HomeAboutRankingsData Sources
Β© 2026 GeneE
🧬
GeneE
10 sources retrieved Β· Most recent: April 2026 Β· Index updated 14 days ago
β“˜GeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
SLC25A10
solute carrier family 25 member 10
Chromosome 17 Β· 17q25.3
NCBI Gene: 1468Ensembl: ENSG00000183048.12HGNC: HGNC:10980UniProt: A0A0S2Z382
143PubMed Papers
21Diseases
0Drugs
3Pathogenic Variants
FUNCTIONAL ROLE
Transporter
CLINICAL
OMIM Disease Gene
DATA QUALITY
βœ“ Experimental GO Evidenceβœ“ Swiss-Prot Reviewed
mitochondrionnucleusdicarboxylic acid transmembrane transporter activityprotein bindingneurodegenerative diseasemitochondrial DNA depletion syndrome 19mitochondrial complex I deficiencyneoplasm
✦AI Summary

SLC25A10 is a mitochondrial inner membrane transporter that catalyzes electroneutral exchange of dicarboxylates (malate, succinate, malonate), phosphate, and inorganic sulfur-containing anions 1. The protein functions as a monomer using a ping-pong kinetic mechanism, where substrates bind and dissociate consecutively at a single binding site rather than simultaneously 1. SLC25A10 plays critical roles in gluconeogenesis, fatty acid metabolism, urea synthesis, and sulfur metabolism, particularly in hepatic tissues, and regulates adipocyte fatty acid release and systemic insulin sensitivity. In cancer pathophysiology, SLC25A10 is significantly upregulated in colorectal, cervical, and osteosarcoma tissues and correlates with poor prognosis 234. SLC25A10 contributes to oncogenic progression through multiple mechanisms: (1) facilitating succinate export to activate the succinate/SUCNR1 axis on macrophages, promoting M2 polarization of tumor-associated macrophages 2; (2) transporting glutathione into mitochondria to activate the mtGSH/GPX4 axis, suppressing ferroptosis-mediated cell death 35; and (3) promoting mitochondrial function necessary for tumor cell proliferation and migration 6. Protein stability of SLC25A10 is regulated by ubiquitination: STUB1-mediated ubiquitination negatively regulates SLC25A10 6, while INHBA acts as a scaffold protein to inhibit TRIM21-mediated degradation 2. Low SLC25A10 expression associates with poor ovarian cancer survival and chemotherapy resistance 7. These findings establish SLC25A10 as a therapeutic target for cancer treatment.

Sources cited
1
SLC25A10 functions as a monomer with ping-pong kinetic mechanism; catalyzes electroneutral exchange of dicarboxylates and other metabolites
PMID: 38937634
2
SLC25A10 upregulation in colorectal cancer promotes succinate/SUCNR1 axis activation and M2 macrophage polarization; protein stabilized by INHBA inhibiting TRIM21-mediated degradation
PMID: 41449244
3
SLC25A10 promotes cervical cancer growth and cisplatin resistance by transporting glutathione and activating GPX4, suppressing ferroptosis
PMID: 41057306
4
SLC25A10 upregulated in osteosarcoma; STUB1-mediated ubiquitination at K254 negatively regulates SLC25A10 protein stability and tumor progression
PMID: 40349811
5
SLC25A10 elevated in osteosarcoma; high expression correlates with poor prognosis, metastasis, and survival rates; regulates CCNE1, P21, P27
PMID: 32774476
6
SLC25A10 overexpression prevents 5-FU-induced ferroptosis and apoptosis in colorectal cancer; interacts with PYCR1
PMID: 36104652
7
Low SLC25A10 expression in ovarian cancer associates with poor survival and chemotherapy resistance
