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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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SENP5
SUMO specific peptidase 5
Chromosome 3 · 3q29
NCBI Gene: 205564Ensembl: ENSG00000119231.12HGNC: HGNC:28407UniProt: B2R9F5
34PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Protease
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingSUMO-specific endopeptidase activityprotein desumoylationdeSUMOylase activityAbruptio Placentaeneurodegenerative diseaseresponse to xenobiotic stimulusneoplasm
✦AI Summary

SENP5 is a SUMO-specific peptidase that catalyzes two essential functions in the SUMOylation pathway: processing full-length SUMO3 to its mature form and deconjugating SUMO2/3 from target proteins 1. Structurally, SENP5 shows preferential specificity for SUMO2/3 over SUMO1 due to favorable interactions between Arg624 and Asp63 in SUMO2/3 1. SENP5 functions as a nucleolar protein involved in ribosome biogenesis, where its inactivation disturbs 40S and 60S ribosomal subunit assembly and triggers both p53-dependent and p53-independent cell cycle checkpoints through CDK6 downregulation 2. The enzyme plays critical roles in cancer progression through multiple mechanisms: promoting homologous recombination-mediated DNA repair via H2AZ deSUMOylation in colorectal cancer 3, driving breast cancer progression through CDK1 deSUMOylation 4, and enhancing endometrial cancer cell growth by regulating β-catenin deSUMOylation to promote ferroptosis resistance 5. SENP5 also participates in mitochondrial dynamics by counteracting SUMO1 modification of Drp1, thereby regulating mitochondrial fission in various pathological conditions 67. Clinically, elevated SENP5 expression correlates with radiotherapy resistance and poor prognosis in multiple cancer types, suggesting its potential as both a prognostic marker and therapeutic target 345.

Sources cited
1
SENP5 catalyzes SUMO processing and deconjugation with specificity for SUMO2/3 over SUMO1
PMID: 40404649
2
SENP5 is involved in ribosome biogenesis and triggers p53-independent cell cycle checkpoints
PMID: 38065954
3
SENP5 promotes DNA repair through H2AZ deSUMOylation and confers radiotherapy resistance
PMID: 37684630
4
SENP5 drives breast cancer progression through CDK1 deSUMOylation
PMID: 40474290
5
SENP5 enhances endometrial cancer growth via β-catenin deSUMOylation and ferroptosis resistance
PMID: 40410883
6
SENP5 regulates mitochondrial dynamics through Drp1 SUMOylation balance
PMID: 38615367
7
SENP5 counteracts MAPL-mediated Drp1 SUMOylation in mitochondrial fission regulation
PMID: 40796734
Disease Associationsⓘ20
Abruptio PlacentaeOpen Targets
0.27Weak
neurodegenerative diseaseOpen Targets
0.26Weak
response to xenobiotic stimulusOpen Targets
0.26Weak
neoplasmOpen Targets
0.10Suggestive
osteosarcomaOpen Targets
0.08Suggestive
breast cancerOpen Targets
0.06Suggestive
gastric cancerOpen Targets
0.06Suggestive
posterior cortical atrophyOpen Targets
0.05Suggestive
stomach neoplasmOpen Targets
0.05Suggestive
Zinc deficiencyOpen Targets
0.04Suggestive
hepatocellular carcinomaOpen Targets
0.04Suggestive
colorectal carcinomaOpen Targets
0.03Suggestive
oral squamous cell carcinomaOpen Targets
0.03Suggestive
esophageal squamous cell carcinomaOpen Targets
0.03Suggestive
cancerOpen Targets
0.03Suggestive
acute myeloid leukemiaOpen Targets
0.02Suggestive
head and neck squamous cell carcinomaOpen Targets
0.02Suggestive
colorectal cancerOpen Targets
0.02Suggestive
cardiomyopathyOpen Targets
0.01Suggestive
acute lung injuryOpen Targets
0.01Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
SENP6Shared pathway100%UBE2IProtein interaction100%RANGAP1Protein interaction92%GNL2Protein interaction90%SUMO4Protein interaction88%NPM1Protein interaction87%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
55%
Brain
54%
Lung
54%
Liver
47%
Heart
46%
Gene Interaction Network
Click a node to explore
SENP5SENP6UBE2IRANGAP1GNL2SUMO4NPM1
PROTEIN STRUCTURE
Preparing viewer…
PDB9GNX · 1.90 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.46Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.30 [0.20–0.46]
RankingsWhere SENP5 stands among ~20K protein-coding genes
  • #11,233of 20,598
    Most Researched34
  • #2,579of 17,882
    Most Constrained (LOEUF)0.46 · top quartile
Genes detectedSENP5
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
SENP5 promotes homologous recombination-mediated DNA damage repair in colorectal cancer cells through H2AZ deSUMOylation.
PMID: 37684630
J Exp Clin Cancer Res · 2023
1.00
2
Astragaloside IV combined with ligustrazine ameliorates abnormal mitochondrial dynamics via Drp1 SUMO/deSUMOylation in cerebral ischemia-reperfusion injury.
PMID: 38615367
CNS Neurosci Ther · 2024
0.90
3
Peptidylprolyl isomerase A guides SENP5/GAU1 DNA-lncRNA triplex generation for driving tumorigenesis.
PMID: 39433793
Nat Commun · 2024
0.80
4
SENP5 drives breast cancer progression through deSUMOYlation of CDK1.
PMID: 40474290
Breast Cancer Res · 2025
0.70
5
Structural basis for the human SENP5's SUMO isoform discrimination.
PMID: 40404649
Nat Commun · 2025
0.60