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25 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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SENP3
SUMO specific peptidase 3
Chromosome 17 · 17p13.1
NCBI Gene: 26168Ensembl: ENSG00000161956.15HGNC: HGNC:17862UniProt: Q9H4L4
181PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Highly ConstrainedProtease
RESEARCH IMPACT
Trending
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
nucleoplasmcysteine-type peptidase activityMLL1 complexdeSUMOylase activityneurodegenerative diseaseatrial fibrillationmyoepithelial tumorneoplasm
✦AI Summary

SENP3 (SUMO specific peptidase 3) is a redox-sensitive desumoylase that specifically cleaves SUMO2 and SUMO3 conjugates from target proteins, with minimal activity against SUMO1 1. The enzyme functions as a critical regulator of cellular stress responses and immune functions through substrate-specific desumoylation. SENP3 enhances transcriptional activity by desumoylating proteins like MEF2D and EP300, and regulates ribosomal RNA processing through NPM1 desumoylation 1. In immune cells, SENP3 serves dual roles: it promotes antitumor immunity in dendritic cells by facilitating STING signaling through IFI204 desumoylation 2, while simultaneously regulating macrophage polarization and ferroptosis sensitivity through FSP1 desumoylation 3. Disease relevance includes significant upregulation in hepatocellular carcinoma, where SENP3 promotes oncogene translation via RACK1 desumoylation and facilitates immune evasion 4. The enzyme also contributes to abdominal aortic aneurysm development by destabilizing CTH through desumoylation, leading to enhanced ferroptosis 5. Clinically, elevated SENP3 expression correlates with poor prognosis in various cancers, making it an attractive therapeutic target for combination immunotherapies 41.

Sources cited
1
SENP3 is a redox-sensitive desumoylase specific for SUMO2/3 conjugates and regulates transcriptional activity
PMID: 33192553
2
SENP3 promotes antitumor immunity in dendritic cells through STING signaling via IFI204 desumoylation
PMID: 33434504
3
SENP3 regulates macrophage ferroptosis sensitivity through FSP1 desumoylation
PMID: 39025016
4
SENP3 is upregulated in hepatocellular carcinoma and promotes oncogene translation via RACK1 desumoylation
PMID: 39755756
5
SENP3 contributes to abdominal aortic aneurysm development through CTH desumoylation and ferroptosis regulation
PMID: 40019399
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.37Weak
atrial fibrillationOpen Targets
0.13Weak
myoepithelial tumorOpen Targets
0.11Weak
neoplasmOpen Targets
0.11Weak
hepatocellular carcinomaOpen Targets
0.11Weak
triple-negative breast cancerOpen Targets
0.10Suggestive
type 2 diabetes mellitusOpen Targets
0.09Suggestive
gastric cancerOpen Targets
0.08Suggestive
breast cancerOpen Targets
0.08Suggestive
obesityOpen Targets
0.08Suggestive
oral squamous cell carcinomaOpen Targets
0.08Suggestive
non-alcoholic fatty liver diseaseOpen Targets
0.08Suggestive
achalasia-alacrima syndromeOpen Targets
0.08Suggestive
posterior cortical atrophyOpen Targets
0.07Suggestive
esophageal squamous cell carcinomaOpen Targets
0.07Suggestive
urinary bladder carcinomaOpen Targets
0.07Suggestive
acute kidney injuryOpen Targets
0.06Suggestive
atherosclerosisOpen Targets
0.06Suggestive
acute lymphoblastic leukemiaOpen Targets
0.05Suggestive
Ischemic strokeOpen Targets
0.05Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
UBE2IProtein interaction100%SENP8Protein interaction100%CUL1Protein interaction100%DPY30Protein interaction100%ASH2LProtein interaction100%WDR18Protein interaction100%
Tissue Expression6 tissues
Brain
100%
Lung
89%
Ovary
76%
Heart
64%
Liver
61%
Bone Marrow
59%
Gene Interaction Network
Click a node to explore
SENP3UBE2ISENP8CUL1DPY30ASH2LWDR18
PROTEIN STRUCTURE
Preparing viewer…
PDB9ME8 · 2.93 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.28Highly Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.17 [0.10–0.28]
RankingsWhere SENP3 stands among ~20K protein-coding genes
  • #2,406of 20,598
    Most Researched181 · top quartile
  • #1,002of 17,882
    Most Constrained (LOEUF)0.28 · top 10%
Genes detectedSENP3
Sources retrieved25 papers
Response time—
📄 Sources
25▼
1
METTL16-SENP3-LTF axis confers ferroptosis resistance and facilitates tumorigenesis in hepatocellular carcinoma.
PMID: 39218945
J Hematol Oncol · 2024
1.00
2
SENP3 sensitizes macrophages to ferroptosis via de-SUMOylation of FSP1.
PMID: 39025016
Redox Biol · 2024
0.90
3
SENP3 loss promotes M2 macrophage polarization and breast cancer progression.
PMID: 33932085
Mol Oncol · 2022
0.80
4
SENP3: Cancers and diseases.
PMID: 39765284
Biochim Biophys Acta Rev Cancer · 2025
0.70
5
Brucella effectors NyxA and NyxB target SENP3 to modulate the subcellular localisation of nucleolar proteins.
PMID: 36609656
Nat Commun · 2023
0.68