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10 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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TRIM50
tripartite motif containing 50
Chromosome 7 · 7q11.23
NCBI Gene: 135892Ensembl: ENSG00000146755.12HGNC: HGNC:19017UniProt: B7ZLG2
24PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
identical protein bindingprotein bindingubiquitin protein ligase activityinnate immune responseovarian neoplasmgastric cancerneoplasmhepatocellular carcinoma
✦AI Summary

TRIM50 is an E3 ubiquitin ligase that functions as a multifaceted tumor suppressor regulating cellular homeostasis through ubiquitin-dependent and independent mechanisms. Structurally, TRIM50 contains a RING domain essential for E3 ligase activity and a B-box domain that mediates protein interactions 1. Primary Function: TRIM50 catalyzes K63-linked polyubiquitination of Beclin-1, enhancing its interaction with ULK1 to promote starvation-induced autophagy initiation 2. It also ubiquitinates p62/SQSTM1, facilitating aggresome-associated protein clearance through HDAC6 interaction 3. Additionally, TRIM50 mediates K48-linked ubiquitination of Src, targeting it for proteasomal degradation 1. Disease Relevance: TRIM50 is consistently downregulated across multiple malignancies including gastric cancer, triple-negative breast cancer, and hepatocellular carcinoma 456. In gastric cancer, TRIM50 ubiquitinates PGK1 to suppress glycolysis and inhibit tumor-associated macrophage M2 polarization, impairing invasion 4. TRIM50 ubiquitinates JUP, preventing its nuclear translocation and MYC pathway activation 7. In ovarian cancer, TRIM50 suppresses Src-dependent progression 1. Clinical Significance: TRIM50 expression inversely correlates with cancer stage, grade, and metastatic status 1. The MAZ/METTL3 axis represses TRIM50 through m6A-dependent mechanisms in hepatocellular carcinoma 68, suggesting TRIM50 restoration as a therapeutic strategy. TRIM50 correlates with immune infiltration and patient prognosis in HCC 8.

Sources cited
1
Structurally, TRIM50 contains a RING domain essential for E3 ligase activity and a B-box domain that mediates protein interactions .
PMID: 31176697
2
Primary Function: TRIM50 catalyzes K63-linked polyubiquitination of Beclin-1, enhancing its interaction with ULK1 to promote starvation-induced autophagy initiation .
PMID: 29604308
3
It also ubiquitinates p62/SQSTM1, facilitating aggresome-associated protein clearance through HDAC6 interaction .
PMID: 24308962
4
Disease Relevance: TRIM50 is consistently downregulated across multiple malignancies including gastric cancer, triple-negative breast cancer, and hepatocellular carcinoma , , .
PMID: 38993561
5
TRIM50 ubiquitinates JUP, preventing its nuclear translocation and MYC pathway activation .
PMID: 37409971
6
The MAZ/METTL3 axis represses TRIM50 through m6A-dependent mechanisms in hepatocellular carcinoma , , suggesting TRIM50 restoration as a therapeutic strategy.
PMID: 40288151
Disease Associationsⓘ20
ovarian neoplasmOpen Targets
0.25Weak
gastric cancerOpen Targets
0.10Weak
neoplasmOpen Targets
0.10Weak
hepatocellular carcinomaOpen Targets
0.09Suggestive
triple-negative breast cancerOpen Targets
0.07Suggestive
breast cancerOpen Targets
0.06Suggestive
gastric carcinomaOpen Targets
0.05Suggestive
HypercholesterolemiaOpen Targets
0.05Suggestive
inflammatory bowel disease 30Open Targets
0.04Suggestive
CDH1-related diffuse gastric and lobular breast cancer syndromeOpen Targets
0.03Suggestive
Familial gastric cancerOpen Targets
0.03Suggestive
NK-cell enteropathyOpen Targets
0.03Suggestive
liver cancerOpen Targets
0.02Suggestive
musculoskeletal system diseaseOpen Targets
0.02Suggestive
ovarian cancerOpen Targets
0.02Suggestive
Crohn's diseaseOpen Targets
0.02Suggestive
cancerOpen Targets
0.01Suggestive
neuroblastomaOpen Targets
0.01Suggestive
lymph node metastatic carcinomaOpen Targets
0.01Suggestive
pancreatic ductal adenocarcinomaOpen Targets
0.00Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
DEFB131BShared pathway100%DEFB131AShared pathway100%DEFB134Shared pathway100%TRIM74Shared pathway100%TRIM73Shared pathway100%BPIFB3Shared pathway100%
Tissue Expression6 tissues
Liver
100%
Ovary
63%
Brain
37%
Lung
32%
Bone Marrow
11%
Heart
0%
Gene Interaction Network
Click a node to explore
TRIM50DEFB131BDEFB131ADEFB134TRIM74TRIM73BPIFB3
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q86XT4
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
1.07LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.80 [0.61–1.07]
RankingsWhere TRIM50 stands among ~20K protein-coding genes
  • #13,337of 20,598
    Most Researched24
  • #10,807of 17,882
    Most Constrained (LOEUF)1.07
Genes detectedTRIM50
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
TRIM50 inhibits glycolysis and the malignant progression of gastric cancer by ubiquitinating PGK1.
PMID: 38993561
Int J Biol Sci · 2024
1.00
2
MAZ-mediated N6-methyladenosine modification of ZEB1 promotes hepatocellular carcinoma progression by regulating METTL3.
PMID: 40038747
J Transl Med · 2025
0.90
3
Tripartite motif-containing protein 50 suppresses triple-negative breast cancer progression by regulating the epithelial-mesenchymal transition.
PMID: 39538371
Cancer Biol Ther · 2024
0.80
4
TRIM50 Inhibits Gastric Cancer Progression by Regulating the Ubiquitination and Nuclear Translocation of JUP.
PMID: 37409971
Mol Cancer Res · 2023
0.70
5
TRIM50 acts as a novel Src suppressor and inhibits ovarian cancer progression.
PMID: 31176697
Biochim Biophys Acta Mol Cell Res · 2019
0.60