduced repetition suppression in the fusiform face area 3. Heterozygous deletions and duplications cause coarctation of the aorta (CoA) and hypoplastic left heart syndrome (HLHS) 1. Clinical significance: MCTP2 is upregulated in recurrent glioblastoma, correlating with poor survival and immune checkpoint marker expression (PD-L1, CTLA-4), suggesting roles in immune evasion and drug resistance 4. MCTP2 variants also associate with Lewy body pathology 5 and promote tumor progression in oral squamous cell carcinoma through EMT-related mechanisms 6.

Sources cited
1
MCTP2 is a dosage-sensitive gene required for cardiac outflow tract development; deletions and duplications cause coarctation of aorta and hypoplastic left heart syndrome
PMID: 23773997
2
MCTP2 mutations cause congenital prosopagnosia with cosegregating frameshift mutations and impaired face recognition in fusiform face area
PMID: 38547502
3
MCTP2 is upregulated in recurrent glioblastoma, correlates with poor survival and immune checkpoint markers, promotes drug resistance
PMID: 41291342
4
MCTP2 (Pex30/MCTP2) marks special ER sites where lipid droplets preferentially arise
PMID: 31075519
5
MCTP2 expression elevated in oral squamous cell carcinoma, associated with lymph node metastasis and EMT phenotype
PMID: 40425609
6
MCTP2 variant (LINC01581/MCTP2 rs547411734) associated with lower middle frontal Lewy body counts in discovery series
PMID: 40091616
7
MCTP2 identified as gene involved in cardiac development and heart rate response to exercise
PMID: 30919020
8
MCTP2 identified as candidate gene for human disease with recessive inheritance pattern in consanguineous population
PMID: 28600779
Disease Associationsⓘ20
heart diseaseOpen Targets
0.36Weak
nephritisOpen Targets
0.33Weak
kidney diseaseOpen Targets
0.31Weak
Abnormality of the skeletal systemOpen Targets
0.31Weak
gram-negative bacterial infectionsOpen Targets
0.29Weak
AlkalosisOpen Targets
0.29Weak
pyogenic granulomaOpen Targets
0.28Weak
systemic inflammatory response syndromeOpen Targets
0.28Weak
enteritisOpen Targets
0.27Weak
HypercholesterolemiaOpen Targets
0.27Weak
temporomandibular joint disorderOpen Targets
0.25Weak
ovarian neoplasmOpen Targets
0.24Weak
muscular diseaseOpen Targets
0.23Weak
insomniaOpen Targets
0.23Weak
primary thrombocytopeniaOpen Targets
0.19Weak
obesityOpen Targets
0.19Weak
genetic disorderOpen Targets
0.19Weak
atherosclerosisOpen Targets
0.19Weak
hypertensionOpen Targets
0.18Weak
multinodular goiterOpen Targets
0.18Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
RCAN2Shared pathway50%MCTP1Shared pathway33%RCAN3Shared pathway33%TSPOAP1Shared pathway25%GNA15Shared pathway25%DYSFShared pathway25%
Tissue Expression6 tissues
Bone Marrow
100%
Lung
66%
Ovary
9%
Liver
9%
Brain
4%
Heart
2%
Gene Interaction Network
Click a node to explore
MCTP2RCAN2MCTP1RCAN3TSPOAP1GNA15DYSF
PROTEIN STRUCTURE
Preparing viewer…
PDB2EP6 · NMR
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.33LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF1.09 [0.90–1.33]
RankingsWhere MCTP2 stands among ~20K protein-coding genes
  • #11,185of 20,598
    Most Researched34
  • #13,933of 17,882
    Most Constrained (LOEUF)1.33
Genes detectedMCTP2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
The landscape of genetic diseases in Saudi Arabia based on the first 1000 diagnostic panels and exomes.
PMID: 28600779
Hum Genet · 2017
1.00
2
Lipid droplet biogenesis.
PMID: 31075519
Curr Opin Cell Biol · 2019
0.90
3
Investigating the impact of MCTP2 on immune suppression and drug resistance in glioblastoma.
PMID: 41291342
Funct Integr Genomics · 2025
0.80
4
Genome-wide association study of neuropathological features in Lewy body disease.
PMID: 40091616
Brain · 2025
0.70
5
MCTP2 is a novel biomarker promoting tumor progression and nodal metastasis in oral squamous cell carcinoma.
PMID: 40425609
Sci Rep · 2025
0.60