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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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TSPAN15
tetraspanin 15
Chromosome 10 · 10q22.1
NCBI Gene: 23555Ensembl: ENSG00000099282.11HGNC: HGNC:23298UniProt: O95858
36PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
regulation of Notch signaling pathwayprotein bindingenzyme bindingnegative regulation of Notch signaling pathwayvenous thromboembolismdeep vein thrombosispulmonary embolismPhlebitis
✦AI Summary

TSPAN15 is a tetraspanin protein that functions primarily as a critical regulator of ADAM10 trafficking and enzymatic activity. As a member of the TspanC8 subfamily, TSPAN15 interacts with the transmembrane metalloprotease ADAM10 to facilitate its exit from the endoplasmic reticulum and trafficking to the cell surface 1. Structurally, TSPAN15 acts as a molecular measuring stick that positions ADAM10's active site approximately 20 Å from the plasma membrane, enabling membrane-proximal substrate cleavage and influencing substrate selectivity 1. TSPAN15 stabilizes ADAM10 at the cell surface while negatively regulating Notch signaling by modulating ADAM10-mediated proteolysis 2. In disease contexts, TSPAN15 shows elevated expression in multiple malignancies. In pancreatic ductal adenocarcinoma, TSPAN15 promotes chemoresistance by sustaining integrin-β1 stability and suppressing ferroptosis through the FAK/AKT/mTOR-GPX4 cascade 3. In intrahepatic cholangiocarcinoma, TSPAN15-ADAM10-Notch1 signaling enhances cancer stem cell properties and chemoresistance 4. In hepatocellular carcinoma, TSPAN15 promotes autophagy-mediated EMT and metastasis via BTRC-dependent PDCD4 degradation 5. Genetically, TSPAN15 variants associate with venous thromboembolism susceptibility and chr10 thromboembolic pulmonary hypertension 67. Additionally, TSPAN15 supports alphavirus replication in astrocytoma cells 8.

Sources cited
1
TSPAN15 binding relieves ADAM10 autoinhibition and positions the enzyme active site ~20 Å from the plasma membrane for membrane-proximal substrate cleavage
PMID: 37516108
2
TSPAN15 stabilizes ADAM10 at the cell surface and regulates ADAM10 trafficking and substrate selectivity as a TspanC8 member
PMID: 31792032
3
TSPAN15 overexpression in pancreatic ductal adenocarcinoma sustains ITGB1 stability and blocks gemcitabine-induced ferroptosis via FAK/AKT/mTOR-GPX4 signaling
PMID: 40505345
4
TSPAN15-ADAM10 signaling enhances cancer stem cell properties and chemoresistance in intrahepatic cholangiocarcinoma through Notch1 activation
PMID: 37545390
5
TSPAN15 promotes hepatocellular carcinoma metastasis by enhancing autophagy through BTRC-mediated PDCD4 degradation
PMID: 40398082
6
TSPAN15 genetic variants are associated with venous thromboembolism susceptibility (OR 1.31, p=1.67×10⁻¹⁶)
PMID: 25772935
7
TSPAN15 locus shows genetic association with chronic thromboembolic pulmonary hypertension
PMID: 38470220
8
TSPAN15 supports Venezuelan equine encephalitis virus replication in astrocytoma cells independently of viral entry
PMID: 39878649
Disease Associationsⓘ20
venous thromboembolismOpen Targets
0.52Moderate
deep vein thrombosisOpen Targets
0.50Moderate
pulmonary embolismOpen Targets
0.49Moderate
PhlebitisOpen Targets
0.49Moderate
ThrombophlebitisOpen Targets
0.48Moderate
heart diseaseOpen Targets
0.46Moderate
ThromboembolismOpen Targets
0.45Moderate
Pulmonary InfarctionOpen Targets
0.40Moderate
cor pulmonaleOpen Targets
0.39Weak
blood coagulation diseaseOpen Targets
0.39Weak
type 2 diabetes mellitusOpen Targets
0.34Weak
insomniaOpen Targets
0.32Weak
lymphatic system diseaseOpen Targets
0.32Weak
lung diseaseOpen Targets
0.32Weak
thrombophiliaOpen Targets
0.32Weak
vein disorderOpen Targets
0.31Weak
jaw diseaseOpen Targets
0.31Weak
Abnormal thrombosisOpen Targets
0.31Weak
self-injurious ideationOpen Targets
0.28Weak
ovarian neoplasmOpen Targets
0.27Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
ADAM10Protein interaction95%CD9Protein interaction88%TSPAN14Protein interaction76%TSPAN5Protein interaction75%PTGFRNProtein interaction71%PRPH2Shared pathway40%
Tissue Expression6 tissues
Lung
100%
Brain
93%
Heart
69%
Liver
20%
Bone Marrow
14%
Ovary
9%
Gene Interaction Network
Click a node to explore
TSPAN15ADAM10CD9TSPAN14TSPAN5PTGFRNPRPH2
PROTEIN STRUCTURE
Preparing viewer…
PDB7RDB · 2.52 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.91LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.60 [0.41–0.91]
RankingsWhere TSPAN15 stands among ~20K protein-coding genes
  • #10,885of 20,598
    Most Researched36
  • #8,224of 17,882
    Most Constrained (LOEUF)0.91
Genes detectedTSPAN15
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
TSPAN15 sustains ITGB1 stability to block gemcitabine-induced ferroptosis in pancreatic ductal adenocarcinoma through the FAK/AKT/Mtor-gpx4 cascade.
PMID: 40505345
Redox Biol · 2025
1.00
2
Structural basis for membrane-proximal proteolysis of substrates by ADAM10.
PMID: 37516108
Cell · 2023
0.90
3
Shared and Distinct Genomics of Chronic Thromboembolic Pulmonary Hypertension and Pulmonary Embolism.
PMID: 38470220
Am J Respir Crit Care Med · 2024
0.80
4
Meta-analysis of 65,734 individuals identifies TSPAN15 and SLC44A2 as two susceptibility loci for venous thromboembolism.
PMID: 25772935
Am J Hum Genet · 2015
0.70
5
Tspan15-ADAM10 signalling enhances cancer stem cell-like properties and induces chemoresistance via Notch1 activation in ICC.
PMID: 37545390
Liver Int · 2023
0.60