HomeAboutRankingsData Sources
Β© 2026 GeneE
🧬
GeneE
10 sources retrieved Β· Most recent: April 2026 Β· Index updated 14 days ago
β“˜GeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
SLC32A1
solute carrier family 32 member 1
Chromosome 20 Β· 20q11.23
NCBI Gene: 140679Ensembl: ENSG00000101438.4HGNC: HGNC:11018UniProt: Q9H598
26PubMed Papers
22Diseases
0Drugs
6Pathogenic Variants
FUNCTIONAL ROLE
Transporter
CLINICAL
OMIM Disease Gene
DATA QUALITY
βœ“ Experimental GO Evidenceβœ“ Swiss-Prot Reviewed
neuron projection terminusneuron projectiondendriteglycine:proton antiporter activitydevelopmental and epileptic encephalopathy 114generalized epilepsy with febrile seizures plus, type 12generalized epilepsy with febrile seizures plusGeneralized epilepsy with febrile seizures-plus
✦AI Summary

SLC32A1 encodes the vesicular inhibitory amino acid transporter (VGAT), a proton-antiporter that loads gamma-aminobutyric acid (GABA) and glycine into synaptic vesicles for neurotransmitter release 1. The transporter exchanges vesicular protons for cytosolic GABA, enabling GABAergic neurotransmission at inhibitory synapses 2. SLC32A1 is the sole protein identified to date responsible for packaging GABA and glycine into synaptic vesicles 1. De novo missense variants in SLC32A1 cause developmental and epileptic encephalopathy (DEE114) characterized by moderate-to-severe intellectual disability, infantile-onset seizures, and movement disorders 1. Pathogenic variants impair GABAergic neurotransmission through two mechanisms: reduced synaptic vesicle GABA filling and altered presynaptic release probability 1. Inherited missense variants also cause genetic epilepsy with febrile seizures plus (GEFS+12) by altering GABA transport 2. Beyond epilepsy, SLC32A1 dysregulation associates with psychiatric and neurodegenerative conditions. In post-traumatic stress disorder, SLC32A1 is downregulated through hsa-mir-589-mediated mechanisms, contributing to GABAergic dysfunction 3. SLC32A1 expression marks early Alzheimer's disease pathology, particularly in dysfunctional synaptic signaling 4. The gene also influences metabolic homeostasis, with variants associated with circulating leptin levels independent of adiposity 5. SLC32A1 represents a critical node in GABAergic neurotransmission with broad relevance to neurological, psychiatric, and metabolic diseases.

Sources cited
1
De novo missense variants in SLC32A1 cause developmental and epileptic encephalopathy with intellectual disability, infantile-onset epilepsy, and movement disorders through impaired GABA vesicle filling or altered synaptic plasticity
PMID: 36073542
2
Inherited missense variants in SLC32A1 cause genetic epilepsy with febrile seizures plus by altering GABA transport into synaptic vesicles
PMID: 34038384
3
SLC32A1 (GABA vesicular transporter) is downregulated in post-traumatic stress disorder brain through miRNA-589-mediated mechanisms, contributing to GABAergic dysfunction
PMID: 40301990
4
SLC32A1 is identified as a hub gene and marker for early Alzheimer's disease subtype characterized by dysfunctional synaptic signaling
PMID: 39650656
5
SLC32A1 locus variants associate with circulating leptin levels independently of adiposity, suggesting roles in metabolic regulation
PMID: 26833098
6
SLC32A1 (Slc32a1) expression is upregulated in AGRP neurons and involved in feeding and stress response behaviors through GABA neurotransmission
PMID: 36189793
Disease Associationsβ“˜22
