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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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ZNF804A
zinc finger protein 804A
Chromosome 2 · 2q32.1
NCBI Gene: 91752Ensembl: ENSG00000170396.9HGNC: HGNC:21711UniProt: Q7Z570
140PubMed Papers
20Diseases
0Drugs
1Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
positive regulation of gene expressionregulation of neuron projection developmentpositive regulation of neuron projection developmentdendritic shaftschizophreniaobesitybipolar disordermajor depressive disorder
✦AI Summary

ZNF804A encodes a zinc finger transcription factor with roles in neurodevelopment and psychiatric disease susceptibility. Functionally, ZNF804A localizes to the cytoplasm, nucleus, and neuronal compartments including dendritic spines and growth cones, where it regulates neuron projection development and gene expression 1. The protein functions as a transcription factor in human brain tissue, particularly in addiction-relevant regions like the dorsolateral prefrontal cortex 2. Mechanistically, ZNF804A expression is regulated upstream by miR-148b-3p, which directly binds the 3' untranslated region of ZNF804A mRNA to suppress its expression 3. ZNF804A then regulates downstream genes including COMT and PRSS16 3. The risk allele rs1344706 associates with reduced D2/D3 dopamine receptor availability in the striatum, suggesting dopaminergic pathway involvement 4. Clinically, ZNF804A variants represent robust psychosis susceptibility loci. The rs1344706 SNP achieves genome-wide significance for schizophrenia across multiple populations 1, with associations confirmed in both Caucasian and Asian populations 5. Beyond schizophrenia, rs1344706 associates with bipolar disorder type I 6, major mood disorders 7, and heroin addiction 2. The gene shows gene-environment interactions, with ZNF804A genotype modulating cannabis use effects on psychosis proneness 8.

Sources cited
1
ZNF804A is a schizophrenia risk gene with rs1344706 achieving genome-wide significance; localizes to neuronal compartments; functions in brain development
PMID: 28289284
2
miR-148b-3p directly targets ZNF804A 3'UTR to inhibit expression; ZNF804A regulates COMT and PRSS16 expression in neuroblastoma cells
PMID: 32626976
3
ZNF804A rs1344706 risk allele associates with reduced D2/D3 dopamine receptor availability in striatum
PMID: 33712377
4
rs1344706 associates with schizophrenia in both Caucasian and Asian populations
PMID: 25526981
5
rs1344706 associates with bipolar disorder type I; ZNF804A expression is elevated in BD patients
PMID: 25935703
6
ZNF804A SNPs associate with major mood disorders including bipolar disorder and major depressive disorder
PMID: 27784192
7
ZNF804A rs1344706 and rs7597593 associate with heroin addiction; gene functions as transcription factor in addiction-relevant brain regions
PMID: 26382569
8
ZNF804A genotype interacts with cannabis use to modulate psychosis proneness and schizotypal traits
PMID: 30118824
Disease Associationsⓘ20
schizophreniaOpen Targets
0.52Moderate
obesityOpen Targets
0.43Moderate
bipolar disorderOpen Targets
0.39Weak
major depressive disorderOpen Targets
0.37Weak
substance-related disorderOpen Targets
0.35Weak
neurotic disorderOpen Targets
0.34Weak
insomniaOpen Targets
0.33Weak
overnutritionOpen Targets
0.32Weak
post-traumatic stress disorderOpen Targets
0.32Weak
intelligenceOpen Targets
0.32Weak
obsessive-compulsive disorderOpen Targets
0.32Weak
anorexia nervosaOpen Targets
0.31Weak
autism spectrum disorderOpen Targets
0.30Weak
neurodegenerative diseaseOpen Targets
0.29Weak
SyncopeOpen Targets
0.29Weak
ovarian neoplasmOpen Targets
0.29Weak
cannabis dependenceOpen Targets
0.28Weak
response to lithium ionOpen Targets
0.27Weak
carotid artery diseaseOpen Targets
0.27Weak
attention deficit hyperactivity disorderOpen Targets
0.25Weak
Pathogenic Variants1
NC_000002.12:g.(?_184830819)_(184884225_?)delLikely pathogenic
Schizophrenia
★☆☆☆2018
View on ClinVar ↗
Related Genes
DISC1Protein interaction79%DAOAProtein interaction77%DTNBP1Protein interaction74%COMTProtein interaction71%NRGNProtein interaction71%FRMD7Shared pathway25%
Tissue Expression6 tissues
Brain
100%
Bone Marrow
35%
Lung
11%
Liver
3%
Ovary
2%
Heart
0%
Gene Interaction Network
Click a node to explore
ZNF804ADISC1DAOADTNBP1COMTNRGNFRMD7
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q7Z570
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
0.37Moderately Constrained
pLIⓘ
1.00Intolerant
Observed/Expected LoF0.12 [0.05–0.37]
RankingsWhere ZNF804A stands among ~20K protein-coding genes
  • #3,296of 20,598
    Most Researched140 · top quartile
  • #4,790of 5,498
    Most Pathogenic Variants1
  • #1,715of 17,882
    Most Constrained (LOEUF)0.37 · top 10%
Genes detectedZNF804A
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
The schizophrenia risk gene ZNF804A: clinical associations, biological mechanisms and neuronal functions.
PMID: 28289284
Mol Psychiatry · 2017
1.00
2
The interaction between the ZNF804A gene and cannabis use on the risk of psychosis in a non-clinical sample.
PMID: 30118824
Prog Neuropsychopharmacol Biol Psychiatry · 2019
0.90
3
Polymorphism in the ZNF804A Gene and Variation in D
PMID: 33712377
Biol Psychiatry Cogn Neurosci Neuroimaging · 2023
0.80
4
Replication of ZNF804A gene variant associations with risk of heroin addiction.
PMID: 26382569
Genes Brain Behav · 2015
0.70
5
Schizophrenia‑associated microRNA‑148b‑3p regulates COMT and PRSS16 expression by targeting the ZNF804A gene in human neuroblastoma cells.
PMID: 32626976
Mol Med Rep · 2020
0.60