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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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PBK
PDZ binding kinase
Chromosome 8 · 8p21.1
NCBI Gene: 55872Ensembl: ENSG00000168078.11HGNC: HGNC:18282UniProt: Q96KB5
145PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Hub GeneKinase
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingnucleusprotein serine/threonine kinase activitymitotic cell cyclehepatocellular carcinomaneoplasmcancerglioblastoma multiforme
✦AI Summary

PDZ binding kinase (PBK) is a serine/threonine kinase primarily active during mitosis that phosphorylates MAP kinase p38 and regulates cell cycle progression 1. PBK functions as a cell proliferation driver through phosphorylation of PRC1, promoting cytokinesis and G2/M phase progression 2. When phosphorylated, PBK forms complexes with TP53, attenuating G2/M checkpoint control during DNA damage [UniProt]. Mechanistically, PBK phosphorylates key regulatory proteins including TRIM37 (promoting NFκB pathway activation) 1 and TIPE2 (regulating ubiquitin-mediated degradation) 3, while interacting with PRC1 to modulate cytokinesis 2. Clinically, PBK dysregulation drives multiple malignancies. Elevated PBK expression confers PARP inhibitor resistance in ovarian cancer through TRIM37/NFκB axis activation and associates with poor prognosis in medulloblastoma and pituitary neuroendocrine tumors 145. In pulmonary arterial hypertension, PBK upregulation in pulmonary artery smooth muscle cells promotes pathological vascular remodeling; PBK inhibition or genetic knockout prevented disease development in animal models 2. PBK also regulates neuroinflammation by disrupting TIPE2 interactions, with PBK inhibition reducing lipopolysaccharide-induced microglial activation 3. These findings establish PBK as a therapeutic target across cancer, cardiovascular, and neuroinflammatory diseases.

Sources cited
1
PBK promotes PARP inhibitor resistance in ovarian cancer through TRIM37 phosphorylation and NFκB pathway activation
PMID: 35859118
2
PBK is upregulated in pulmonary artery smooth muscle cells and promotes proliferation through PRC1 phosphorylation and cytokinesis; PBK inhibition reverses pulmonary hypertension in animal models
PMID: 38682326
3
PBK regulates neuroinflammation by interacting with TIPE2; PBK inhibition reduces LPS-mediated microglial activation and neuroinflammation
PMID: 40658838
4
PBK is upregulated in medulloblastoma and higher expression associates with poor prognosis; PBK inhibition impairs MB cell proliferation and induces apoptosis
PMID: 35593307
5
PBK overexpression promotes pituitary neuroendocrine tumor cell proliferation and migration, and is associated with poor prognosis in PitNET patients
PMID: 38167466
Disease Associationsⓘ20
hepatocellular carcinomaOpen Targets
0.12Weak
neoplasmOpen Targets
0.12Weak
cancerOpen Targets
0.11Weak
glioblastoma multiformeOpen Targets
0.11Weak
breast cancerOpen Targets
0.11Weak
non-small cell lung carcinomaOpen Targets
0.10Weak
gastric cancerOpen Targets
0.10Weak
esophageal squamous cell carcinomaOpen Targets
0.10Weak
gliomaOpen Targets
0.10Suggestive
lung adenocarcinomaOpen Targets
0.10Suggestive
prostate cancerOpen Targets
0.10Suggestive
ovarian cancerOpen Targets
0.10Suggestive
renal cell carcinomaOpen Targets
0.10Suggestive
psoriasisOpen Targets
0.10Suggestive
nasopharyngeal carcinomaOpen Targets
0.09Suggestive
lung cancerOpen Targets
0.09Suggestive
colorectal carcinomaOpen Targets
0.09Suggestive
Miyoshi myopathyOpen Targets
0.09Suggestive
colon carcinomaOpen Targets
0.09Suggestive
Mobius syndromeOpen Targets
0.08Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
CENPAProtein interaction98%CDC20Protein interaction98%CENPEProtein interaction98%FOXM1Protein interaction98%NEK2Protein interaction98%PCLAFProtein interaction98%
Tissue Expression6 tissues
Bone Marrow
100%
Brain
24%
Lung
3%
Liver
1%
Heart
1%
Ovary
0%
Gene Interaction Network
Click a node to explore
PBKCENPACDC20CENPEFOXM1NEK2PCLAF
PROTEIN STRUCTURE
Preparing viewer…
PDB5J0A · 2.74 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.06LoF Tolerant
pLIⓘ
0.43Tolerant
Observed/Expected LoF0.34 [0.14–1.06]
RankingsWhere PBK stands among ~20K protein-coding genes
  • #3,144of 20,598
    Most Researched145 · top quartile
  • #10,606of 17,882
    Most Constrained (LOEUF)1.06
Genes detectedPBK
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
PBK drives PARP inhibitor resistance through the TRIM37/NFκB axis in ovarian cancer.
PMID: 35859118
Exp Mol Med · 2022
1.00
2
PDZ-Binding Kinase, a Novel Regulator of Vascular Remodeling in Pulmonary Arterial Hypertension.
PMID: 38682326
Circulation · 2024
0.90
3
Nano- and microplastic PBK modeling in the context of human exposure and risk assessment.
PMID: 38537584
Environ Int · 2024
0.80
4
Targeting PBK with small-molecule 1-
PMID: 40658838
Proc Natl Acad Sci U S A · 2025
0.70
5
Identification of PBK as a hub gene and potential therapeutic target for medulloblastoma.
PMID: 35593307
Oncol Rep · 2022
0.60