developmental and epileptic encephalopathy 114Open Targets
0.64Moderate
generalized epilepsy with febrile seizures plus, type 12Open Targets
0.58Moderate
generalized epilepsy with febrile seizures plusOpen Targets
0.47Moderate
Generalized epilepsy with febrile seizures-plusOpen Targets
0.39Weak
SeizureOpen Targets
0.37Weak
Intellectual disabilityOpen Targets
0.37Weak
early-infantile DEEOpen Targets
0.37Weak
restless legs syndromeOpen Targets
0.33Weak
neurodegenerative diseaseOpen Targets
0.26Weak
neuroinflammatory disorderOpen Targets
0.25Weak
alcohol drinkingOpen Targets
0.24Weak
Abruptio PlacentaeOpen Targets
0.24Weak
hypothyroidismOpen Targets
0.22Weak
developmental and epileptic encephalopathyOpen Targets
0.22Weak
genetic disorderOpen Targets
0.19Weak
obesityOpen Targets
0.12Weak
Generalized-onset seizureOpen Targets
0.12Weak
Mild global developmental delayOpen Targets
0.12Weak
Alzheimer diseaseOpen Targets
0.08Suggestive
metabolic syndromeOpen Targets
0.07Suggestive
Developmental and epileptic encephalopathy 114UniProt
Generalized epilepsy with febrile seizures plus 12UniProt
Pathogenic Variants6
NM_080552.3(SLC32A1):c.272C>G (p.Ala91Gly)Likely pathogenic
not provided
β˜…β˜†β˜†β˜†2024β†’ Residue 91
NM_080552.3(SLC32A1):c.806T>C (p.Leu269Pro)Likely pathogenic
Seizure;Intellectual disability
β˜…β˜†β˜†β˜†2021β†’ Residue 269
NM_080552.3(SLC32A1):c.965T>G (p.Phe322Cys)Likely pathogenic
Intellectual disability;Seizure|Developmental and epileptic encephalopathy 114
β˜…β˜†β˜†β˜†2021β†’ Residue 322
NM_080552.3(SLC32A1):c.989T>C (p.Met330Thr)Pathogenic
Generalized epilepsy with febrile seizures plus|Generalized epilepsy with febrile seizures plus, type 12
β˜†β˜†β˜†β˜†2024β†’ Residue 330
NM_080552.3(SLC32A1):c.1403T>C (p.Leu468Pro)Pathogenic
Generalized epilepsy with febrile seizures plus|Generalized epilepsy with febrile seizures plus, type 12
β˜†β˜†β˜†β˜†2024β†’ Residue 468
NM_080552.3(SLC32A1):c.806T>A (p.Leu269Gln)Pathogenic
Developmental and epileptic encephalopathy 114
β˜†β˜†β˜†β˜†2024β†’ Residue 269
View on ClinVar β†—
Related Genes
SLC17A8Protein interaction98%SLC18A1Protein interaction95%SSTProtein interaction94%SYT1Protein interaction92%DNAJC5Protein interaction91%VAMP2Protein interaction91%
Tissue Expression6 tissues
Brain
100%
Bone Marrow
51%
Ovary
0%
Heart
0%
Lung
0%
Liver
0%
Gene Interaction Network
Click a node to explore
SLC32A1SLC17A8SLC18A1SSTSYT1DNAJC5VAMP2
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted Β· UniProt Q9H598
View on AlphaFold β†—
Constraintβ“˜
LOEUFβ“˜
0.40Moderately Constrained
pLIβ“˜
1.00Intolerant
Observed/Expected LoF0.22 [0.13–0.40]
RankingsWhere SLC32A1 stands among ~20K protein-coding genes
  • #12,878of 20,598
    Most Researched26
  • #3,432of 5,498
    Most Pathogenic Variants6
  • #1,976of 17,882
    Most Constrained (LOEUF)0.40 Β· top quartile
Genes detectedSLC32A1
Sources retrieved10 papers
Response timeβ€”
πŸ“„ Sources
10β–Ό
1
Endothelial TFEB signaling-mediated autophagic disturbance initiates microglial activation and cognitive dysfunction.
PMID: 36588318
Autophagy Β· 2023
1.00
2
Identification of early Alzheimer's disease subclass and signature genes based on PANoptosis genes.
PMID: 39650656
Front Immunol Β· 2024
0.90
3
A multi-omic approach implicates novel protein dysregulation in post-traumatic stress disorder.
PMID: 40301990
Genome Med Β· 2025
0.80
4
PMID: 34038378
Neurology Β· 2021
0.70
5
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission.
PMID: 36073542
Ann Neurol Β· 2022
0.60