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50 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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PPIA
peptidylprolyl isomerase A
Chromosome 7 · 7p13
NCBI Gene: 5478Ensembl: ENSG00000196262.16HGNC: HGNC:9253UniProt: P62937
647PubMed Papers
20Diseases
3Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Apoptosis
RESEARCH IMPACT
Highly StudiedTrending
CLINICAL
FDA Approved Target
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
nucleuspeptidyl-prolyl cis-trans isomerase activitynegative regulation of viral life cycleregulation of apoptotic signaling pathwayHIV infectionpsoriasisgraft versus host diseasekeratitis
✦AI Summary

PPIA (peptidylprolyl isomerase A) is a peptidyl-prolyl cis-trans isomerase that functions as a protein folding chaperone and plays critical roles in cancer progression and cellular stress responses. The protein stabilizes key oncogenic factors, particularly NRF2, by physically binding to prevent ubiquitin-mediated degradation, thereby promoting lung cancer progression 1. PPIA acts through direct protein-protein interactions, with structural studies revealing it binds to a trans-proline 174-harboring hydrophobic sequence in target proteins 1. In breast cancer, NQO1 stabilizes PPIA by preventing oxidation at cysteine residue C161, leading to CD147 activation and subsequent neutrophil recruitment and NET formation that drives lung metastasis 2. PPIA also functions as a secreted factor that modulates immune responses and can serve as a receptor for microbial adhesin proteins 2. The protein has emerged as a therapeutic target, with FDA-approved cyclosporin A effectively disrupting PPIA-NRF2 interactions and suppressing NRF2-hyperactivated cancer cell growth 1. Additionally, PPIA inhibition sensitizes multiple myeloma cells to proteasome inhibitors and reduces SARS-CoV-2 replication when pharmacologically targeted 34. Multiple studies identify PPIA as a potential biomarker for hepatocellular carcinoma diagnosis 5.

Sources cited
1
PPIA stabilizes NRF2 protein by preventing ubiquitin-mediated degradation and can be targeted by cyclosporin A
PMID: 38830868
2
NQO1 stabilizes PPIA by preventing oxidation at C161, and PPIA activates CD147 leading to neutrophil recruitment and NET formation in breast cancer metastasis
PMID: 39073320
3
PPIA is identified as a therapeutic target in resistant multiple myeloma and CRISPR deletion or ciclosporin inhibition sensitizes cells to proteasome inhibitors
PMID: 33619369
4
Pharmacological inhibition of PPIA reduces SARS-CoV-2 replication in human cell lines
PMID: 33349665
5
PPIA is identified as a potential diagnostic biomarker for hepatocellular carcinoma through machine learning analysis
PMID: 40169794
Disease Associationsⓘ20
HIV infectionOpen Targets
0.62Moderate
psoriasisOpen Targets
0.57Moderate
graft versus host diseaseOpen Targets
0.51Moderate
keratitisOpen Targets
0.49Moderate
eye diseaseOpen Targets
0.47Moderate
inflammationOpen Targets
0.47Moderate
keratoconjunctivitisOpen Targets
0.46Moderate
dry eye syndromeOpen Targets
0.41Moderate
kidney transplantOpen Targets
0.40Moderate
leukemiaOpen Targets
0.39Weak
hepatitis C virus infectionOpen Targets
0.39Weak
severe acute respiratory syndromeOpen Targets
0.39Weak
rheumatoid arthritisOpen Targets
0.39Weak
Keratoconjunctivitis siccaOpen Targets
0.38Weak
neurodegenerative diseaseOpen Targets
0.37Weak
immune system diseaseOpen Targets
0.37Weak
conjunctivitisOpen Targets
0.37Weak
corneal diseaseOpen Targets
0.37Weak
psoriasis vulgarisOpen Targets
0.37Weak
allergic conjunctivitisOpen Targets
0.37Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets3
ALISPORIVIRPhase III
Cyclophilin A inhibitor
CYCLOSPORINEApproved
Cyclophilin A modulator
SCY 635Phase II
Cyclophilin A inhibitor
hepatitis C virus infection
Related Genes
BSGProtein interaction100%ACTBProtein interaction100%PPP3CAProtein interaction100%RPL13AProtein interaction100%FKBP1AProtein interaction100%PPP3R1Protein interaction99%
Tissue Expression6 tissues
Brain
100%
Liver
87%
Bone Marrow
80%
Lung
79%
Ovary
52%
Heart
35%
Gene Interaction Network
Click a node to explore
PPIABSGACTBPPP3CARPL13AFKBP1APPP3R1
PROTEIN STRUCTURE
Preparing viewer…
PDB9BG4 · 1.14 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.43Moderately Constrained
pLIⓘ
0.98Intolerant
Observed/Expected LoF0.14 [0.06–0.43]
RankingsWhere PPIA stands among ~20K protein-coding genes
  • #347of 20,598
    Most Researched647 · top 5%
  • #733of 1,025
    FDA-Approved Drug Targets1
  • #2,300of 17,882
    Most Constrained (LOEUF)0.43 · top quartile
Genes detectedPPIA
Sources retrieved50 papers
Response time—
📄 Sources
50▼
1
PPIA dictates NRF2 stability to promote lung cancer progression.
PMID: 38830868
Nat Commun · 2024
1.00
2
Autophagy deficiency abolishes liver mitochondrial DNA segregation.
PMID: 35220898
Autophagy · 2022
0.90
3
Peptidylprolyl isomerase A guides SENP5/GAU1 DNA-lncRNA triplex generation for driving tumorigenesis.
PMID: 39433793
Nat Commun · 2024
0.82
4
Identification of resistance pathways and therapeutic targets in relapsed multiple myeloma patients through single-cell sequencing.
PMID: 33619369
Nat Med · 2021
0.80
5
PMID: 34584568
Oncol Lett · 2021
0.80