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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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FZD10
frizzled class receptor 10
Chromosome 12 · 12q24.33
NCBI Gene: 11211Ensembl: ENSG00000111432.5HGNC: HGNC:4039UniProt: Q6NSL8
34PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
regulation of actin cytoskeleton organizationprotein bindingWnt receptor activitynon-canonical Wnt signaling pathwayneurodegenerative diseaseandrogenetic alopeciaadverse effectresponse to stimulus
✦AI Summary

FZD10 is a G protein-coupled Wnt receptor that functions primarily in the canonical Wnt/β-catenin signaling pathway, leading to disheveled activation, GSK-3 inhibition, β-catenin nuclear accumulation, and transcriptional activation of Wnt target genes 1. Beyond canonical signaling, FZD10 also participates in non-canonical pathways involving PKC and calcium fluxes, with potential roles in tissue morphogenesis and polarity information transduction. FZD10 has significant disease relevance, particularly in cancer development and progression. In hepatocellular carcinoma, elevated FZD10 expression—regulated by METTL3-dependent N6-methyladenosine methylation—promotes liver cancer stem cell self-renewal and lenvatinib resistance through β-catenin/YAP1 activation 1. FZD10-containing exosomes sustain cancer cell proliferation across colorectal, gastric, hepatic, and cholangiocarcinoma cells, potentially mediating long-distance metastatization 2. FZD10 is highly expressed in synovial sarcoma tumors but absent in most normal tissues, making it an attractive therapeutic target 34. Clinically, FZD10 shows promise as both a prognostic biomarker and therapeutic target. Radioimmunotherapy with anti-FZD10 antibodies demonstrates feasibility in synovial sarcoma patients 4, while FDA-approved drugs targeting FZD10 show cytotoxicity against nasopharyngeal carcinoma cells 5. Additionally, FZD10+ cochlear glial cells exhibit neuronal differentiation potential enhanced by Wnt signaling 6, suggesting broader regenerative medicine applications.

Sources cited
1
FZD10 is a G protein-coupled Wnt receptor that functions primarily in the canonical Wnt/β-catenin signaling pathway, leading to disheveled activation, GSK-3 inhibition, β-catenin nuclear accumulation, and transcriptional activation of Wnt target genes .
PMID: 36764493
2
FZD10-containing exosomes sustain cancer cell proliferation across colorectal, gastric, hepatic, and cholangiocarcinoma cells, potentially mediating long-distance metastatization .
PMID: 31349740
3
FZD10 is highly expressed in synovial sarcoma tumors but absent in most normal tissues, making it an attractive therapeutic target , .
PMID: 29884132
4
Radioimmunotherapy with anti-FZD10 antibodies demonstrates feasibility in synovial sarcoma patients , while FDA-approved drugs targeting FZD10 show cytotoxicity against nasopharyngeal carcinoma cells .
PMID: 39733096
5
Additionally, FZD10+ cochlear glial cells exhibit neuronal differentiation potential enhanced by Wnt signaling , suggesting broader regenerative medicine applications.
PMID: 39871249
Disease Associationsⓘ20
neurodegenerative diseaseOpen Targets
0.30Weak
androgenetic alopeciaOpen Targets
0.29Weak
adverse effectOpen Targets
0.26Weak
response to stimulusOpen Targets
0.26Weak
premature birthOpen Targets
0.20Weak
alopeciaOpen Targets
0.19Weak
myopiaOpen Targets
0.18Weak
Abruptio PlacentaeOpen Targets
0.13Weak
Dental malocclusionOpen Targets
0.13Weak
major salivary gland cancerOpen Targets
0.13Weak
thyroiditisOpen Targets
0.13Weak
squamous cell carcinomaOpen Targets
0.10Suggestive
metabolic diseaseOpen Targets
0.09Suggestive
clavicle fractureOpen Targets
0.09Suggestive
shoulder fractureOpen Targets
0.09Suggestive
facial morphologyOpen Targets
0.09Suggestive
colorectal carcinomaOpen Targets
0.09Suggestive
nasopharyngeal carcinomaOpen Targets
0.08Suggestive
gastric cancerOpen Targets
0.08Suggestive
neoplasmOpen Targets
0.06Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
DVL1Protein interaction99%BAMBIProtein interaction93%CTNNB1Protein interaction93%ZNRF3Protein interaction92%WNT3AProtein interaction92%GNAQProtein interaction91%
Tissue Expression6 tissues
Brain
100%
Ovary
87%
Lung
65%
Heart
20%
Bone Marrow
3%
Liver
3%
Gene Interaction Network
Click a node to explore
FZD10DVL1BAMBICTNNB1ZNRF3WNT3AGNAQ
PROTEIN STRUCTURE
Preparing viewer…
PDB7X8T · 2.51 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.86LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.56 [0.38–0.86]
RankingsWhere FZD10 stands among ~20K protein-coding genes
  • #11,156of 20,598
    Most Researched34
  • #7,472of 17,882
    Most Constrained (LOEUF)0.86
Genes detectedFZD10
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
N6-Methyladenosine-Mediated Up-Regulation of FZD10 Regulates Liver Cancer Stem Cells' Properties and Lenvatinib Resistance Through WNT/β-Catenin and Hippo Signaling Pathways.
PMID: 36764493
Gastroenterology · 2023
1.00
2
FZD10 Carried by Exosomes Sustains Cancer Cell Proliferation.
PMID: 31349740
Cells · 2019
0.90
3
Repurposing FDA-approved drugs targeting FZD10 in nasopharyngeal carcinoma: insights from molecular dynamics simulations and experimental validation.
PMID: 39733096
Sci Rep · 2024
0.80
4
Effects of aging and anatomic location on gene expression in human retina.
PMID: 22666212
Front Aging Neurosci · 2012
0.70
5
A first-in-human study investigating biodistribution, safety and recommended dose of a new radiolabeled MAb targeting FZD10 in metastatic synovial sarcoma patients.
PMID: 29884132
BMC Cancer · 2018
0.60