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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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FZD7
frizzled class receptor 7
Chromosome 2 · 2q33.1
NCBI Gene: 8324Ensembl: ENSG00000155760.3HGNC: HGNC:4045UniProt: O75084
110PubMed Papers
20Diseases
1Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
CLINICAL
Early Pipeline
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
negative regulation of cardiac muscle cell differentiationphosphatidylinositol-4,5-bisphosphate bindingcanonical Wnt signaling pathwaymesenchymal to epithelial transitionAbnormality of the skeletal systemattention deficit hyperactivity disordersubstance abuseUterine leiomyoma
✦AI Summary

FZD7 (frizzled class receptor 7) functions as a transmembrane receptor for Wnt signaling pathways, playing critical roles in cancer progression and cellular development. The protein serves as a receptor for various Wnt ligands, including WNT2, WNT7A, and WNT11, mediating both canonical and non-canonical Wnt signaling 1 2 3. FZD7 activates downstream pathways including β-catenin signaling and FZD7/JAK1/STAT3 signaling, promoting tumor cell proliferation, invasion, and metastasis 2 4. In melanoma, WNT11-FZD7-DAAM1 signaling supports tumor-initiating abilities and amoeboid invasion through activation of Rho-ROCK1/2-Myosin II pathways 3. The receptor is significantly overexpressed in multiple cancer types including gastric cancer, colorectal cancer, intrahepatic cholangiocarcinoma, head and neck squamous cell carcinoma, and endometriosis 5 4 2 6. Therapeutically, soluble FZD7 decoy receptors can competitively inhibit Wnt signaling and reduce tumor cell viability, suggesting FZD7 as a potential therapeutic target 5 7. The protein also shows zonated expression patterns in hepatocytes, indicating roles in normal tissue organization 8.

Sources cited
1
FZD7 serves as a receptor for WNT2 ligand
PMID: 30191337
2
WNT7A activates FZD7/JAK1/STAT3 signaling pathway in head and neck cancer
PMID: 38246919
3
WNT11-FZD7-DAAM1 signaling supports tumor-initiating abilities and melanoma invasion
PMID: 33082334
4
FZD7 is overexpressed in gastric and colorectal cancers and soluble FZD7 can inhibit tumor progression
PMID: 35655594
5
FZD7 is upregulated in intrahepatic cholangiocarcinoma and promotes cancer progression
PMID: 34509526
6
FZD7 is upregulated in endometriosis
PMID: 40021920
7
FZD7 is a β-catenin target gene and potential therapeutic target
PMID: 29786110
8
FZD7 shows zonated expression in hepatocytes
PMID: 31535084
Disease Associationsⓘ20
Abnormality of the skeletal systemOpen Targets
0.46Moderate
attention deficit hyperactivity disorderOpen Targets
0.31Weak
substance abuseOpen Targets
0.31Weak
Uterine leiomyomaOpen Targets
0.31Weak
hair colorOpen Targets
0.29Weak
radius fractureOpen Targets
0.23Weak
ulna fractureOpen Targets
0.23Weak
bone fractureOpen Targets
0.21Weak
smoking initiationOpen Targets
0.16Weak
neoplasmOpen Targets
0.12Weak
breast cancerOpen Targets
0.10Weak
gastric cancerOpen Targets
0.10Weak
ovarian neoplasmOpen Targets
0.09Suggestive
esophageal squamous cell carcinomaOpen Targets
0.08Suggestive
cataractOpen Targets
0.08Suggestive
melanomaOpen Targets
0.08Suggestive
arthritisOpen Targets
0.08Suggestive
trauma complicationOpen Targets
0.08Suggestive
Alzheimer diseaseOpen Targets
0.08Suggestive
gliomaOpen Targets
0.08Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets1
VANTICTUMABPhase I
Frizzled-1 antagonist
Related Genes
AXIN1Protein interaction100%ROR1Protein interaction100%ROR2Protein interaction100%VANGL2Protein interaction99%SDC4Protein interaction98%DAAM1Protein interaction98%
Tissue Expression6 tissues
Heart
100%
Ovary
88%
Lung
19%
Brain
16%
Liver
4%
Bone Marrow
3%
Gene Interaction Network
Click a node to explore
FZD7AXIN1ROR1ROR2VANGL2SDC4DAAM1
PROTEIN STRUCTURE
Preparing viewer…
PDB6NE2 · 1.30 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.78LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.54 [0.38–0.78]
RankingsWhere FZD7 stands among ~20K protein-coding genes
  • #4,317of 20,598
    Most Researched110 · top quartile
  • #6,392of 17,882
    Most Constrained (LOEUF)0.78
Genes detectedFZD7
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
Spatial sorting enables comprehensive characterization of liver zonation.
PMID: 31535084
Nat Metab · 2019
1.00
2
Multi‑layered prevention and treatment of chronic inflammation, organ fibrosis and cancer associated with canonical WNT/β‑catenin signaling activation (Review).
PMID: 29786110
Int J Mol Med · 2018
0.90
3
WNT11-FZD7-DAAM1 signalling supports tumour initiating abilities and melanoma amoeboid invasion.
PMID: 33082334
Nat Commun · 2020
0.80
4
Structural and dynamic characterization of human Wnt2-Fzd7 complex using computational approaches.
PMID: 30191337
J Mol Model · 2018
0.70
5
Circular RNA ACTN4 promotes intrahepatic cholangiocarcinoma progression by recruiting YBX1 to initiate FZD7 transcription.
PMID: 34509526
J Hepatol · 2022
0.60