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25 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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DRD1
dopamine receptor D1
Chromosome 5 · 5q35.2
NCBI Gene: 1812Ensembl: ENSG00000184845.5HGNC: HGNC:3020UniProt: P21728
315PubMed Papers
20Diseases
15Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Highly ConstrainedReceptor
RESEARCH IMPACT
Trending
CLINICAL
FDA Approved Target
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
arrestin family protein bindingG protein-coupled receptor complexdopamine neurotransmitter receptor activity, coupled via Gsnon-motile ciliumParkinson diseasehemorrhagemajor depressive disordercardiovascular disease
✦AI Summary

DRD1 is a G protein-coupled dopamine receptor that mediates cellular responses through adenylyl cyclase activation and cyclic adenosine monophosphate (cAMP) signaling 1. Structurally, DRD1 recognizes dopamine through a polar interaction network and can form heterotetramers with DRD3 to regulate beta-arrestin recruitment and locomotor activity 2. Beyond classical neurotransmission, DRD1 plays immunomodulatory roles: dopamine suppresses group 2 innate lymphoid cell responses in allergic airway inflammation through DRD1-dependent inhibition of mitochondrial oxidative phosphorylation 3, and DRD1 signaling prevents NLRP3 inflammasome activation via cAMP-mediated ubiquitination and degradation, thereby reducing neuroinflammation and systemic inflammation 1. Clinically, DRD1 gene polymorphisms (particularly rs4532) are associated with hypertension risk in ethnicity-specific patterns 4 and with chr5 obstructive pulmonary disease subtypes featuring mucin hypersecretion and accelerated lung function decline 5. DRD1 agonists show promise as antifibrotic agents through YAP/TAZ pathway inhibition in pulmonary fibrosis 6. Additionally, DRD1 variants associate with alcohol dependence in some populations 7 and represent candidate genes in attention-deficit/hyperactivity disorder pathogenesis 8.

Sources cited
1
DRD1 structure, dopamine recognition mechanisms, allosteric regulation, and G protein coupling
PMID: 33571432
2
DRD1-dependent dopamine suppression of ILC2 responses and allergic lung inflammation via mitochondrial OXPHOS inhibition
PMID: 36693372
3
DRD1 signaling inhibits NLRP3 inflammasome through cAMP-mediated ubiquitination via MARCH7, reducing neuroinflammation and systemic inflammation
PMID: 25594175
4
DRD1 rs4532 polymorphism associated with hypertension risk with ethnicity-specific patterns
PMID: 26730182
5
DRD1 gene variant near rs4532 associated with COPD emphysema subtype featuring chronic bronchitis and mucin hypersecretion
PMID: 37268414
6
DRD1 agonists inhibit YAP/TAZ signaling and demonstrate antifibrotic effects in pulmonary fibrosis
PMID: 39329703
7
DRD1 rs4532 polymorphism shows association with alcohol dependence in meta-analysis
PMID: 37466123
8
DRD1 is a candidate gene in ADHD pathogenesis related to dopaminergic pathway dysfunction
PMID: 36211978
Disease Associationsⓘ20
Parkinson diseaseOpen Targets
0.63Moderate
hemorrhageOpen Targets
0.59Moderate
major depressive disorderOpen Targets
0.56Moderate
cardiovascular diseaseOpen Targets
0.50Moderate
Alzheimer diseaseOpen Targets
0.50Moderate
hypertensionOpen Targets
0.47Moderate
neurodegenerative diseaseOpen Targets
0.46Moderate
Tourette syndromeOpen Targets
0.46Moderate
schizophreniaOpen Targets
0.40Moderate
depressive disorderOpen Targets
0.37Weak
psychosisOpen Targets
0.37Weak
lysosomal storage diseaseOpen Targets
0.37Weak
TicsOpen Targets
0.37Weak
multiple sclerosisOpen Targets
0.37Weak
spontaneous abortionOpen Targets
0.37Weak
liver diseaseOpen Targets
0.34Weak
cocaine dependenceOpen Targets
0.33Weak
acute kidney injuryOpen Targets
0.33Weak
cerebral atherosclerosisOpen Targets
0.33Weak
kidney failureOpen Targets
0.26Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets15
AMINEPTINEApproved
Dopamine D1 and D2 receptor antagonist
major depressive disorder
AMOXAPINEApproved
Dopamine receptor antagonist
major depressive disorder
ECOPIPAMPhase III
Dopamine D1 receptor antagonist
cocaine dependence
ERGOLOID MESYLATESApproved
Serotonin 1a (5-HT1a) receptor agonist
cardiovascular disease
FENOLDOPAMApproved
Dopamine D1 receptor agonist
cardiovascular disease
FENOLDOPAM MESYLATEApproved
Dopamine D1 receptor agonist
hypertension
METHYLERGONOVINEApproved
Serotonin 2b (5-HT2b) receptor partial agonist
spontaneous abortion
METHYLERGONOVINE MALEATEApproved
Serotonin 2b (5-HT2b) receptor partial agonist
hemorrhage
MEVIDALENPhase II
Dopamine D1 receptor positive allosteric modulator
Parkinson disease
MINAPRINEApproved
Dopamine D1 and D2 receptor agonist
depressive disorder
MINAPRINE HYDROCHLORIDEUNKNOWN
Dopamine D1 and D2 receptor agonist
PERGOLIDEApproved
Dopamine receptor agonist
Parkinson disease
PERGOLIDE MESYLATEUNKNOWN
Dopamine receptor agonist
PIMOZIDEApproved
Dopamine receptor antagonist
Tics
TAVAPADONPhase III
Dopamine D1 receptor partial agonist
Parkinson disease
Related Genes
DLG4Protein interaction100%CALYProtein interaction95%GNALProtein interaction95%GNASProtein interaction95%COMTProtein interaction94%GRIA1Protein interaction93%
Tissue Expression6 tissues
Brain
100%
Liver
36%
Lung
22%
Ovary
6%
Bone Marrow
4%
Heart
1%
Gene Interaction Network
Click a node to explore
DRD1DLG4CALYGNALGNASCOMTGRIA1
PROTEIN STRUCTURE
Preparing viewer…
PDB9I54 · 2.72 Å · EM
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.25Highly Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.08 [0.03–0.25]
RankingsWhere DRD1 stands among ~20K protein-coding genes
  • #1,075of 20,598
    Most Researched315 · top 10%
  • #151of 1,025
    FDA-Approved Drug Targets10 · top quartile
  • #781of 17,882
    Most Constrained (LOEUF)0.25 · top 5%
Genes detectedDRD1
Sources retrieved25 papers
Response time—
📄 Sources
25▼
1
Dopamine inhibits group 2 innate lymphoid cell-driven allergic lung inflammation by dampening mitochondrial activity.
PMID: 36693372
Immunity · 2023
1.00
2
Dopamine controls systemic inflammation through inhibition of NLRP3 inflammasome.
PMID: 25594175
Cell · 2015
0.90
3
YAP/TAZ Signaling in the Pathobiology of Pulmonary Fibrosis.
PMID: 39329703
Cells · 2024
0.80
4
Ligand recognition and allosteric regulation of DRD1-Gs signaling complexes.
PMID: 33571432
Cell · 2021
0.70
5
Structural basis of psychedelic LSD recognition at dopamine D
PMID: 39094559
Neuron · 2024
0.68