PMID: 36114504
8
SLC25A10 is a mitochondrial dicarboxylate carrier involved in redox homeostasis and fatty acid synthesis; upregulated in cancer to support tumor metabolism and growth
PMID: 41102706
Disease Associationsβ“˜21
neurodegenerative diseaseOpen Targets
0.50Moderate
mitochondrial DNA depletion syndrome 19Open Targets
0.41Moderate
mitochondrial complex I deficiencyOpen Targets
0.27Weak
neoplasmOpen Targets
0.08Suggestive
hepatocellular carcinomaOpen Targets
0.08Suggestive
osteosarcomaOpen Targets
0.08Suggestive
colorectal carcinomaOpen Targets
0.07Suggestive
posterior cortical atrophyOpen Targets
0.07Suggestive
Familial exudative vitreoretinopathyOpen Targets
0.05Suggestive
X-linked retinal dysplasiaOpen Targets
0.05Suggestive
ovarian cancerOpen Targets
0.04Suggestive
exudative vitreoretinopathy 2, X-linkedOpen Targets
0.03Suggestive
exudative vitreoretinopathyOpen Targets
0.03Suggestive
cancerOpen Targets
0.03Suggestive
cataractOpen Targets
0.02Suggestive
prostate cancerOpen Targets
0.01Suggestive
Crohn's diseaseOpen Targets
0.01Suggestive
Alzheimer diseaseOpen Targets
0.01Suggestive
colorectal cancerOpen Targets
0.01Suggestive
type 2 diabetes mellitusOpen Targets
0.01Suggestive
Mitochondrial DNA depletion syndrome 19UniProt
Pathogenic Variants3
NM_012140.5(SLC25A10):c.304A>T (p.Lys102Ter)Likely pathogenic
Mitochondrial complex I deficiency|Mitochondrial DNA depletion syndrome 19
β˜…β˜…β˜†β˜†2021β†’ Residue 102
NM_012140.5(SLC25A10):c.329-2A>TLikely pathogenic
Mitochondrial DNA depletion syndrome 19
β˜…β˜†β˜†β˜†2023
NM_012140.5(SLC25A10):c.762+1G>ALikely pathogenic
See cases
β˜…β˜†β˜†β˜†2022
View on ClinVar β†—
Related Genes
MTCH1Protein interaction88%MTCH2Protein interaction81%SLC37A4Shared pathway29%SLC13A5Shared pathway25%SLC13A2Shared pathway25%SLC13A3Shared pathway22%
Tissue Expression6 tissues
Liver
100%
Bone Marrow
9%
Brain
6%
Heart
4%
Ovary
3%
Lung
2%
Gene Interaction Network
Click a node to explore
SLC25A10MTCH1MTCH2SLC37A4SLC13A5SLC13A2SLC13A3
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted Β· UniProt Q9UBX3
View on AlphaFold β†—
Constraintβ“˜
LOEUFβ“˜
1.18LoF Tolerant
pLIβ“˜
0.00Tolerant
Observed/Expected LoF0.88 [0.66–1.18]
RankingsWhere SLC25A10 stands among ~20K protein-coding genes
  • #3,207of 20,598
    Most Researched143 Β· top quartile
  • #3,959of 5,498
    Most Pathogenic Variants3
  • #12,367of 17,882
    Most Constrained (LOEUF)1.18
Genes detectedSLC25A10
Sources retrieved10 papers
Response timeβ€”
πŸ“„ Sources
10β–Ό
1
Inhibin beta A drives colorectal cancer progression through macrophage M2 polarization and mitochondria-dependent ferroptosis suppression.
PMID: 41449244
Signal Transduct Target Ther Β· 2025
1.00
2
STUB1-mediated ubiquitination of SLC25A10 regulates mitochondrial function and drives osteosarcoma progression: A novel therapeutic target.
PMID: 40349811
Cell Signal Β· 2025
0.90
3
Identification and validation of a gene-based signature reveals SLC25A10 as a novel prognostic indicator for patients with ovarian cancer.
PMID: 36114504
J Ovarian Res Β· 2022
0.80
4
SLC25A10 promotes cisplatin resistance by inhibiting ferroptosis in cervical cancer.
PMID: 41057306
Cell Death Discov Β· 2025
0.70
5
Targeting mitochondrial transporters and metabolic reprogramming for disease treatment.
PMID: 41102706
J Transl Med Β· 2025
0.60