HomeAboutRankingsData Sources
© 2026 GeneE
🧬
GeneE
3 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
ⓘGeneE is for informational purposes only. It is not a substitute for professional medical advice, diagnosis, or treatment.
ZNRD2
zinc ribbon domain containing 2
Chromosome 11 · 11q13.1
NCBI Gene: 10534Ensembl: ENSG00000173465.8HGNC: HGNC:11328UniProt: G3V1B8
59PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
protein bindingmitotic cell cycleidentical protein bindingcytoplasmosteoarthritis, hipdiabetes mellitustype 2 diabetes mellitusneoplasm
✦AI Summary

ZNRD2 (zinc ribbon domain containing 2) is a multi-functional protein with primary roles in protein quality control and viral restriction. Its primary function involves serving as an adaptor protein that recruits the E3 ubiquitin ligase HERC2 to recognize orphaned subunits of the cytosolic chaperonin CCT, facilitating their selective ubiquitination and degradation 1. This recognition mechanism is essential for assembly quality control, as orphan subunits represent a major source of cellular quality control substrates 1. Structurally, ZNRD2 contains a zinc ribbon domain (ZNRD2) and functions as a Tankyrase 1 binding partner through its C-terminal domain, which additionally serves as a nuclear export signal 2. Beyond quality control, ZNRD2 acts as a host restriction factor against respiratory syncytial virus (RSV) by promoting aggregation and insolubility of RSV nucleoprotein, thereby impairing viral replication 3. However, RSV phosphoprotein antagonizes this antiviral function by maintaining viral nucleoprotein in monomeric form, creating a dynamic virus-host interaction 3. ZNRD2's centromere association and role in mitosis suggest additional functions in cell cycle regulation, and its identification as an autoantigen in Sjögren's syndrome and scleroderma indicates potential clinical relevance in autoimmune diseases 2.

Sources cited
1
ZNRD2 functions as an adaptor recruiting HERC2 E3 ligase to recognize and target orphaned CCT subunits for degradation in protein quality control
PMID: 37480851
2
ZNRD2 (zinc ribbon domain type 2) contains a zinc finger fold, binds Tankyrase 1 through its C-terminal domain, and functions as a nuclear export signal; associated with centromere and mitosis
PMID: 32170109
3
ZNRD2 acts as a host restriction factor against RSV by enhancing oligomerization of viral nucleoprotein, while RSV antagonizes this function and sequesters ZNRD2 into insoluble aggregates
PMID: 41566792
⚠Limited data available — This gene has 3 indexed publications. Summary and analysis may be incomplete.
Disease Associationsⓘ20
osteoarthritis, hipOpen Targets
0.16Weak
diabetes mellitusOpen Targets
0.15Weak
type 2 diabetes mellitusOpen Targets
0.14Weak
neoplasmOpen Targets
0.11Weak
breast cancerOpen Targets
0.11Weak
carpal tunnel syndromeOpen Targets
0.11Weak
cancerOpen Targets
0.11Weak
hepatocellular carcinomaOpen Targets
0.11Weak
gastric cancerOpen Targets
0.10Weak
nasopharyngeal carcinomaOpen Targets
0.10Weak
osteosarcomaOpen Targets
0.10Suggestive
melanomaOpen Targets
0.09Suggestive
stenosing tenosynovitisOpen Targets
0.09Suggestive
myocardial infarctionOpen Targets
0.09Suggestive
lymphomaOpen Targets
0.09Suggestive
non-small cell lung carcinomaOpen Targets
0.09Suggestive
Miyoshi myopathyOpen Targets
0.09Suggestive
chronic lymphocytic leukemiaOpen Targets
0.08Suggestive
cholesteatomaOpen Targets
0.08Suggestive
chronic myelogenous leukemiaOpen Targets
0.08Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
MYBL2Shared pathway100%CCT5Protein interaction100%NEK3Shared pathway50%NEDD1Shared pathway50%NEK9Shared pathway50%PBKShared pathway50%
Tissue Expression6 tissues
Bone Marrow
100%
Liver
92%
Lung
79%
Heart
77%
Ovary
71%
Brain
63%
Gene Interaction Network
Click a node to explore
ZNRD2MYBL2CCT5NEK3NEDD1NEK9PBK
PROTEIN STRUCTURE
Preparing viewer…
PDB6HCZ · 2.30 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
1.03LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.68 [0.46–1.03]
RankingsWhere ZNRD2 stands among ~20K protein-coding genes
  • #7,835of 20,598
    Most Researched59
  • #10,132of 17,882
    Most Constrained (LOEUF)1.03
Genes detectedZNRD2
Sources retrieved3 papers
Response time—
📄 Sources
3
1
Mechanism of orphan subunit recognition during assembly quality control.
PMID: 37480851
Cell · 2023
1.00
2
Sjögren syndrome/scleroderma autoantigen 1 is a direct Tankyrase binding partner in cancer cells.
PMID: 32170109
Commun Biol · 2020
0.67
3
ZNRD2 Mediated Nucleoprotein Aggregation Impairs Respiratory Syncytial Virus Replication.
PMID: 41566792
Adv Sci (Weinh) · 2026
0.33