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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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HMOX2
heme oxygenase 2
Chromosome 16 · 16p13.3
NCBI Gene: 3163Ensembl: ENSG00000103415.12HGNC: HGNC:5014UniProt: A0A087WT44
145PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
response to hypoxiaheme oxygenase (decyclizing) activityplasma membranemembraneneuroinflammatory disorderschizophreniamigraine disordercancer
✦AI Summary

HMOX2 (heme oxygenase 2) catalyzes the oxidative cleavage of heme at the alpha-methene bridge, releasing carbon monoxide, biliverdin, and ferrous iron 1. This enzyme plays critical roles in heme catabolism and cellular responses to oxidative stress and hypoxia 2. Mechanistically, HMOX2 functions downstream of major hypoxic pathway regulators. In Tibetan populations, HMOX2 variants show evidence of positive selection and male-specific associations with hemoglobin levels, suggesting the enzyme modifies high-altitude adaptation by regulating heme breakdown and maintaining relatively low hemoglobin levels 3. Disease relevance spans multiple conditions. HMOX2 is associated with migraine susceptibility, specifically identified as a risk variant for migraine with aura 4. It was identified as a novel candidate gene in late-onset Parkinson's disease, with rare deleterious variants showing significant excess in affected individuals 5. In cancer biology, HMOX2 serves as a biomarker for tumor-initiating cells (TICs) in lung tumors and is therapeutically targetable, with selective HMOX2 inhibition reducing tumor growth and increasing survival 6. Additionally, HMOX2 contributes to melanosphere formation in melanoma through B-Raf-dependent mechanisms 7. Clinically, HMOX2 represents a promising therapeutic target for cancer treatment, particularly for therapy-resistant TICs 8, and understanding its variants may inform personalized approaches to migraine and neurodegenerative disease management.

Sources cited
1
HMOX2 catalyzes heme degradation to carbon monoxide, ferrous iron, and biliverdin; these products modulate inflammation, cell proliferation, apoptosis, and antioxidant defense
PMID: 27604527
2
HMOX is one of two isoforms (HMOX1 and HMOX2) that catalyzes the rate-controlling step of heme breakdown
PMID: 23720291
3
HMOX2 harbors adaptive variants in Tibetans; C allele at rs4786504 increases HMOX2 expression and associates with lower hemoglobin levels in males, contributing to high-altitude adaptation
PMID: 26781569
4
HMOX2 contains a risk variant specific for migraine with aura identified in genome-wide association study of 102,084 migraine cases
PMID: 35115687
5
HMOX2 identified as novel candidate gene in late-onset Parkinson's disease with significant excess of deleterious variants in affected individuals
PMID: 34148545
6
HMOX2 is a biomarker for tumor-initiating cells; targeting HMOX2 inhibits tumor growth and increases survival in lung cancer models
PMID: 31436967
7
HMOX2 transcriptional activation by oncogenic B-RafV600E increases melanosphere formation in melanoma
PMID: 32558263
8
HMOX2 mediates probe binding selectivity for tumor-initiating cells; ABCB1 regulates efflux and intracellular retention of HMOX2-targeting probes
PMID: 41520971
Disease Associationsⓘ20
neuroinflammatory disorderOpen Targets
0.23Weak
schizophreniaOpen Targets
0.15Weak
migraine disorderOpen Targets
0.13Weak
cancerOpen Targets
0.08Suggestive
cutaneous lupus erythematosusOpen Targets
0.06Suggestive
skin cancerOpen Targets
0.05Suggestive
dominant beta-thalassemiaOpen Targets
0.05Suggestive
Alzheimer diseaseOpen Targets
0.05Suggestive
Beta-thalassemia - X-linked thrombocytopeniaOpen Targets
0.05Suggestive
beta-thalassemia-X-linked thrombocytopenia syndromeOpen Targets
0.05Suggestive
hemoglobin D diseaseOpen Targets
0.05Suggestive
paramyotonia congenita of Von EulenburgOpen Targets
0.05Suggestive
dehydrated hereditary stomatocytosisOpen Targets
0.05Suggestive
Congenital dyserythropoietic anemia type IOpen Targets
0.05Suggestive
Hemoglobin C - beta-thalassemiaOpen Targets
0.04Suggestive
hemoglobin C-beta-thalassemia syndromeOpen Targets
0.04Suggestive
hemoglobin H diseaseOpen Targets
0.04Suggestive
overhydrated hereditary stomatocytosisOpen Targets
0.04Suggestive
Ichthyosis - hepatosplenomegaly - cerebellar degenerationOpen Targets
0.04Suggestive
ichthyosis-hepatosplenomegaly-cerebellar degeneration syndromeOpen Targets
0.04Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
NFE2L2Protein interaction99%PORProtein interaction97%HEPHProtein interaction94%HARS2Protein interaction93%COX10Protein interaction91%CPProtein interaction91%
Tissue Expression6 tissues
Liver
100%
Heart
96%
Brain
65%
Lung
47%
Bone Marrow
30%
Ovary
26%
Gene Interaction Network
Click a node to explore
HMOX2NFE2L2PORHEPHHARS2COX10CP
PROTEIN STRUCTURE
Preparing viewer…
PDB5UC9 · 1.90 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.09LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.77 [0.55–1.09]
RankingsWhere HMOX2 stands among ~20K protein-coding genes
  • #3,138of 20,598
    Most Researched145 · top quartile
  • #11,060of 17,882
    Most Constrained (LOEUF)1.09
Genes detectedHMOX2
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Genome-wide analysis of 102,084 migraine cases identifies 123 risk loci and subtype-specific risk alleles.
PMID: 35115687
Nat Genet · 2022
1.00
2
Identification of sixteen novel candidate genes for late onset Parkinson's disease.
PMID: 34148545
Mol Neurodegener · 2021
0.90
3
Heme Oxygenases in Cardiovascular Health and Disease.
PMID: 27604527
Physiol Rev · 2016
0.80
4
A Near-Infrared Probe Tracks and Treats Lung Tumor Initiating Cells by Targeting HMOX2.
PMID: 31436967
J Am Chem Soc · 2019
0.70
5
HMOX2 Functions as a Modifier Gene for High-Altitude Adaptation in Tibetans.
PMID: 26781569
Hum Mutat · 2016
0.60