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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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TRIM41
tripartite motif containing 41
Chromosome 5 · 5q35.3
NCBI Gene: 90933Ensembl: ENSG00000146063.21HGNC: HGNC:19013UniProt: Q8WV44
58PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingdefense response to viruspositive regulation of type I interferon-mediated signaling pathwaycellular response to lipopolysaccharideAbnormality of the skeletal systemjoint diseaseazoospermiapartial chromosome Y deletion
✦AI Summary

TRIM41 is an E3 ubiquitin ligase with primary roles in innate antiviral immunity and genome protection. As an intrinsic antiviral restriction factor, TRIM41 directly binds influenza A virus and vesicular stomatitis virus nucleoproteins through its SPRY domain and catalyzes their polyubiquitination, targeting them for proteasomal degradation and limiting viral infection 1. TRIM41 also activates antiviral signaling by monoubiquitinating cGAS, enhancing DNA sensing responses. In genome maintenance, TRIM41 ubiquitinates LINE-1 ORF2p protein; nuclear cGAS enhances this interaction following DNA damage-induced phosphorylation, suppressing L1 retrotransposition and preserving genome integrity 2. TRIM41-mediated cGAS ubiquitination can be weakened by specific amino acid changes, as observed in naked mole-rats, prolonging cGAS chr5 binding and potentiating DNA repair 3. Beyond immune functions, TRIM41 catalyzes degradation of other substrates including GPX4 (regulating ferroptosis) 4, ZSCAN21 (affecting α-synuclein expression in Parkinson's disease pathogenesis) 5, TOP3B (in DNA repair), and p53 (in cancer drug resistance) 6. TRIM41 exists as multiple isoforms localizing to both cytoplasm and nucleus 7, positioning it as a multifunctional regulator linking viral defense, DNA repair, cellular aging, and disease susceptibility.

Sources cited
1
TRIM41 ubiquitinates influenza A virus nucleoprotein and limits IAV infection
PMID: 29899090
2
TRIM41 promotes ORF2p degradation to suppress L1 retrotransposition; cGAS enhances TRIM41-ORF2p association
PMID: 38086852
3
Altered cGAS reduces TRIM41-mediated ubiquitination, prolonging cGAS chromatin binding and enhancing DNA repair
PMID: 41066557
4
TRIM41 is an E3 ubiquitin ligase of GPX4 affecting ferroptosis regulation
PMID: 40305884
5
TRIM41 ubiquitinates ZSCAN21, regulating α-synuclein expression; deregulation linked to Parkinson's disease
PMID: 30485814
6
TRIM41 ubiquitinates TOP3B cleavage complexes in DNA repair pathway
PMID: 33378676
7
circRNA_0067717 acts as scaffold promoting TRIM41-mediated p53 degradation in cancer drug resistance
PMID: 36705889
8
TRIM41 exists as multiple isoforms localizing to cytoplasm and nucleus
PMID: 16022281
Disease Associationsⓘ20
Abnormality of the skeletal systemOpen Targets
0.34Weak
joint diseaseOpen Targets
0.18Weak
azoospermiaOpen Targets
0.10Weak
partial chromosome Y deletionOpen Targets
0.09Suggestive
spermatogenic failure 63Open Targets
0.08Suggestive
spermatogenic failure 65Open Targets
0.08Suggestive
spermatogenic failure 84Open Targets
0.08Suggestive
spermatogenic failure 93Open Targets
0.08Suggestive
spermatogenic failure 25Open Targets
0.08Suggestive
spermatogenic failure 56Open Targets
0.08Suggestive
spermatogenic failure 92Open Targets
0.08Suggestive
spermatogenic failure 94Open Targets
0.08Suggestive
spermatogenic failure, X-linked, 3Open Targets
0.08Suggestive
spermatogenic failure 54Open Targets
0.08Suggestive
spermatogenic failure 40Open Targets
0.08Suggestive
spermatogenic failure 76Open Targets
0.08Suggestive
spermatogenic failure 80Open Targets
0.08Suggestive
spermatogenic failure 58Open Targets
0.08Suggestive
spermatogenic failure 39Open Targets
0.08Suggestive
spermatogenic failure 47Open Targets
0.08Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
TOP3BProtein interaction88%SPG7Protein interaction80%BBOX1Protein interaction78%TRAT1Protein interaction78%TRIM45Protein interaction78%MAVSProtein interaction72%
Tissue Expression6 tissues
Liver
100%
Bone Marrow
67%
Lung
63%
Ovary
60%
Heart
58%
Brain
56%
Gene Interaction Network
Click a node to explore
TRIM41TOP3BSPG7BBOX1TRAT1TRIM45MAVS
PROTEIN STRUCTURE
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PDB2EGM · NMR
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.48Moderately Constrained
pLIⓘ
0.99Intolerant
Observed/Expected LoF0.33 [0.23–0.48]
RankingsWhere TRIM41 stands among ~20K protein-coding genes
  • #7,927of 20,598
    Most Researched58
  • #2,807of 17,882
    Most Constrained (LOEUF)0.48 · top quartile
Genes detectedTRIM41
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
A cGAS-mediated mechanism in naked mole-rats potentiates DNA repair and delays aging.
PMID: 41066557
Science · 2025
1.00
2
Nuclear cGAS restricts L1 retrotransposition by promoting TRIM41-mediated ORF2p ubiquitination and degradation.
PMID: 38086852
Nat Commun · 2023
0.90
3
Noscapine derivative 428 suppresses ferroptosis through targeting GPX4.
PMID: 40305884
Redox Biol · 2025
0.80
4
Intracellular localization and domain organization of human TRIM41 proteins.
PMID: 16022281
Mol Biol Rep · 2005
0.70
5
The E3 Ubiquitin Ligases TRIM17 and TRIM41 Modulate α-Synuclein Expression by Regulating ZSCAN21.
PMID: 30485814
Cell Rep · 2018
0.60