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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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PLA2G15
phospholipase A2 group XV
Chromosome 16 · 16q22.1
NCBI Gene: 23659Ensembl: ENSG00000103066.13HGNC: HGNC:17163UniProt: B4DJW4
41PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
phosphatidylcholine metabolic processphosphatidylglycerol metabolic processGO:0005615protein bindingAbnormality of the skeletal systemmathematical abilitydisease of peritoneummetabolic syndrome
✦AI Summary

PLA2G15 is a lysosomal phospholipase A2 enzyme with dual phospholipase and O-acyltransferase activities that plays crucial roles in lysosomal lipid homeostasis 1. The enzyme exhibits calcium-independent activity with an acidic pH optimum and preferentially hydrolyzes the sn-1 fatty acyl group of phospholipids, including phosphatidylcholines, phosphatidylethanolamines, and phosphatidylglycerols 1. Mechanistically, PLA2G15 serves as a key regulator of bis(monoacylglycero)phosphate (BMP) catabolism in lysosomes, where it acts as a physiological BMP hydrolase essential for lysosomal lipid turnover 23. The enzyme can transfer fatty acyl groups to lipophilic alcohols and is involved in processing oxidized phospholipids during oxidative stress 1. Disease relevance is significant, as PLA2G15 dysfunction contributes to multiple pathological conditions. The enzyme is inhibited by glycerophosphodiesters in Batten disease, leading to toxic lysophospholipid accumulation 4. Additionally, PLA2G15 inhibition by cationic amphiphilic drugs predicts drug-induced phospholipidosis 5. Clinically, targeting PLA2G15 shows therapeutic potential - its inhibition ameliorates Niemann-Pick disease type C1 pathologies and extends lifespan in mouse models 2. The enzyme also promotes healthy aging, as its suppression improves healthspan in C. elegans 6.

Sources cited
1
PLA2G15 is a lysosomal phospholipase A2 with calcium-independent activity, acidic pH optimum, and dual phospholipase/O-acyltransferase activities
PMID: 30077006
2
PLA2G15 is a physiological BMP hydrolase that catabolizes BMP lipids in lysosomes
PMID: 40335701
3
PLA2G15 regulates BMP lipid catabolism and is controlled by TFEB
PMID: 40373767
4
PLA2G15 is inhibited by glycerophosphodiesters in Batten disease, leading to lysophospholipid accumulation
PMID: 38447580
5
PLA2G15 inhibition by cationic amphiphilic drugs predicts drug-induced phospholipidosis
PMID: 34087196
6
Targeting PLA2G15 ameliorates Niemann-Pick disease type C1 pathologies and extends lifespan
PMID: 40335701
7
PLA2G15 suppression improves healthspan and promotes healthy aging in C. elegans
PMID: 40655094
Disease Associationsⓘ20
Abnormality of the skeletal systemOpen Targets
0.12Weak
mathematical abilityOpen Targets
0.07Suggestive
disease of peritoneumOpen Targets
0.07Suggestive
metabolic syndromeOpen Targets
0.06Suggestive
refractive errorOpen Targets
0.05Suggestive
Familial hemophagocytic lymphohistiocytosisOpen Targets
0.05Suggestive
familial hypercholesterolemiaOpen Targets
0.05Suggestive
infectionOpen Targets
0.05Suggestive
pulmonary alveolar proteinosis with hypogammaglobulinemiaOpen Targets
0.04Suggestive
activated PI3K-delta syndromeOpen Targets
0.04Suggestive
homozygous familial hypercholesterolemiaOpen Targets
0.04Suggestive
autoimmune lymphoproliferative syndrome type 4Open Targets
0.04Suggestive
RAS-associated autoimmune leukoproliferative diseaseOpen Targets
0.04Suggestive
sitosterolemia 2Open Targets
0.04Suggestive
sea-blue histiocyte syndromeOpen Targets
0.04Suggestive
Sea-blue histiocytosisOpen Targets
0.04Suggestive
idiopathic hypereosinophilic syndromeOpen Targets
0.04Suggestive
combined immunodeficiency due to ZAP70 deficiencyOpen Targets
0.04Suggestive
immunodeficiency, common variable, 1Open Targets
0.03Suggestive
immunodeficiency 78 with autoimmunity and developmental delayOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
PLA2G12AProtein interaction96%LYPLA1Protein interaction93%LCATProtein interaction91%GPCPD1Protein interaction90%PLA2G6Protein interaction86%PLA2G2FProtein interaction85%
Tissue Expression6 tissues
Heart
100%
Lung
53%
Liver
43%
Ovary
23%
Brain
17%
Bone Marrow
16%
Gene Interaction Network
Click a node to explore
PLA2G15PLA2G12ALYPLA1LCATGPCPD1PLA2G6PLA2G2F
PROTEIN STRUCTURE
Preparing viewer…
PDB4X90 · 1.84 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.77LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.52 [0.36–0.77]
RankingsWhere PLA2G15 stands among ~20K protein-coding genes
  • #10,053of 20,598
    Most Researched41
  • #6,187of 17,882
    Most Constrained (LOEUF)0.77
Genes detectedPLA2G15
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Glycerophosphodiesters inhibit lysosomal phospholipid catabolism in Batten disease.
PMID: 38447580
Mol Cell · 2024
1.00
2
Inhibition of lysosomal phospholipase A2 predicts drug-induced phospholipidosis.
PMID: 34087196
J Lipid Res · 2021
0.90
3
Lysosomal phospholipase A2.
PMID: 30077006
Biochim Biophys Acta Mol Cell Biol Lipids · 2019
0.80
4
Lysosomal damage due to cholesterol accumulation triggers immunogenic cell death.
PMID: 39663580
Autophagy · 2025
0.70
5
Hepatic lipid remodeling in cold exposure uncovers direct regulation of bis(monoacylglycero)phosphate lipids by phospholipase A2 group XV.
PMID: 40373767
Cell Metab · 2025
0.60