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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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MST1
macrophage stimulating 1
Chromosome 3 · 3p21.31
NCBI Gene: 4485Ensembl: ENSG00000173531.16HGNC: HGNC:7380UniProt: G3XAK1
105PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
regulation of cAMP-dependent protein kinase activityGO:0005615receptor tyrosine kinase bindingextracellular matrixinflammatory bowel diseaseulcerative colitisCrohn's diseasesclerosing cholangitis
✦AI Summary

MST1 (macrophage stimulating 1) is a serine/threonine kinase and core component of the Hippo signaling pathway, a conserved cascade regulating cell proliferation, survival, and organ size control 1. MST1 functions as part of a kinase cascade with MST2 and LATS1/2 to phosphorylate and inhibit the transcriptional coactivators YAP and TAZ, thereby suppressing cell growth programs 1. MST1 mechanistically responds to diverse signals including mechanical forces and cellular stress; for example, oscillatory shear stress inhibits MST1 phosphorylation, reducing its ability to phosphorylate connexin 43 and leading to endothelial dysfunction and atherosclerosis 2. MST1 also phosphorylates Nur77 at threonine 366 to enhance endometrial receptivity by promoting β3-integrin expression, facilitating embryo implantation 3. In liver, accumulated glycogen sequesters MST1/2 in liquid droplets, blocking Hippo signaling and promoting YAP-dependent tumorigenesis 4. MST1 inhibition by IL-17A in keratinocytes reduces MST1-LATS1 interaction, activating YAP-AREG signaling in psoriasis 5. Pharmacological MST1/2 inhibition augments tissue repair and regeneration 6. Genetically predicted MST1 levels show inverse association with inflammatory bowel disease risk 7, suggesting therapeutic potential in IBD management.

Sources cited
1
MST1/2 are core kinases in the Hippo pathway regulating cell growth, proliferation, survival, and organ size control
PMID: 30566373
2
Oscillatory shear stress inhibits MST1 phosphorylation, reducing connexin 43 phosphorylation and promoting endothelial dysfunction and atherosclerosis
PMID: 36164986
3
MST1 phosphorylates Nur77 at threonine 366 to enhance β3-integrin expression and endometrial receptivity for embryo implantation
PMID: 36623453
4
Accumulated glycogen sequesters MST1/2 in liquid droplets, blocking Hippo signaling and promoting YAP-dependent liver tumorigenesis
PMID: 34678143
5
IL-17A promotes MST1 recruitment to ACT1, reducing MST1-LATS1 interaction and activating YAP-AREG signaling in psoriatic keratinocytes
PMID: 35304250
6
MST1/2 inhibition augments tissue repair and regeneration in intestinal and liver injury models
PMID: 27535619
7
Genetically predicted MST1 levels are inversely associated with inflammatory bowel disease risk
PMID: 36857861
8
Oxidative stress promotes MOB1 acetylation, which increases phosphorylation and activates LATS1 downstream of MST1/2
PMID: 35349706
Disease Associationsⓘ20
inflammatory bowel diseaseOpen Targets
0.52Moderate
ulcerative colitisOpen Targets
0.51Moderate
Crohn's diseaseOpen Targets
0.49Moderate
sclerosing cholangitisOpen Targets
0.48Moderate
ulcer diseaseOpen Targets
0.39Weak
ulcerative proctosigmoiditisOpen Targets
0.38Weak
hypertensionOpen Targets
0.37Weak
psoriasisOpen Targets
0.34Weak
ankylosing spondylitisOpen Targets
0.34Weak
proctitisOpen Targets
0.32Weak
colitisOpen Targets
0.31Weak
enteritisOpen Targets
0.31Weak
intelligenceOpen Targets
0.30Weak
mathematical abilityOpen Targets
0.30Weak
endometriosisOpen Targets
0.29Weak
prostate carcinomaOpen Targets
0.27Weak
ileocolitisOpen Targets
0.26Weak
chronic obstructive pulmonary diseaseOpen Targets
0.26Weak
Back painOpen Targets
0.26Weak
Abnormality of the skeletal systemOpen Targets
0.25Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
MST1RProtein interaction100%APEHProtein interaction84%SPINT1Protein interaction83%HPNProtein interaction83%SPINT2Protein interaction82%SAV1Protein interaction82%
Tissue Expression6 tissues
Liver
100%
Bone Marrow
2%
Ovary
1%
Lung
1%
Heart
0%
Brain
0%
Gene Interaction Network
Click a node to explore
MST1MST1RAPEHSPINT1HPNSPINT2SAV1
PROTEIN STRUCTURE
Preparing viewer…
PDB2ASU · 1.85 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.95LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.79 [0.65–0.95]
RankingsWhere MST1 stands among ~20K protein-coding genes
  • #4,543of 20,598
    Most Researched105 · top quartile
  • #8,901of 17,882
    Most Constrained (LOEUF)0.95
Genes detectedMST1
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
The Hippo Pathway: Biology and Pathophysiology.
PMID: 30566373
Annu Rev Biochem · 2019
1.00
2
Glycogen accumulation and phase separation drives liver tumor initiation.
PMID: 34678143
Cell · 2021
0.90
3
MST1 Suppresses Disturbed Flow Induced Atherosclerosis.
PMID: 36164986
Circ Res · 2022
0.80
4
Mst1-mediated phosphorylation of Nur77 improves the endometrial receptivity in human and mice.
PMID: 36623453
EBioMedicine · 2023
0.70
5
IL-17A Promotes Psoriasis-Associated Keratinocyte Proliferation through ACT1-Dependent Activation of YAP-AREG Axis.
PMID: 35304250
J Invest Dermatol · 2022
0.60