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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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UQCR11
ubiquinol-cytochrome c reductase, complex III subunit XI
Chromosome 19 · 19p13.3
NCBI Gene: 10975Ensembl: ENSG00000127540.13HGNC: HGNC:30862UniProt: O14957
15PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Hub GeneTransporter
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
mitochondrial inner membranemitochondrionmitochondrial electron transport, ubiquinol to cytochrome ccellular respirationendocrine system diseaseIGA glomerulonephritisulcerative colitismyocardial infarction
✦AI Summary

UQCR11 encodes a component of mitochondrial complex III (ubiquinol-cytochrome c oxidoreductase) that participates in the electron transport chain and oxidative phosphorylation 12. The protein functions in electron transfer from ubiquinol to cytochrome c, contributing to ATP synthesis and cellular energy production 3. UQCR11 plays critical roles in cellular protection and metabolic regulation. In traumatic brain injury models, UQCR11 overexpression reduces oxidative stress and neuronal apoptosis, while improving motor function and memory recovery 4. The gene demonstrates neuroprotective effects through promoting neuron survival and inhibiting oxidative damage 4. In cardiovascular contexts, UQCR11 downregulation correlates with reduced cardiac function following myocardial infarction, where it appears to regulate immunometabolism 3. Clinically, UQCR11 deletions occur frequently in ovarian cancer, creating dependency on paralogue pathways that can be therapeutically targeted 1. The gene shows altered expression in various cancers, including lung adenocarcinoma and brain metastases, suggesting roles in cancer metabolism 25. UQCR11 expression is also regulated during cardiac regeneration and adipocyte differentiation, highlighting its importance in tissue remodeling and metabolic reprogramming 67.

Sources cited
1
UQCR11 is a component of mitochondrial complex III involved in electron transport and is frequently deleted in ovarian cancer
PMID: 36131208
2
UQCR11 is associated with mitochondrial ATP synthesis and oxidative phosphorylation pathways in lung adenocarcinoma
PMID: 26840709
3
UQCR11 overexpression reduces oxidative stress, neuronal apoptosis, and improves motor/memory function after traumatic brain injury
PMID: 37884186
4
UQCR11 downregulation correlates with reduced cardiac function in myocardial infarction and regulates immunometabolism
PMID: 40496861
5
UQCR11 shows altered expression patterns in brain metastases from lung adenocarcinoma
PMID: 39341452
6
UQCR11 expression is regulated during cardiac regeneration
PMID: 38459019
7
UQCR11 functions as a late-stage regulator in adipocyte differentiation and maturation
PMID: 41325391
Disease Associationsⓘ20
endocrine system diseaseOpen Targets
0.05Suggestive
IGA glomerulonephritisOpen Targets
0.03Suggestive
ulcerative colitisOpen Targets
0.02Suggestive
myocardial infarctionOpen Targets
0.01Suggestive
neoplasmOpen Targets
0.01Suggestive
familial hyperaldosteronismOpen Targets
0.01Suggestive
atherosclerosisOpen Targets
0.01Suggestive
breast cancerOpen Targets
0.00Suggestive
heart failureOpen Targets
0.00Suggestive
secondary progressive multiple sclerosisOpen Targets
0.00Suggestive
meningeal tuberculosisOpen Targets
0.00Suggestive
ovarian neoplasmOpen Targets
0.00Suggestive
Alzheimer diseaseOpen Targets
0.00Suggestive
cancerOpen Targets
0.00Suggestive
cardiac hypertrophyOpen Targets
0.00Suggestive
heart diseaseOpen Targets
0.00Suggestive
Huntington diseaseOpen Targets
0.00Suggestive
non-alcoholic fatty liver diseaseOpen Targets
0.00Suggestive
Parkinson diseaseOpen Targets
0.00Suggestive
schizoaffective disorderOpen Targets
0.00Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
BCS1LProtein interaction100%COX4I1Protein interaction100%COX7A2Protein interaction100%COX8AProtein interaction100%COX1Protein interaction100%CYTBProtein interaction100%
Tissue Expression6 tissues
Heart
100%
Liver
93%
Brain
73%
Lung
50%
Ovary
32%
Bone Marrow
12%
Gene Interaction Network
Click a node to explore
UQCR11BCS1LCOX4I1COX7A2COX8ACOX1CYTB
PROTEIN STRUCTURE
Preparing viewer…
PDB9CG3 · 2.96 Å · EM
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.90LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF1.34 [0.81–1.90]
RankingsWhere UQCR11 stands among ~20K protein-coding genes
  • #15,731of 20,598
    Most Researched15
  • #17,257of 17,882
    Most Constrained (LOEUF)1.90
Genes detectedUQCR11
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
N-Acetyltransferase 10 represses Uqcr11 and Uqcrb independently of ac4C modification to promote heart regeneration.
PMID: 38459019
Nat Commun · 2024
1.00
2
Integrated proteomic and glycoproteomic analysis reveals heterogeneity and molecular signatures of brain metastases from lung adenocarcinomas.
PMID: 39341452
Cancer Lett · 2024
0.90
3
Metabolic collateral lethal target identification reveals MTHFD2 paralogue dependency in ovarian cancer.
PMID: 36131208
Nat Metab · 2022
0.80
4
Uqcr11 alleviates oxidative stress and apoptosis after traumatic brain injury.
PMID: 37884186
Exp Neurol · 2023
0.70
5
Gene expression profiling analysis of lung adenocarcinoma.
PMID: 26840709
Braz J Med Biol Res · 2016
0.60