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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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ANXA13
annexin A13
Chromosome 8 · 8q24.13
NCBI Gene: 312Ensembl: ENSG00000104537.18HGNC: HGNC:536UniProt: P27216
28PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
phosphatidylserine bindingcalcium ion bindingcalcium-dependent phospholipid bindingphosphatidylglycerol bindingOtitis mediabreast carcinomaeustachian tube diseaseprostate carcinoma
✦AI Summary

ANXA13 is a calcium-dependent phospholipid-binding protein that functions in membrane organization and cellular signaling. Mechanistically, ANXA13 binds anionic membranes (phosphatidylserine, phosphatidylglycerol) in a calcium-dependent manner, requiring approximately 320 μM calcium for half-maximal binding [UniProt], and induces membrane curvature through fragmented rolling of negatively charged membranes 1. ANXA13 serves dual, context-dependent roles in disease: it is renoprotective in acute kidney injury (AKI) by directly binding TGF-β receptor type 1 and inhibiting Smad3 signaling-mediated tubular cell death 2, whereas it promotes tumorigenesis in multiple cancers. ANXA13 is upregulated in clear cell renal cell carcinoma, lung adenocarcinoma, and colorectal cancer, where it enhances cell proliferation, invasion, and migration while suppressing apoptosis 345. High ANXA13 expression predicts poor prognosis and correlates with lymph node metastasis in colorectal cancer patients 5. Additionally, ANXA13 mediates intracellular transport of ribosome-inactivating proteins 6 and serves as a receptor for bacterial adhesion factors on intestinal epithelial cells 7. ANXA13 shows diagnostic value as a biomarker distinguishing cholangiocellular carcinoma from pancreatic adenocarcinoma 8.

Sources cited
1
ANXA13 is lost in AKI kidneys and protects against ischemic-reperfusion and cisplatin-induced AKI by inhibiting TGF-β/Smad3 signaling
PMID: 41486854
2
ANXA13 is upregulated in clear cell renal cell carcinoma and promotes cell proliferation, migration, and invasion while attenuating apoptosis
PMID: 37520951
3
ANXA13 is required for intracellular transport of vesicles containing ribosome-inactivating proteins
PMID: 33119820
4
ANXA13 induces fragmented membrane rolling on anionic membranes, generating membrane curvature
PMID: 29985397
5
ANXA13 is a biomarker candidate elevated in cholangiocellular carcinoma with diagnostic value
PMID: 26644413
6
ANXA13 is highly expressed in lung adenocarcinoma, predicts poor prognosis, and promotes proliferation and migration via epithelial-mesenchymal transition
PMID: 32145097
7
ANXA13 promotes colorectal cancer cell invasion in vitro and correlates with lymph node metastasis and poor survival
PMID: 28423508
8
ANXA13 functions as a receptor-like molecule mediating bacterial adhesion to intestinal epithelial cells
PMID: 24936355
Disease Associationsⓘ20
Otitis mediaOpen Targets
0.45Moderate
breast carcinomaOpen Targets
0.44Moderate
eustachian tube diseaseOpen Targets
0.44Moderate
prostate carcinomaOpen Targets
0.41Moderate
Conductive hearing impairmentOpen Targets
0.35Weak
tympanic membrane diseaseOpen Targets
0.33Weak
triple-negative breast cancerOpen Targets
0.33Weak
otitis media with effusionOpen Targets
0.30Weak
Paralytic ileusOpen Targets
0.28Weak
COVID-19Open Targets
0.27Weak
multiple myelomaOpen Targets
0.27Weak
auditory system diseaseOpen Targets
0.27Weak
chronic intestinal vascular insufficiencyOpen Targets
0.21Weak
hyperpituitarismOpen Targets
0.21Weak
neoplasmOpen Targets
0.09Suggestive
Barrett's esophagusOpen Targets
0.08Suggestive
hepatocellular carcinomaOpen Targets
0.08Suggestive
colorectal carcinomaOpen Targets
0.07Suggestive
nonpapillary renal cell carcinomaOpen Targets
0.07Suggestive
tibia, hypoplasia or aplasia of, with polydactylyOpen Targets
0.06Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
PPDPFLShared pathway100%ETV3LShared pathway100%ERFLShared pathway100%NKX1-2Shared pathway100%NHSL2Shared pathway100%ZNF800Shared pathway100%
Tissue Expression6 tissues
Liver
100%
Brain
17%
Ovary
11%
Lung
3%
Heart
0%
Bone Marrow
0%
Gene Interaction Network
Click a node to explore
ANXA13PPDPFLETV3LERFLNKX1-2NHSL2ZNF800
PROTEIN STRUCTURE
Preparing viewer…
PDB6B3I · 2.60 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.96LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.71 [0.54–0.96]
RankingsWhere ANXA13 stands among ~20K protein-coding genes
  • #12,299of 20,598
    Most Researched28
  • #9,052of 17,882
    Most Constrained (LOEUF)0.96
Genes detectedANXA13
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Annexin A13 Protects Against Acute Kidney Injury by Inactivating TGF-β/Smad3 Signaling.
PMID: 41486854
Adv Sci (Weinh) · 2026
1.00
2
ANXA13 promotes cell proliferation and invasion and attenuates apoptosis in renal cell carcinoma.
PMID: 37520951
Heliyon · 2023
0.90
3
Intracellular Transport of Ribosome-Inactivating Proteins Depends on Annexin 13.
PMID: 33119820
Dokl Biochem Biophys · 2020
0.80
4
Annexins induce curvature on free-edge membranes displaying distinct morphologies.
PMID: 29985397
Sci Rep · 2018
0.70
5
Immunohistochemical Markers Distinguishing Cholangiocellular Carcinoma (CCC) from Pancreatic Ductal Adenocarcinoma (PDAC) Discovered by Proteomic Analysis of Microdissected Cells.
PMID: 26644413
Mol Cell Proteomics · 2016
0.60