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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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LSM14A
LSM14A mRNA processing body assembly factor
Chromosome 19 · 19q13.11
NCBI Gene: 26065Ensembl: ENSG00000257103.10HGNC: HGNC:24489UniProt: Q8ND56
118PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
RNA bindingcytoplasmic stress granulecytoplasmic ribonucleoprotein granulemitotic spindlegram-negative bacterial infectionsplacenta praevianeurodegenerative diseasehepatocellular carcinoma
✦AI Summary

LSM14A is an RNA-binding protein essential for processing body (P-body) formation, cytoplasmic membraneless organelles that sequester translationally inactive mRNAs 123. LSM14A acts as a translational repressor and directly associates with core P-body proteins like DDX6 to facilitate their condensation through liquid-liquid phase separation 45. Beyond canonical P-body assembly, LSM14A plays critical roles in innate immunity by sensing viral RNA to activate interferon-β production pathways 6, while also regulating translation of DNA damage response genes including RTEL1 and LIG4 upon genotoxic stress 7. In disease contexts, LSM14A is a core component of the YAP/TAZ-driven P-body axis that promotes colorectal cancer cell proliferation and tumorigenesis 8. Genome-wide association studies identified LSM14A variants associated with diabetic kidney disease susceptibility 9. However, LSM14A appears dispensable for spermatogenesis, suggesting functional redundancy among LSM family members in certain contexts 10. Pathogenic viruses exploit LSM14A's antiviral function: SFTSV NSs protein directly inhibits LSM14A-mediated interferon signaling to evade host immunity 11.

Sources cited
1
LSM14A is essential for P-body formation and mRNA storage
PMID: 16484376
2
LSM14A protects mRNAs from degradation in P-bodies
PMID: 17074753
3
LSM14A acts as a translational repressor in P-bodies
PMID: 29510985
4
LSM14A interacts with DDX6 to promote P-body assembly and protein synthesis inhibition
PMID: 38769438
5
LSM14A-TRIBE-STAMP identifies P-body-associated mRNAs and their dynamic association patterns
PMID: 41213943
6
LSM14A mediates interferon-β production by sensing viral RNA in innate immunity
PMID: 28666650
7
LSM14A regulates translation of DNA damage response genes upon genotoxic stress
PMID: 40275106
8
LSM14A is a P-body core gene promoting YAP/TAZ-driven cancer cell proliferation
PMID: 39046443
9
LSM14A variants are associated with diabetic kidney disease risk
PMID: 35763030
10
LSM14A is dispensable for spermatogenesis in mice, suggesting functional redundancy
PMID: 41237998
11
SFTSV NSs protein inhibits LSM14A-mediated antiviral signaling
PMID: 34244294
Disease Associationsⓘ20
gram-negative bacterial infectionsOpen Targets
0.32Weak
placenta praeviaOpen Targets
0.24Weak
neurodegenerative diseaseOpen Targets
0.22Weak
hepatocellular carcinomaOpen Targets
0.19Weak
multiple myelomaOpen Targets
0.19Weak
gastric adenocarcinomaOpen Targets
0.19Weak
lung adenocarcinomaOpen Targets
0.19Weak
acute myeloid leukemiaOpen Targets
0.18Weak
breast ductal adenocarcinomaOpen Targets
0.18Weak
central nervous system primitive neuroectodermal neoplasmOpen Targets
0.18Weak
colon adenocarcinomaOpen Targets
0.18Weak
Hepatobiliary NeoplasmOpen Targets
0.18Weak
HER2 Positive Breast CarcinomaOpen Targets
0.18Weak
kidney neoplasmOpen Targets
0.18Weak
lung carcinomaOpen Targets
0.18Weak
melanomaOpen Targets
0.18Weak
rectal adenocarcinomaOpen Targets
0.18Weak
skin basal cell carcinomaOpen Targets
0.18Weak
spitz nevusOpen Targets
0.18Weak
squamous cell lung carcinomaOpen Targets
0.18Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
DCP2Protein interaction100%EDC3Protein interaction100%DCP1AProtein interaction100%LSM1Protein interaction100%NCLProtein interaction100%G3BP1Protein interaction100%
Tissue Expression6 tissues
Bone Marrow
100%
Ovary
59%
Brain
59%
Heart
58%
Lung
48%
Liver
40%
Gene Interaction Network
Click a node to explore
LSM14ADCP2EDC3DCP1ALSM1NCLG3BP1
PROTEIN STRUCTURE
Preparing viewer…
PDB6F9W · 2.62 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.45Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.28 [0.18–0.45]
RankingsWhere LSM14A stands among ~20K protein-coding genes
  • #4,001of 20,598
    Most Researched118 · top quartile
  • #2,502of 17,882
    Most Constrained (LOEUF)0.45 · top quartile
Genes detectedLSM14A
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
YAP/TAZ enhances P-body formation to promote tumorigenesis.
PMID: 39046443
Elife · 2024
1.00
2
Genome-wide meta-analysis and omics integration identifies novel genes associated with diabetic kidney disease.
PMID: 35763030
Diabetologia · 2022
0.90
3
Energy stress promotes P-bodies formation via lysine-63-linked polyubiquitination of HAX1.
PMID: 38769438
EMBO J · 2024
0.80
4
Systematic characterization of the composition and dynamics of processing body-associated mRNAs.
PMID: 41213943
Nat Commun · 2025
0.70
5
Functional characterization of duck LSm14A in IFN-β induction.
PMID: 28666650
Dev Comp Immunol · 2017
0.60