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GeneE
10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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ZYG11B
zyg-11 family member B, cell cycle regulator
Chromosome 1 · 1p32.3
NCBI Gene: 79699Ensembl: ENSG00000162378.14HGNC: HGNC:25820UniProt: B4DK95
44PubMed Papers
20Diseases
0Drugs
1Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
Cul2-RING ubiquitin ligase complexprotein quality control for misfolded or incompletely synthesized proteinspositive regulation of proteasomal ubiquitin-dependent protein catabolic processprotein bindingneurodegenerative diseasecraniofacial microsomiaspondylolisthesiscolorectal carcinoma
✦AI Summary

ZYG11B is a substrate adapter for the CRL2 E3 ubiquitin ligase complex that targets proteins bearing N-terminal degrons for proteasomal degradation 1. The complex preferentially recognizes N-terminal glycine residues, with the first four amino acids of substrates serving as the primary recognition elements, though ZYG11B also accepts N-terminal serine, alanine, and cysteine 2. Structurally, ZYG11B utilizes armadillo repeats forming a deep cavity that accommodates degrons through conserved hydrogen bonds 2. ZYG11B functions in multiple biological contexts. During apoptosis, it mediates clearance of proteolytic fragments generated by caspase cleavage, as N-terminal glycine degrons are enriched at caspase cleavage sites 1. It participates in quality control of N-myristoylation by degrading proteins when myristoylation fails 1. ZYG11B amplifies innate immune responses by enhancing cGAS-DNA binding, oligomerization, and condensation to potentiate antiviral interferon production 3. Additionally, ZYG11B suppresses enterovirus replication by targeting viral VP1 protein for degradation via K33-linked ubiquitination 4. Clinically, ZYG11B demonstrates tumor-suppressive functions in colorectal cancer, with reduced expression correlating with poor prognosis and increased proliferation 5. Its substrate specificity makes it a promising platform for targeted protein degradation therapeutics, including PROTACs and aptamer-based approaches 67.

Sources cited
1
ZYG11B targets N-terminal glycine degrons for proteasomal degradation and participates in apoptosis and N-myristoylation quality control
PMID: 31273098
2
ZYG11B recognizes the first four residues of Gly/N-degrons through armadillo repeats with conserved hydrogen bonds coordinating the α-amino group
PMID: 34214466
3
ZYG11B mediates N-glycine-mediated degradation of NLRP1 N-terminal fragment during enteroviral infection
PMID: 33093214
4
ZYG11B enhances cGAS-DNA binding, oligomerization, and condensation to amplify antiviral immune responses
PMID: 36933219
5
ZYG11B targets enterovirus VP1 structural protein for proteasomal degradation via K33-linked ubiquitination
PMID: 40135890
6
ZYG11B is downregulated in colorectal cancer and functions as a tumor suppressor with prognostic significance
PMID: 39350118
7
ZYG11B can be exploited as an E3 ligase warhead for amino acid-based PROTACs targeting oncogenic proteins
PMID: 39114932
8
ZYG11B serves as an E3 ligase platform for aptamer-based PROTACs enabling targeted protein degradation
PMID: 40082426
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.30Weak
craniofacial microsomiaOpen Targets
0.27Weak
spondylolisthesisOpen Targets
0.16Weak
colorectal carcinomaOpen Targets
0.06Suggestive
chronic obstructive pulmonary diseaseOpen Targets
0.06Suggestive
readingOpen Targets
0.06Suggestive
neoplasmOpen Targets
0.04Suggestive
colorectal cancerOpen Targets
0.04Suggestive
cancerOpen Targets
0.01Suggestive
COVID-19Open Targets
0.01Suggestive
colorectal adenocarcinomaOpen Targets
0.01Suggestive
polyp of colonOpen Targets
0.01Suggestive
retinitisOpen Targets
0.01Suggestive
pancreatic ductal adenocarcinomaOpen Targets
0.00Suggestive
infectionOpen Targets
0.00Suggestive
ataxia telangiectasiaOpen Targets
0.00Suggestive
nasopharyngeal carcinomaOpen Targets
0.00Suggestive
Enterovirus infectious diseaseOpen Targets
0.00Suggestive
non-small cell lung carcinomaOpen Targets
0.00Suggestive
pancreatic carcinomaOpen Targets
0.00Suggestive
Pathogenic Variants1
NM_024646.3(ZYG11B):c.628C>T (p.Arg210Ter)Likely pathogenic
Craniofacial microsomia 1
★☆☆☆2022→ Residue 210
View on ClinVar ↗
Related Genes
ELOCProtein interaction97%KLHDC3Protein interaction95%PRAMEF6Protein interaction94%PRAMEF15Protein interaction93%CUL2Protein interaction92%FEM1BProtein interaction92%
Tissue Expression6 tissues
Brain
100%
Heart
83%
Liver
39%
Ovary
25%
Lung
23%
Bone Marrow
21%
Gene Interaction Network
Click a node to explore
ZYG11BELOCKLHDC3PRAMEF6PRAMEF15CUL2FEM1B
PROTEIN STRUCTURE
Preparing viewer…
PDB7EP1 · 1.85 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.54Moderately Constrained
pLIⓘ
0.66Intermediate
Observed/Expected LoF0.39 [0.29–0.54]
RankingsWhere ZYG11B stands among ~20K protein-coding genes
  • #9,681of 20,598
    Most Researched44
  • #5,136of 5,498
    Most Pathogenic Variants1
  • #3,371of 17,882
    Most Constrained (LOEUF)0.54 · top quartile
Genes detectedZYG11B
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
A glycine-specific N-degron pathway mediates the quality control of protein
PMID: 31273098
Science · 2019
1.00
2
Distinct Amino Acid-Based PROTACs Target Oncogenic Kinases for Degradation in Non-Small Cell Lung Cancer (NSCLC).
PMID: 39114932
J Med Chem · 2024
0.90
3
Molecular basis for recognition of Gly/N-degrons by CRL2
PMID: 34214466
Mol Cell · 2021
0.80
4
Enteroviral 3C protease activates the human NLRP1 inflammasome in airway epithelia.
PMID: 33093214
Science · 2020
0.70
5
ZYG11B suppresses multiple enteroviruses by triggering viral VP1 degradation.
PMID: 40135890
J Virol · 2025
0.60