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25 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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TARBP2
TARBP2 subunit of RISC loading complex
Chromosome 12 · 12q13.13
NCBI Gene: 6895Ensembl: ENSG00000139546.12HGNC: HGNC:11569UniProt: Q15633
157PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
pre-miRNA bindingdouble-stranded RNA bindingprotein bindingenzyme bindingneurodegenerative diseasebreast cancerhepatocellular carcinomaneoplasm
✦AI Summary

TARBP2 is a double-stranded RNA-binding protein with multifaceted roles in viral infection, gene expression, and cancer biology. As a component of the RISC-loading complex, TARBP2 functions in miRNA processing by acting as a Dicer cofactor, though it does not affect Dicer stability or overall miRNA abundance 1. In the context of HIV-1 infection, TARBP2 binds viral TAR RNA and stimulates translation of TAR-containing RNAs partly by inhibiting the kinase PKR, reducing phosphorylation of translation initiation factors 2. Additionally, TARBP2 recruits the FTSJ3 methyltransferase to HIV-1 RNA for 2'-O-methylation, enabling viral immune evasion 3. In innate immunity, TARBP2 negatively regulates interferon-β production by targeting MAVS, thereby suppressing antiviral responses 4. In cancer pathology, TARBP2 exhibits context-dependent roles. Frameshift mutations in TARBP2 impair miRNA processing and destabilize DICER1, promoting microsatellite instability in carcinomas 5. Conversely, TARBP2 overexpression promotes tumor angiogenesis and metastasis by destabilizing antiangiogenic factor mRNAs through 3'UTR binding 6. TARBP2 also drives oncogenic dysregulation by recruiting m6A methylation machinery to pre-mRNAs, promoting intron retention and nuclear exosome-mediated degradation 7. Thus, TARBP2 functions as either tumor suppressor or promoter depending on mutational status and expression level.

Sources cited
1
TARBP2 functions as a Dicer cofactor affecting processing of select miRNAs without altering Dicer stability or overall miRNA abundance
PMID: 25437560
2
TARBP2 binds HIV-1 TAR RNA and stimulates translation by inhibiting PKR kinase activity
PMID: 11438532
3
TARBP2 recruits FTSJ3 methyltransferase to HIV-1 RNA for 2'-O-methylation enabling immune evasion
PMID: 30626973
4
TARBP2 negatively regulates interferon-β production and antiviral response by targeting MAVS
PMID: 30390472
5
TARBP2 frameshift mutations impair miRNA processing, destabilize DICER1, and are associated with microsatellite instability in carcinomas
PMID: 19219043
6
TARBP2 promotes tumor angiogenesis and metastasis by destabilizing antiangiogenic factor mRNAs through 3'UTR targeting
PMID: 33484209
7
Nuclear TARBP2 promotes intron retention and nuclear exosome-mediated degradation through m6A methylation machinery recruitment
PMID: 31300274
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.34Weak
breast cancerOpen Targets
0.10Suggestive
hepatocellular carcinomaOpen Targets
0.10Suggestive
neoplasmOpen Targets
0.09Suggestive
adrenal cortex carcinomaOpen Targets
0.09Suggestive
azoospermiaOpen Targets
0.08Suggestive
viral diseaseOpen Targets
0.08Suggestive
diffuse large B-cell lymphomaOpen Targets
0.07Suggestive
partial chromosome Y deletionOpen Targets
0.06Suggestive
osteosarcomaOpen Targets
0.06Suggestive
adenomaOpen Targets
0.06Suggestive
spermatogenic failure 48Open Targets
0.05Suggestive
spermatogenic failure 54Open Targets
0.05Suggestive
spermatogenic failure 25Open Targets
0.05Suggestive
spermatogenic failure, X-linked, 3Open Targets
0.05Suggestive
spermatogenic failure 1Open Targets
0.05Suggestive
spermatogenic failure 84Open Targets
0.05Suggestive
spermatogenic failure 93Open Targets
0.05Suggestive
spermatogenic failure 65Open Targets
0.05Suggestive
carcinomaOpen Targets
0.05Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
DDX6Protein interaction100%DHX9Protein interaction100%EIF4EProtein interaction100%PRORPProtein interaction100%GEMIN4Protein interaction100%TNRC6AProtein interaction100%
Tissue Expression6 tissues
Liver
100%
Lung
66%
Ovary
57%
Bone Marrow
50%
Heart
40%
Brain
20%
Gene Interaction Network
Click a node to explore
TARBP2DDX6DHX9EIF4EPRORPGEMIN4TNRC6A
PROTEIN STRUCTURE
Preparing viewer…
PDB6ZBK · 1.49 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.91LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.64 [0.46–0.91]
RankingsWhere TARBP2 stands among ~20K protein-coding genes
  • #2,875of 20,598
    Most Researched157 · top quartile
  • #8,273of 17,882
    Most Constrained (LOEUF)0.91
Genes detectedTARBP2
Sources retrieved25 papers
Response time—
📄 Sources
25▼
1
The role of TARBP2 in the development and progression of cancers.
PMID: 26486325
Tumour Biol · 2016
1.00
2
Organization of the human tarbp2 gene reveals two promoters that are repressed in an astrocytic cell line.
PMID: 11641396
J Biol Chem · 2001
0.90
3
Deletion of human tarbp2 reveals cellular microRNA targets and cell-cycle function of TRBP.
PMID: 25437560
Cell Rep · 2014
0.80
4
Nuclear TARBP2 Drives Oncogenic Dysregulation of RNA Splicing and Decay.
PMID: 31300274
Mol Cell · 2019
0.70
5
Clinical and functional impact of TARBP2 over-expression in adrenocortical carcinoma.
PMID: 23671264
Endocr Relat Cancer · 2013
0.68