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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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OLIG2
oligodendrocyte transcription factor 2
Chromosome 21 · 21q22.11
NCBI Gene: 10215Ensembl: ENSG00000205927.6HGNC: HGNC:9398UniProt: Q13516
101PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
OncogeneTranscription Factor
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingsequence-specific double-stranded DNA bindingE-box bindingaxon developmentcolon adenocarcinomaEndometrial Endometrioid Adenocarcinomacolorectal adenocarcinomasmall cell lung carcinoma
✦AI Summary

OLIG2 (oligodendrocyte transcription factor 2) is a basic helix-loop-helix transcription factor essential for oligodendrocyte development and glioblastoma biology. In normal development, OLIG2 is required for oligodendrocyte specification and differentiation, functioning in combination with other transcription factors like SOX10 and NKX6.2 to directly reprogram human fibroblasts into oligodendrocyte-like cells within 16 days 1. During neural development, OLIG2+ cells differentiate from PAX6+ neural stem cells around day 12, subsequently expressing NKX2.2 and SOX10 as they progress toward mature oligodendrocytes 2. In glioblastoma pathology, OLIG2 plays a critical oncogenic role as part of a core set of neurodevelopmental transcription factors (POU3F2, SOX2, SALL2, and OLIG2) essential for tumor propagation 3. OLIG2 functions redundantly with ASCL1 to drive glioblastoma initiation and regulate tumor cell heterogeneity 4. Notably, OLIG2+ glioma cells exhibit distinct biological properties, promoting single-cell vessel co-option through Wnt7b signaling while preserving the blood-brain barrier, contrasting with OLIG2-negative cells that form dense perivascular collections and promote angiogenesis 5. This dual role in normal oligodendrocyte development and glioblastoma progression makes OLIG2 a significant therapeutic target.

Sources cited
1
OLIG2 functions with SOX10 and NKX6.2 to directly reprogram human fibroblasts into oligodendrocyte-like cells within 16 days
PMID: 33770499
2
OLIG2+ cells differentiate from PAX6+ neural stem cells around day 12 during oligodendrocyte development
PMID: 26134954
3
OLIG2 is part of a core set of transcription factors essential for glioblastoma tumor-propagating cell function
PMID: 24726434
4
OLIG2 functions redundantly with ASCL1 to drive glioblastoma initiation and regulate tumor cell heterogeneity
PMID: 39609428
5
OLIG2+ glioma cells promote single-cell vessel co-option through Wnt7b signaling while preserving blood-brain barrier integrity
PMID: 29681511
Disease Associationsⓘ20
colon adenocarcinomaOpen Targets
0.37Weak
colorectal adenocarcinomaOpen Targets
0.37Weak
Endometrial Endometrioid AdenocarcinomaOpen Targets
0.37Weak
small cell lung carcinomaOpen Targets
0.28Weak
breast carcinomaOpen Targets
0.28Weak
breast ductal adenocarcinomaOpen Targets
0.28Weak
cecum adenocarcinomaOpen Targets
0.28Weak
cervical squamous cell carcinomaOpen Targets
0.28Weak
esophageal adenocarcinomaOpen Targets
0.28Weak
gastric carcinomaOpen Targets
0.28Weak
gastric intestinal type adenocarcinomaOpen Targets
0.28Weak
Hepatobiliary NeoplasmOpen Targets
0.28Weak
hepatocellular carcinomaOpen Targets
0.28Weak
lung adenocarcinomaOpen Targets
0.28Weak
rectal adenocarcinomaOpen Targets
0.28Weak
skin basal cell carcinomaOpen Targets
0.28Weak
soft tissue sarcomaOpen Targets
0.28Weak
squamous cell lung carcinomaOpen Targets
0.28Weak
thyroid carcinomaOpen Targets
0.28Weak
urinary bladder carcinomaOpen Targets
0.28Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
AIF1Protein interaction92%CNPProtein interaction92%MBPProtein interaction92%PLP1Protein interaction92%S100BProtein interaction92%SOX10Protein interaction92%
Tissue Expression6 tissues
Brain
100%
Bone Marrow
1%
Lung
0%
Ovary
0%
Heart
0%
Liver
0%
Gene Interaction Network
Click a node to explore
OLIG2AIF1CNPMBPPLP1S100BSOX10
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q13516
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
1.84LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF1.25 [0.79–1.84]
RankingsWhere OLIG2 stands among ~20K protein-coding genes
  • #4,732of 20,598
    Most Researched101 · top quartile
  • #16,789of 17,882
    Most Constrained (LOEUF)1.84
Genes detectedOLIG2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Reconstructing and reprogramming the tumor-propagating potential of glioblastoma stem-like cells.
PMID: 24726434
Cell · 2014
1.00
2
Transcription factors ASCL1 and OLIG2 drive glioblastoma initiation and co-regulate tumor cell types and migration.
PMID: 39609428
Nat Commun · 2024
0.90
3
Single-cell RNA-sequencing of human eosinophils in allergic inflammation in the esophagus.
PMID: 38871184
J Allergy Clin Immunol · 2024
0.80
4
One-step Reprogramming of Human Fibroblasts into Oligodendrocyte-like Cells by SOX10, OLIG2, and NKX6.2.
PMID: 33770499
Stem Cell Reports · 2021
0.70
5
Generation and isolation of oligodendrocyte progenitor cells from human pluripotent stem cells.
PMID: 26134954
Nat Protoc · 2015
0.60