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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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RANBP10
RAN binding protein 10
Chromosome 16 · 16q22.1
NCBI Gene: 57610Ensembl: ENSG00000141084.12HGNC: HGNC:29285UniProt: B3KP49
61PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingubiquitin ligase complexguanyl-nucleotide exchange factor activityprotein-macromolecule adaptor activitymarfanoid habitus and intellectual disabilitytooth diseaseRare hemorrhagic disorder due to a constitutional platelet anomalyglioblastoma multiforme
✦AI Summary

RANBP10 is a multifunctional adapter protein with roles in transcriptional regulation, protein degradation, and cellular proliferation. As a core component of the CTLH E3 ubiquitin-protein ligase complex, RANBP10 mediates ubiquitination and proteasomal degradation of target proteins including the transcription factor HBP1 1. It acts as a guanine nucleotide exchange factor (GEF) for RAN GTPase and functions as a transcriptional coactivator, enhancing androgen receptor (AR) and glucocorticoid receptor (NR3C1) transactivation 2. RanBP10 plays important roles in disease pathogenesis. In non-small cell lung cancer, RANBP10 and its paralog RANBP9 function as partial antagonists regulating CTLH complex output; higher RANBP9/RANBP10 ratios correlate with increased proliferation, while elevated RANBP10 slows cell proliferation 3. In glioblastoma, RANBP10 overexpression promotes progression by suppressing the FBXW7 promoter, stabilizing c-Myc 4. In Huntington's disease, elevated RANBP10 expression impairs neuronal morphology and cytoskeletal dynamics; miR-196a-mediated RANBP10 suppression enhances β-tubulin polymerization and provides neuroprotection 5. RANBP10 may also contribute to DNA damage responses 6 and participates in cell cycle progression through interactions with YPEL5 7. During erythropoiesis, stage-dependent RANBP10-CTLH-UBE2H modules regulate differentiation and enucleation 8.

Sources cited
1
RANBP10 is a core component of the CTLH E3 ubiquitin-protein ligase complex that mediates ubiquitination and proteasomal degradation of HBP1
PMID: 29911972
2
RANBP10 enhances androgen receptor and glucocorticoid receptor (NR3C1) transactivation activity but not estrogen receptor
PMID: 18222118
3
RANBP9 and RANBP10 cooperate as partial antagonists in NSCLC; higher RANBP9/RANBP10 ratios associate with greater proliferation while elevated RANBP10 decreases proliferation
PMID: 40883813
4
RANBP10 overexpression promotes glioblastoma progression by suppressing FBXW7 promoter activity and stabilizing c-Myc protein
PMID: 34671019
5
RANBP10 impairs neuronal morphology and β-tubulin polymerization; miR-196a-mediated RANBP10 suppression provides neuroprotection in Huntington's disease
PMID: 28744327
6
RANBP10 (Scorpin) contains sites for PIK-kinase phosphorylation and is phosphorylated following genotoxic stress, suggesting involvement in DNA damage response
PMID: 29914204
7
RANBP10 interacts with YPEL5 protein and is involved in cell cycle progression
PMID: 20580816
8
Dynamic stage-dependent RANBP10-CTLH-UBE2H E2-E3 modules regulate erythroid maturation and enucleation
PMID: 36459484
Disease Associationsⓘ20
marfanoid habitus and intellectual disabilityOpen Targets
0.12Weak
tooth diseaseOpen Targets
0.10Suggestive
Rare hemorrhagic disorder due to a constitutional platelet anomalyOpen Targets
0.07Suggestive
glioblastoma multiformeOpen Targets
0.07Suggestive
Beta-thalassemia - X-linked thrombocytopeniaOpen Targets
0.07Suggestive
beta-thalassemia-X-linked thrombocytopenia syndromeOpen Targets
0.07Suggestive
autosomal dominant macrothrombocytopeniaOpen Targets
0.07Suggestive
Glanzmann thrombasthenia 1Open Targets
0.07Suggestive
thrombocytopenia 7Open Targets
0.07Suggestive
Von Willebrand diseaseOpen Targets
0.07Suggestive
Bernard-Soulier syndromeOpen Targets
0.06Suggestive
bleeding disorder, platelet-type, 24Open Targets
0.06Suggestive
non-small cell lung carcinomaOpen Targets
0.06Suggestive
macrothrombocytopenia and granulocyte inclusions with or without nephritis or sensorineural hearing lossOpen Targets
0.06Suggestive
thrombocytopenia 9Open Targets
0.06Suggestive
MYH9-related diseaseOpen Targets
0.06Suggestive
platelet-type bleeding disorder 10Open Targets
0.06Suggestive
ThrombocytopeniaOpen Targets
0.06Suggestive
platelet-type bleeding disorder 15Open Targets
0.06Suggestive
bleeding disorder, platelet-type, 25Open Targets
0.06Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
GANShared pathway100%MKLN1Protein interaction100%MAEAProtein interaction100%ARMC8Protein interaction100%GID8Protein interaction100%RMND5AProtein interaction100%
Tissue Expression6 tissues
Bone Marrow
100%
Liver
96%
Ovary
50%
Lung
41%
Heart
38%
Brain
15%
Gene Interaction Network
Click a node to explore
RANBP10GANMKLN1MAEAARMC8GID8RMND5A
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q6VN20
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
0.48Moderately Constrained
pLIⓘ
0.99Intolerant
Observed/Expected LoF0.34 [0.25–0.48]
RankingsWhere RANBP10 stands among ~20K protein-coding genes
  • #7,601of 20,598
    Most Researched61
  • #2,832of 17,882
    Most Constrained (LOEUF)0.48 · top quartile
Genes detectedRANBP10
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Scorpins in the DNA Damage Response.
PMID: 29914204
Int J Mol Sci · 2018
1.00
2
RANBP9 and RANBP10 cooperate in regulating non-small cell lung cancer proliferation.
PMID: 40883813
J Exp Clin Cancer Res · 2025
0.90
3
Cellular Transcriptional Coactivator RanBP10 and Herpes Simplex Virus 1 ICP0 Interact and Synergistically Promote Viral Gene Expression and Replication.
PMID: 26739050
J Virol · 2016
0.80
4
YPEL5 protein of the YPEL gene family is involved in the cell cycle progression by interacting with two distinct proteins RanBPM and RanBP10.
PMID: 20580816
Genomics · 2010
0.70
5
RANBP10 promotes glioblastoma progression by regulating the FBXW7/c-Myc pathway.
PMID: 34671019
Cell Death Dis · 2021
0.60